Hemophilia/Factors VIII and IX: 2 Questions

Question 1

What is Hemophilia?

Answer 1

A rare genetic disorder; natural coagulation and hemostasis factors are limited or absent.

Question 2

What type of Hemophilia is most common

Answer 2

Hemophilia A

Question 3

What factor is associated with Hemophilia A (Most Common)?

Answer 3

– Factor VIII: Caused by missing or defective factor VIII (a clotting protein)

Question 4

What is the nickname for Hemophilia B?

Answer 4

Factor IX-9 (aka Christmas disease) Caused by missing or defective IX (a clotting factor)

Question 5

What are the medications for Hemophilia A (Factor XIII)?

Answer 5

Plasma (Hemofil-M) and Recombinant Factor VIII (Advate)

Question 6

What are the medications for Hemophilia B (Factor IX)?

Answer 6

Plasma (AlphaNine SD) and
Recombinant Factor IX (Benefix)

Question 7

What are the symptoms of Hemophilia ?

Answer 7

Excessive bleeding, easy bruising, Bleeding in joints, Injury=prolonged bleeding, and internal bleeding=slight injury

Question 8

What is the treatment for Hemophilia?

Answer 8

Synthetically produced factors or derived from human blood.

Question 9

What should you monitor during hemophilia assessment?

Answer 9

Monitor I & O; color of urine; swelling of joints; bleeding from gums, stool, or emesis; vitals HIGH HR and RR, Low BP

Question 10

What labs should be monitored for Hemophilia assessment?

Answer 10

Hematocrit (HCT), direct Coombs test, Plasma factor VIII levels, platelet count

Question 11

What type of tempature should be applied for bleeding ?

Answer 11

Apply cold (Ice) because heat can prolong bleeding.

Question 12

What products should you avoid with hemophilia ?

Answer 12

ASA or NSAIDS

Question 13

How long should you apply pressure for IV or IM sites?

Answer 13

5 Min

Question 14

Should you avoid less punctures (Venipuncture’s)?

Answer 14

YES

Question 15

What should a patient bring with them before traveling ?

Answer 15

Adequate supply of factor 8