lecture 10 [musculoskeletal + neuromuscular] Flashcards
what are the acquired skeletal defects?
(6)
- Legg-Calve-Perthes
- slipped capital femoral epiphysis(SCFE)
- kyphosis
- lordosis
- scoliosis
- spinal neuromuscular atrophy
what is Legg-Calve-Perthes disease?
asceptic necrosis of the femoral head that can either be unilateral or bilateral
what are the symptoms of LCP?
(6)
- painless limping
- hip stiffness
- limited ROM
- hip, thigh, & knee pain
- shortened affected leg
- muscle wasting
what are the treatment goals for LCP?
(4)
- eliminate hip irritability
- maintain ROM
- prevent bone collapse
- ensure well-rounded femoral head
what are the primary therapeutic measures for LCP?
- abduction brace/ cast
- traction
what is slipped capital femoral epiphysis (SCFE)?
spontaneous displacement of the proximal femoral epiphysis that develops shortly before onset of puberty or accelerated growth
SCFE is more commonly seen in boys & obese children
true
which conditions are associated with SCFE?
- GH therapy
- endocrine disorders
- renal osteodystrophy
- radiotherapy
what are the primary treatments for SCFE?
- non-weight bearing activity
- surgery
SCFE must be diagnosed early
true
what is kyphosis?
convex curvature of the thoracic spine
kyphosis is usually a secondary condition to other diseases like:
- TB
- chronic arthritis
- compression fractures
how is kyphosis treated?
- shoulder/ abdomen exercises
- bracing
what is lordosis?
cervical or lumbar curvature of the spine
lordosis is often associated with which other conditions?
- hip contractures
- scoliosis
- obesity
- hip dysplasia
- SCFE
what is scoliosis?
lateral curvature of the spine, possible spinal rotation & thoracic hypokyphosis
what is the “gold standard” treatment for scoliosis?
bracing
what are the different types of braces for scoliosis?
(3)
- Boston
- Milwaukee
- Charleston
what are the congenital muscular disorders?
- spinal muscular atrophies
- Duchenne’s muscular dystrophy
Duchenne’s muscular dystrophy is the most severe form of muscular dystrophy
true
why are males more affected with Duchenne’s?
it is primarily an x-linked genetic disorder
what are the diagnostic procedures for Duchenne’s?
- muscle biopsy
- blood polymerase chain reaction to detect dystrophin gene mutation
- blood creatine phosphokinase (elevated)
there is no treatment for Duchenne’s; and families only need to be prepared for impending cardiac & respiratory difficulties along w/ mental retardation
true
what are the manifestations of Duchenne’s?
(5)
- Gowers sign
- waddling
- difficulty rising to positions
- progressive muscle atrophy
- loss of ability to walk by 12yrs
what are the congenital skeletal defects?
(5)
- hip dysplasia
- club foot
- genu varum
- genu valgum
- osteogenesis imperfecta
what are the expected diagnostic signs of hip dysplasia?
(6)
- Ortolani sign (hip is reduced w/ abduction)
- Galeazzi/ Allis sign (uneven knee levels)
- Barlow sign (hip dislocates by adduction)
- Trendelenberg sign w/ lordosis (tilted hips with standing on one foot)
- U/S or x-ray
when is an ultrasound appropriate for hip dysplasia?
2 weeks old
when is an x-ray appropriate to diagnose hip dysplasia?
older than 4mos
what are the treatments for hip dysplasia?
- Pavlik harness
- Bryant traction
- Hip spica cast
- surgical reduction
at what age is the Pavlik harness appropriate?
newborn to 6 months
what is a Pavlik harness?
a chest harness that abducts legs
what is the treatment for hip dysplasia WITH adduction contracture?
- Bryant traction
- Hip spica cast
when is surgical reduction appropriate for a child with hip dysplasia?
when they are 6 months to 2 years old
what is club foot?
a complex deformity of the ankle & foot that is sometimes associated with cerebral palsy & spina bifida
what are the categories of club foot?
