Miller's Peds Flashcards

1
Q

86% of elbow ROM returns when after SCH CRPP

A

3 mos

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2
Q

what can happen if submuscular plate is not removed after healed in femur fracture ORIF

A

genu valgum

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3
Q

age when dens physis closes in kids

A

6 yo

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4
Q

Abx for Lyme

A

> 8 yo doxy

< 8 yo Amoxicillin

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5
Q

consider this bug if kid not responding to IV abx for diskitis

A

TB

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6
Q

treatment for chronic recurrent mulitfocal osteomyelitis

A

NSAIDs

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7
Q

most likely cause of osteomyelitis in kid with sickle cell

A

Staph a is #1

- but this is the group we can see salmonella

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8
Q

earliest XR finding for kid with discitis

A

loss of lumbar lordosis

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9
Q

procedure for stiff knee gait in CP kid

A

hamstring lengthening and rectus transfer

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10
Q

Surgical procedures for CP with equinovarus foot

A

Split PT to peroneals with overactive PT

Splint TA to cuboid with overactive TA

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11
Q

Myelodysplasia kid

- level that they can walk

A

L4

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12
Q

maternal finding assoc with sacral agenesis

A

diabetes

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13
Q

scoliosis degree when you want to fuse in Duchenes

A

> 20-25

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14
Q

Findings in Fascioscapulohumeral Muscular Dystrophy

A

normal CK
scapular winging
can’t whistle

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15
Q

Foot deformity in Freidrich Ataxia

A

cavus

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16
Q

pathology of Freidrich ataxia

A

degeneration of spinocerebellar and posterior columns of spinal cord

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17
Q

GAA repeat

A

Friedrichs ataxia

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18
Q

Cause of death in Friedrichs Ataxia

A

cardiomyopathy

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19
Q

Dysphagia
excessive sweating
postural hypotension

A

Riley Day Syndrome

occurs in Ashkenazi Jews

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20
Q

Pathology of myasthenia gravis

A

Ab against Ach receptors

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21
Q

treatment options for myasthenia gravis

A

thymectomy
steroids
Ach-esterase inhibitors (pyridostigmine)
plasmapheresis (to remove the Ab)

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22
Q

newly developed unilateral external rotation in a kid

- what should you consider the cause

A

SCFE

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23
Q

Treatment for tarsal coalition

  • talocal
  • talonavic
A

talocal
< 50% -> resection + fat interposition
> 50% -> fusion
Calnavic
resection with fat interposition

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24
Q

overlapping 5th toe treatments

A

observation as this usually resolves

Tenotomy + dorsal capsulotomy if doesn’t and is bothersome

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25
congenital curly toe treatment
observation or flexor tendon tenotomy if bothersome after a few years
26
PITX1 mutation assoc with
Clubfoot
27
Adam's forwadr bend test measurement that warrants referral
7 degrees
28
AIS MRI indications
``` Left Thoracic curve pain apical kyphosis rapid curve progression neurological signs congenital anomalies ```
29
Risk factors for curve progression after maturity
Thoracic curve > 50 lumbar curve > 30 will progress 1-2 degrees/year
30
Level that determines CTLSO vs TLSO
Apex T7 and higher -> CTLSO (Milwaukee) | Apex T8 and lower -> TLSO
31
when to perform anterior AND posterior for AIS
< 10 yo | curve > 75 (he said maybe)
32
Delayed infection (9-12 mos) in AIS s/p fusion
remove implant | ABX
33
Alveoli continue to multiply until what age
8 yo
34
spinal deformity with highest risk of neurological injury with progress
Congenital Kyphosis
35
That with atlanto-axial instability
Downs RA Grisel's
36
how to treat pseudosubluxation of C spine in kid
NTD
37
Most important risk factor for DDH
Breech
38
If done, what is the purpose of femoral osteotomy for DDH during closed reduction
prevent AVN | treat sever anterversion
39
When to leave DDH alone
bilateral over 6 yo | unilateral over 8yo
40
Lateral pillar classification is not valid until what phase of the disease
end of fragmentation
41
Defect in what gene leads to longitudinal femoral def
Sonic Hedge Hog gene
42
Common knee finding with congenital short femur
absent ACL
43
treatment for congenital patellar dislocation
lateral release + some type of realignmen
44
Mucopolysaccharidoses have what type of dwarfism
proportionate
45
What genes/molecule influences limb bud to form
Homeobox | Sonic Hedgehog
46
When are primary centers of ossification present
all present at birth
47
Abnormalities affectein the primary center of ossification
Long femorl def Cleidopcranial dysplasi Apert's
48
Congenital disease with high incidence of coxa vara
Cleidocranial dysplasia
49
Dysplasia affecting the secondary ossification centers
MEd SED congenita SED tarda Diastrophic dysplasia
50
What disease do you think of if they show you hips with appearance of bilateral Perthes (they will be symmetric)
MED
51
COL2A1 mutation
Spondyloepiphyseal Dysplasia | abnormal type II collagen casugin intracelluyliuar procollagen inclusions
52
Major workup necessary for kid with spondyloepiphyseal dysplasia
C spine films as they can have atlanto-axial instability (odontoid hypoplasia) which may require fusion
53
portion of msk system not affected in MED
spine (which does occur in SED)
54
cervical spine finding with diastrophic dysplasia
cervical kyphosis which may cause quadraplegia
55
Area in growth plate with FGFR-3 mutation
prolierative zone | causes and QUANTITATIVE defect
56
if asked a treatment for mucopolysaccharidosis
bone marrow transplant
57
osteochondroma that occurs in the epiphysis | - cause?
Trevor's Disease (Dysplasia epiphysealis hemimelica) | - defect in groove of ranvier
58
area of physis leading to osteochondroma
groove of ranvier
59
glycine substitution on procollagen - disease - ramification
OI | - this leads to abnormal cross linking
60
Medication given to kid with OI
IV pamidronate
61
Path of Scurvy
low Vit C -> prevents conversion of proline to hydroxyproline
62
common treatment for osteopetrosis
bone marrow transplant
63
When asked hemihypertrophy-> think ?
Neurofibromatosis
64
When to fusion Downs C1/2
sx's or ADI < 10mm
65
Accessory calcaneal ossification | - other ortho condutions to check
Larsen's - cervi al kyphosis - dislocated joints
66
Shoulder motion most likely to be limited in Sprengles
shoulder abduction
67
thumb present but no radius
thrombocytopenia absent radius
68
abnormal ligament in Madelung's
Vicker's ligament - abnormal palmar ligament that tethers the lunate to the radius
69
When do you fit a prosthesis in a kid
age 6 when they start sitting