Hypoplastic Left Heart Syndrome

Question 1

Hypoplastic Left Heart Syndrome is:

Answer 1

One ventricle pumping to the lungs as well as systemically.

Question 2

The ventricle takes on ____ ____ ____ pressures.

Answer 2

right and left

Question 3

One main effect that hypoplastic left heart syndrome is

Answer 3

pulmonary hypertension

Question 4

Cause of Hypoplastic left heart syndrome:

Answer 4

• When the heart tube folds and bends, the primitive LV doesn’t develop

Question 5

Associated lesions with hypoplastic left heart syndrome:

Answer 5

1. MV stenosis
2. Narrowed and Atretic AO valve
3. LV filled with clots
4. Hypoplastic LA
5. Retrograde coronary perfusion
6. PDA
7. ASD and VSD

Question 6

Surgical steps taken to treat Hypoplastic Left Heart Syndrome:

Answer 6

1. Keep PDA open
2. Correct metabolic acidosis
3. Manipulate PVR
4. Intubation of infant
5. Cardiac medication treatment