Noninflammatory Blistering Disorders Flashcards
1
Q
What are porphyrins?
A
Pigments that are normally present in hemoglobin, myoglobin, and cytochromes.
2
Q
What are the five major types of porphyria?
A
- Congenital erythropoietic porphyria
- Erythrohepatic protoporphyria
- Acute intermittent porphyria
- Porphyria cutanea tarda
- Mixed porphyria
3
Q
What are the cutaneous manifestations of porphyria?
A
Cutaneous manifestations consist of urticaria and vesicles associated with scarring that are exacerbated by exposure to sunlight. The vesicles are subepidermal in location and the adjacent dermis contains vessels with walls that are thickened by glassy deposits of serum proteins, including immunoglobulins.
4
Q
What is porphyria?
A
A group of uncommon inborn or acquired disturbances of porphyrin metabolism.
