Paediatric Cardiology Flashcards
In the foetal circulation, is the resistance in the lungs high or low?
High
In the foetal circulation, is the resistance in the systemic circulation high or low?
Low
Oxygenated blood from the placenta travels to a foetus via what vessel?
The umbilical vein
Blood from the umbilical vein bypasses the liver as a result of what anatomical structure?
Ductus venosus
Blood from the umbilical vein drains into where?
IVC
In the foetal circulation, most blood from the IVC passes straight into the left atrium as a result of what anatomical structure?
Foramen ovale
In the foetal circulation, there is shunting of blood in what direction?
Right to left
In the foetal circulation, blood can pass from the pulmonary artery into the aorta as a result of what anatomical structure?
Ductus arteriosus
What happens to the pulmonary vascular resistance at birth?
It decreases
What happens to the systemic vascular resistance at birth?
It increases
Congenital heart disease is an umbrella term for abnormalities in the structure of the heart that develop when in embryogenesis?
Days 20-50
A high maternal alcohol consumption in pregnancy gives an increased risk of which congenital heart defects?
VSD and ASD
Maternal use of lithium in pregnancy increases the risk of what congenital heart defect in the foetus?
Ebstein’s anomaly
Apical displacement of tricuspid valve leaflets describes what congenital heart defect?
Ebstein’s anomaly
What congenital heart defects are likely to be seen in an individual with Turner’s syndrome?
Coarctation of the aorta and bicuspid aortic valves
Which congenital heart defects are likely to be seen in an individual with Down’s syndrome?
VSD or AVSD
There is an increased risk of which congenital heart disease in Down’s, Edward’s and Patau’s syndromes?
VSD
Name the acyanotic congenital heart defects which cause the formation of a left to right shunt?
ASD, VSD, AVSD and patent ductus arteriosus
Name the obstructive acyanotic congenital heart defects?
Aortic/pulmonary stenosis, coarctation of the aorta and hypoplastic left heart
Name the two cyanotic congenital heart defects?
Tetralogy of Fallot and transposition of the great arteries
What is the most common congenital heart defect?
VSD
In patent ductus arteriosus, blood is shunted from where to where?
Aorta to pulmonary artery
All babies with Down’s syndrome should undergo what investigation in the first few days of life to assess for congenital heart disease?
ECHO
A harsh pansystolic murmur heard best at the lower left sternal edge is heard in what congenital heart defect?
VSD
An ejection systolic murmur in the 2nd intercostal space is heard in what congenital heart defect?
ASD
A loud, low-pitched, continuous, machinery-like murmur is heard in what congenital heart defect?
Patent ductus arteriosus
Increased blood flow through the lungs as a result of a left-right shunt eventually leads to what irreversible complication?
Pulmonary hypertension
What is meant by Eisenmenger’s syndrome?
When pulmonary pressure becomes higher than systemic pressure (causing a left to right shunt to become a right to left shunt)
What investigation is used to confirm a diagnosis of congenital heart disease?
ECHO
What complication of congenital heart disease with a left to right shunt may be seen on an ECG?
Right ventricular hypertrophy
How are small congenital heart defects with a left to right shunt treated?
ECHO every 6-12 months (they will usually close spontaneously)
How are large congenital heart defects with a left to right shunt treated?
Surgical repair
How are babies with congenital heart disease fed, in order to promote their growth?
High calorie formula via an NG tube