- positional
- syndromic
- congenital
what causes positional clubfoot?
intrauterine crowding
what is syndromic clubfoot?
a category of the disorder that occurs with other syndromes
what are the therapeutic procedures for club foot?
casting
how are the series of casts implemented for clubfoot?
applied every 2-3 days for up to 3 weeks, then 1-2 week intervals
genu varum
genu valgum
what is osteogenesis imperfecta?
an inherited connective tissue disorder that results in bone fractures along w/ restricted growth
“brittle bone disease”
what are the clinical manifestations of osteogenesis imperfecta?
- multiple bone fractures
- blue sclera
- early hearing loss
- hypoplastic discolored teeth
what is the treatment for osteogenesis imperfecta?
pamidronate IV with biphosphate
what is the expected MOA of pamidronate?
increases bone density
what are the types of fracture in children?
- bend
- buckle
- greenstick
- complete
bend fratcures only occur in the ulna & fibula when there is a fracture in the radius & tibia
true
the most common site for a fracture in a child is the growth plates, where is it?
located on the ends of the hard bone (epiphysis)
what are the types of fracture lines?
- transverse
- oblique
- spiral (circular)
what are the signs of compartment syndrome that occurs with casts?
5 P’s
- paresthesia
- pallor
- paralysis
- pain
- pulselessness
what are the nursing priorities for a child with a cast?
regular skin checks & neurovascular checks
what are the components of neurovascular assessments?
- sensation
- skin temperature
- skin color
- cap refill
- pulses
- movement
what are tractions used for?
(4)
- provide muscle rest
- immobilization
- alignment
- prevent contractures
what are the types of tractions?
(3)
- skin
- manual
- skeletal
how do skin tractions correct musculoskeletal dislocations?
applies pulling force using tape & straps on the skin (w/ weights)
what are the types of skin tractions?
- Bryant
- Buck
- Russell
what is a skeletal traction?
a continuous pulling force through the use of weights that uses pins or rods inserted through a bone
what are the types of skeletal traction?
- cervical/ halo
- 90-90
- external fixators
what is a manual traction?
application of casts along with having a closed reduction
what are the infectious musculoskeletal problems?
(4)
- osteomyelitis
- septic arthritis
- lupus
- juvenile arthritis
what is osteomyelitis?
an infection within the bone secondary to a bacterial infection (open fracture or bloodborne)
what are the treatments & measures for osteomyelitis?
(3)
- IV/ oral ABX
- immobilize w/ cast
- monitor for adverse rxns (such as superinfection & hepatic, renal, and hematologic complications)
what is septic arthritis?
bacterial infection of the joint
what is the most common bacterial agent for septic arthritis?
S. aureus
what are the manifestations of septic arthritis?
(3)
- severe joint pain
- swelling
- warmth at site
what is juvenile arthritis?
a chronic inflammation of synovium & eventual erosion of articular cartilage
what are the medications for juvenile arthritis?
(4)
- NSAIDs
- Methotrexate
- Etanercept (tumor-necrosis factor alpha receptor)
- Prednisone
nurses must apply heat packs to the affected joints for pain & stiffness reduction
true
what is lupus?
a chronic multisystem autoimmune disease of connective tissue & blood vessels
what are the congenital neuromuscular problems?
(4)
- cerebral palsy
- neural tube defects
- hypotonia
what are the types of neural tube defects?
- anencephaly
- spina bifida
what is cerebral palsy?
a nonprogressive impairment of motor function that causes spasticity or dyskinesia (involuntary movements)
what is the most prominent etiology of cerebral palsy?
kernicterus
elevated bilirubin in newborns
what are some risk factors for cerebral palsy?
- LBW
- maternal chorionaminionitis
- anoxia in-utero
what are the s/s of cerebral palsy?
(8)
- persistent Moro reflex or tonic neck reflex
- failure to smile by 3 months
- persistent tongue thrust by 6 months
- spasticity
- scissoring of legs
- nystagmus
- hearing loss
- feeding difficulties
what kinds of care management do patients with cerebral palsy need?
(5)
- physical therapy
- speech therapy
- occupation therapy
- rhizotomy (surgery)
- medication
children with cerebral palsy are more likely to aspirate while feeding
true
what are the medications that are usually given to patients with cerebral palsy?
