Interrupted Aortic Arch (IAA) Flashcards
What is IAA?
IAA is a CHD in which the aorta is divided.
In IAA, what does the divide separate?
In IAA, the aortic divide separates the ascending aorta and most of the aortic arch (with its superior vessels) from the rest of the aortic arch and the descending aorta.
What does IAA stand for?
Interrupted Aortic Arch
What does IAA usually come with?
A VSD
Is IAA a critical CHD?
Yes
What exams and tests are usually required for patients with IAA? (1, 2)
Usually only simple tests, such as an echocardiogram and a chest x-ray are required for patients with IAA.
What is a chest x-ray?
A chest x-ray is an x-ray of the thoratic region.
What is an echocardiogram (echo)?
An echocardiogram (echo) is a detailed ultrasound of the heart
What is the thoratic region?
The region of the body containing the chest cavity.
What is needed to treat IAA and its effects?
Surgery is needed to repair the aorta and close off the VSD (treat IAA)
What medicine is continuously injected into babies with IAA and why?
Dinoprostone (a medicine) is continuously injected into one of the veins of a baby with IAA to keep their PDA open.
Why may surgery be delayed for a certain amount of time?
Surgery may be delayed for several days to get the baby in its best condition
What is a PDA?
Patent ductus arteriosus: An extra blood vessel that connects the top of the MPA and the bottom of the arcus aortae.
Sometimes as the baby grows, … (1). This leads to… (2)
Sometimes as the baby grows, the repair of the aorta does not. This leads to the narrowing of the aorta and therefore further treatment
It is common to develop… (1). These new narrowings… (3)
It is common to develop new narrowings around or at the aortic valve. These new narrowings may be serious and may require further major surgery or even valve replacement as the child grows.
Even many years after the operation(s), it is possible to develop… (1). This also may… (1)
Even many years after the operation(s), it is possible to develop an aneurysm in the wall of the aorta. This also may require further surgery.
_____ _____ _____ in the _____ _____ are therefore _____ throughout the patient’s _____ _____.
Regular check-ups in the outpatient clinic are therefore necessary throughout the patient’s entire life.
What is an aneurysm?
An aneurysm is a weak spot in a vessel wall.
Some children with IAA also have other…
Some children with IAA also have other abnormalities
What is the most common abnormality that comes with IAA (except VSD)? What is it?
22q11deletion syndrome. 22q11 deletion syndrome is a genetic abnormality in which a small part of a chromosome is missing
Although some children with 22q11 deletion syndrome _____ and _____ _____; others will have _____ or _____ _____ or _____ _____ _____ _____ _____ _____.
Although some children with 22q11 deletion syndrome grow and develop normally; others will have learning or speech difficulties or difficulty fighting certain types of infection.
Why is it important that the development of a child with 22q11 deletion syndrome is monitored?
It is important that the development of a child with 22q11 deletion syndrome is monitored so that help can be given early if necessary.
What test is usually used to diagnose 22q11 deletion syndrome? When will the results usually return?
A blood test is usually used to check for 22q11 deletion syndrome, but it may take some weeks for the results to return.
