neuromuscular musculoskeletal disorder Flashcards
Exam 3
Anatomic Differences in Children versus Adults Related to NM and MS Systems:
When does motor development begin? How does it develop?
Motor development begins at birth and proceeds in predictable sequence.
Anatomic Differences in Children versus Adults Related to NM and MS Systems:
How is range of motion at birth?
Full range of motion is present at birth.
Anatomic Differences in Children versus Adults Related to NM and MS Systems:
How is a child’s spinal cord compared to an adult?
The child’s spinal cord is more mobile than the adult.
Anatomic Differences in Children versus Adults Related to NM and MS Systems:
When is myelinization complete?
Myelinization is not complete until 2 years of age.
Anatomic Differences in Children versus Adults Related to NM and MS Systems
What is ossification? When does this occur? When is it complete?
Ossification is when the cartilage turns to bone.
This occurs throughout childhood and is complete by adolescence.
Anatomic Differences in Children versus Adults Related to NM and MS Systems:
Where does growth of bones occur?
Growth of bones occurs primarily at specialized growth plates at the end of the long bones.
Anatomic Differences in Children versus Adults Related to NM and MS Systems:
How are children’s bones compared to adults?
Children’s bones are more vascular and tend to heal faster than adults.
Eliciting History of Present Neurologic Disorder
Changes in gait, any “clumsiness”
Activity level compared to peers
Recent trauma
Poor feeding
Lethargy
Fever
Weakness
Alteration in muscle tone - Hypo and hypertonia are abnormal signs
History of developmental milestones
Physical assessment:
Inspection and observation?
Motor function.
Reflexes.
Sensory function.
Physical assessment:
Palpation
Muscle strength and tone.
Physical assessment
Auscultation
Lungs for adventitious sounds.
Laboratory and Diagnostic Tests for NM and MS Disorders
CBC, creatine kinase
Radiographs
Fluoroscopy, arthrography
Myelography, electromyography (EMG),
muscle biopsy
Nerve conduction testing
CT, MRI, ultrasound
Genetic testing
Types of Neuromuscular or Musculoskeletal Disorders:
Congenital
Acquired
Types of Neuromuscular or Musculoskeletal Disorders:
Congenital: What is it? When does it develop?
Structural abnormality.
Genetic abnormality (may develop later in life).
Types of Neuromuscular or Musculoskeletal Disorders
Acquired: How?
Trauma, any hypoxia to the brain or spinal cord.
Autoimmune, bacterial or viral infections.
Types of Neuromuscular or Musculoskeletal Disorders:
What can Congenital and Acquired result in?
Each can result in neuromuscular or musculoskeletal dysfunction.
Positional alterations:
How are infants hips normally?
What is it called?
Infants hips are usually flexed, abducted, and externally rotated, with the knees flexed and lower limbs internally rotated. This is a normal developmental variation termed internal tibial torsion.
Positional alterations:
What is the term for bowlegged?
Genu varum: bowlegged
Positional alterations:
What happens to ITT and varum as a child gets older? What can develop instead? When does that resolve?
As ITT and varum resolve as child gets older, Genu valgum, or knock knees can happen by age 2-3. Should resolve by 7-8 years old.
Congenital/Developmental Neuromuscular and Musculoskeletal Disorders
Neural tube defects
Structural disorders of the skeleton
Developmental dysplasia of the hip
Torticollis
Tibia vara
Genetic disorders
Congenital/Developmental Neuromuscular and Musculoskeletal Disorders:
Neural tube defects including
Spina bifida occulta
Meningocele
Myelomeningocele
Congenital/Developmental Neuromuscular and Musculoskeletal Disorders
Structural disorders of the skeleton
Pectus excavatum and carinatum,
limb deficiencies,
polydactyly/syndactyly,
metatarsus adductus)
Congenital club foot
Congenital/Developmental Neuromuscular and Musculoskeletal Disorders
Genetic disorders
Osteogenesis imperfecta
Various types of muscular dystrophy
Spinal muscular atrophy
Osteogenesis Imperfecta: What is it?
Brittle bone disease
Osteogenesis Imperfecta: What are signs and symptoms?
Lax joints
Small, weak muscles
Osteogenesis Imperfecta: Diagnosis?
Clinical symptoms and level of disability
Radiographic studies
Osteogenesis Imperfecta: Nursing care- What should you teach parents?
Teach parents to watch for signs of fractures (irritability, fever, and refusal to eat)
Osteogenesis Imperfecta: Nursing care continued:
Olpadronate (bone-resorption inhibitor) therapy
Bisphosphonates
Postoperative care
Osteogenesis Imperfecta:
Education/discharge instructions
Play and physical therapy
ROM
Ambulatory devices
Genetic counseling
Protect child while allowing as normal a life as possible
Osteogenesis Imperfecta: What is the hallmark sign?
Blue eyes- blue sclera
Muscular Dystrophy: What is it?
General term for a group of inherited types of neuromuscular disorders that affect voluntary muscles.
Muscular Dystrophy: How do symptoms appear?
Symptoms not always evident at birth; may manifest later in childhood.
Muscular Dystrophy: How is lifespan?
May limit life span due to compromised ability to adequately support ventilation.
Nursing Management Goals for a Child With Muscular Dystrophy:
Promoting mobility
Managing elimination
Maintaining cardiopulmonary function
Preventing complications and maximizing quality of life
Nursing Management Goals for a Child With Muscular Dystrophy:
Promoting mobility- What should be done?
Administering medications
Performing passive stretching and strengthening exercises
Nursing Management Goals for a Child With Muscular Dystrophy
Maintaining cardiopulmonary function: How?
Teaching deep breathing exercises
Performing chest physical therapy
Nursing Management Goals for a Child With Muscular Dystrophy
Preventing complications and maximizing quality of life: How?
Developing a diversional schedule
Providing emotional support
Duchenne’s Muscular Dystrophy: What is it?
Progressive weakness and wasting of muscles
Duchenne’s Muscular Dystrophy: When is onset?
Who is it in mainly?
Onset 3-5 years old
Primarily males
Duchenne’s Muscular Dystrophy: What is a major sign of this disorder?
Gower’s sign