(7)
- Baclofen
- Diazepam
- Botulinin toxin A
- Dilantin
- Valium
- Botox
- ADHD meds
what are the measures that parents can take to prevent aspiration in children with cerebral palsy?
- jaw support
- upright position
what is the etiology of anencephaly?
the neurall tube in-utero fails to close, leading to an underdeveloped brain in which the infant does not have a forebrain nor a cerebrum
what is spina bifida?
an NTD characterized by failure of the osseus spine to close
what are the categories of spina bifida?
(2)
- occulta
- cystica
what are the characteristics of spina bifida occulta?
(4)
- affects the lumbosacral area
- not visible externally
- missing vertebral bone surface(dimpling)
- no spinal cord involvement
what are the characteristics of spina bifida cystica?
visible defect w/ sac-like protrusion
what are the subtypes of spina bifida occulta?
- meningocele
- myelomeningocele
what are the characteristics of spina bifida cystica w/ a meningocele?
- sac contains spinal fluid & meninges
- no neurologic deficits
what are the characteristics of spina bifida cystica w/ a myelomeningocele?
- sac contains spinal fluid, meninges, and nerves
- caused by failure to close of neural tube
- decreased motor & sensory function
what are the expected findings of spina bifida occulta?
(4)
- dimpling in the lumbosacral area
- port wine angioma
- dark hair tufts
- subcutaneous lipoma
what are the expected findings of spina bifida cystica?
(5)
- flaccid muscles
- lack of bowel control
- rectal prolapse
- spinal curvature abnormalities (kyphosis/ scoliosis)
- protruding sac
most patients with spina bifida have a latex allergy
true
what are the s/s of hydrocephalus?
- sunset eyes
- increased head circumference
- Cri du chat
- poor feeding (w/ increased ICP)
what is the primary cause for hydrocephalus?
Arnold Chiari syndrome
what is another term for hypotonia?
floppy infant syndrome
what is the most common diagnostic test for hypotonia?
EMG
measures muscle response to a nerve’s stimulation of the muscle
what are the causes of spinal cord injuries?
(4)
- MVA
- long-acting PCN in the artery
- hyperextension of the neck
- spinal compression
cervical spines 1-8 innervate which part of the body?
- diaphragm
- neck
- upper arms
- upper trunk
thoracic spines 1-12 innervate which part of the body?
- anterior trunk
- posterior trunk
- intercostal muscles
lumbar spine 1 through lumbar spine 5 innervate which part of the body?
(5)
- lower trunk
- bladder
- rectum
- sexual organs
- legs
what is stage 1 of spinal cord injuries?
(5)
- flaccid paralysis
- loss of sensation
- spinal shock syndrome
- edema
- autonomic dysreflexia
what happens duing stage 2 of a spinal cord injury?
- autonomic dysreflexia
- spinal reflex activity returns
what are the diagnostic tests for spinal cord injuries?
- check sensation along dermatomes
- CT
- MRI
what is the nursing management for spinal cord injuries?
(6)
- cervical traction
- reduce spinal swelling with steroids
- immobilize the spine
- assess neuro status q1h
- rehab
what are the infectious neuromuscular dysfunctions?
- Guillain Barre syndrome
- Tetanus
- Botulism
Guillain Barre syndrome usually arises from viral infections & vaccinations as an immune response
true
what is the hallmark sign for Guillian Barre syndrome?
ascending paralysis
which neurotoxin causes tetanus?
“lock jaw”
clostridium tetani
how long is the incubation period for C. tetani?
3 days - 3 weeks
what are the s/s of tetanus?
- risus sardonicus
- opisthotonus
- muscular rigidity of neck muscles
- trismus (lock jaw)
what is the treatment for children w/ tetanus who are unimmunized?
- tetanus immune globulin
- tetanus toxoid
- ABX
what is botulism?
serious food poisoning caused by the bacteria clostridium botulinum from improperly sterilized food
what are the s/s of botulism?
(5)
- blurred vision
- dizziness
- vomiting
- dysphagia
- descending paralysis
honey is the most common cause for botulism
true