Module 16 : Restrictive and Other Cardiomyopathies Flashcards
what is another term for restrictive cardiomyopathy RCMO
- infiltrative CMO
what does RCMO refer to
- disease other than ischemici heart disease which cause increased resistance to LV filling due to increased myocardial stiffness
- increased LVEDP
- increase mLAP
what is the main cause of RCMO
- abnormal infiltration, storage, or fibrosis within the myocardium
what are the 4 classes of RCMO
- non infiltrative
- infiltrative
- storage disease
- endomyocardial
what are the 2 main causes of non infiltrative RCMO
- HCMO
- diabetic CMO
what are the 2 causes of infiltrative RCMOq
- amyloidosis
- sarcoidosis
what is a main cause of storage disease RCMO
- GSD
what are the 2 endomyocardial causes of rCMO
- endomyocardial fobroelastosis
- carcinoid heart disease
what is the etiology of infiltrative RCMO
- disease of heart muscle secondary to a disorder that produces histological changes to cardiac muscle by depositing a substance inside or in between muscle cells
what 2 things may infiltrative RCMO lead to
- infiltration of myocardium
- restrictive filling pattern
what are the 3 clinical findings of RCMO
- diastolic dysfunction (HFnEF) backwards failure
- early stags normal systolic function
- arrhythmias
what are the echo findings in RCMO
- LV cavity size normal
- wall thickness increased
- bi atrial enlargments
- small pericardial effusion
what are the 5 roles of echo in RCMO
- asses chamber function and size
- degree of DD
- degree of MR or TR
- determine RVSP
- differentiate from constrictive pericarditis
what will the ECG look like with RCMO
- atrial and ventricular arrhythmias
- low voltage QRS
- conduction defects
what are the 5 medical treatments of restrictive CMO
- treat underlying aetiology
- diuretics
- ace inhibitors
- anticoagulnats
- anti arrhythmias
what are the 2 surgical treatments of RCMP
- pace maker / defibrilaors
- cardiac transplant
what is the most common type of RCMO
- amyloidosis
what is amyloidosis RCMO
- deposits of amyloid protein in between myocytes
- inderdiagnosed