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Pediatrics > \general pediatrics > Flashcards

\general pediatrics Flashcards

1
Q
A

measles
3c and 1 K
coryza, cough, conjunctivitis,

coryza= inflammation of membrane int he nose

Kooplik spots ( white spots that occur inside cheeks)

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2
Q

p

person with sickle cell disease, history of acute chest syndrome with worsening chest tightness at night and dry cough most likely has

what would you do to diagnose?

A

asthma

spirometry

vs PE would see persistent chest pain and cough.

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3
Q

4A preterm baby with rapidly increasing head circumference, seizures, lethargy, hypotonia most likely has

A

Intraventricular hemorrhage

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4
Q

acute chest syndrome

A

vascoocculustion of pulmonary vasculature
common in SCD

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5
Q

acute onset of pain over the anterior surface of the neck, worsens with swallowing or sticking out tongue + fever and chills is?

A

infected thyroglossal cyst

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6
Q

acute post streptococcal glomerulonephritis

what lab should you draw for diagnosis?

A

complement since it lowers complement 3
antigen form IgG ang IgM immune complexes to kidney cells
- will see lower complement 3 , hematuria, and proteinuria

vs IgA nephropathy ( IgA complexes in mesangium)/ Henoch Schonlein purpura
- IgA does not fix complements so will see normal complements

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7
Q

angelman syndrome

A

happy puppet syndrome
- unusual gait, unprovoked outbursts of laughter, seizures, microcephaly, speech impairment, hyperactivity, fascination with water, poor sleeping
- deletion of chromosome 15q11-13 from maternal side

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8
Q

anorexia induced ammenorrhea labs

A

FSH and LH are low

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9
Q

antibiotic pcp px is indicated for

A

Severe Combined Immunodeficiency,
chronic granulomatous disease

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10
Q

asymmteric red reflex is a sign of ______ ,
can be in someone with a________

diagnostic test?

A

strabismus, retinoblastoma
dilated funduscopic exam

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11
Q

Ataxia telangiectasia

A

autosomal recessive disorder that causes defective DNA repair => tumors and immunodeficiency

B and T cell dysfunction
4 A’s:

ATM gene mutation, Ataxia, spider Angioma, IgA deficiency,

ataxia- gait abnormality, movement abnormality, strabismus

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12
Q

bacterial meningitis

A

few days of fever and progresses to CNS symptoms ( HA, lethargy, irritability)

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13
Q

bacterial vs viral rhinosinusitis

A

*Bacterial more intense
fever more that 3 days,
symptoms 10 days or more
new or recurrent fever after improvement

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14
Q

Beckman Wiedmann Syndrome

What is is, now to monitor, tx?

A

gene disorder

Big Becky likes to get Big
-macrosomia -big head, macroglossia- big tongue
-organomegaly (big organs)
—-> big pancreas produces too much insulin =>hypoglycemia
—-> omphalocele: organs protrude from belly button cus too

likes to get big unevenly
- tumors: nephroblastoma, hepatoblastoma
- hemihypertrophy

Assessment
-abdominal US q3 months until 8 yo
-Alpha-fetoprotein q3 months until 4 yo

Tx. Frequent feedings, resection of tumor

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15
Q

biliary atresia

A

absence of extrahepatic biliary tree, commonly common bile duct
- billirubin can;t be excreted and builds up => Jaundice, scleral icterus

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16
Q

Blount Disease

A

bowlegs
-abnormality in medial aspect of proximal tibial epiphysis

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17
Q

Brudzinki sign

A

sigen for meningitis, knees flex when neck is flexed

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18
Q

Bun:Cr ratio in
pre-renal azotemia
intrinsic renal failure

A

> 20 (pre-renal)
<15 (“I” ntrinsic) I looks like 1

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19
Q

cause of viral meningitis in unvaccinated child
CSF values

A

mumps, elevated WBC & protein, low glucose

rubella can’t cause meningitis

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20
Q

Causes of membranous nephropathy

A

Infection ( Hep B, Hep C, Syphillis)

Malignancy
Autoimmune (Lupus, thyroiditis)
Drugs ( NSAIDS)

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21
Q

Chediak Higashi syndrome

A

phagocytic deficiency
oculocutaneous albinism, peripheral neuropathy, progresssive neurological dysfxn

CHEDIA-k
CNS abnormality
HEmorrhage
Decreased Immunity
Albinism

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22
Q

Child most with a hoarse voice, most likely had a mother who

A

had an active HPV infection,

lesion affected kid’s vocal cords

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23
Q

Chlamydia trachomatis pneumonia onset

A

4-12 weeks
typically afebrile and mild

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24
Q

cholesteatoma

A

keratinizing squamous epithelium grows from tympanic membrane or auditory canal to the middle ear mucosa or mastoid air cells

form of chronic otitis media

  • foul smelling discharge from ear, conductive hearing loss

-otoscope findings
1)retraction pocket that appears as a brown irregular man
2) pearly white mass behind tympanic membrane

Xray of mastoid process, CT of temporal bone
Tx: surgery

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25
Q

Chronic granulomatous disease

A

defectiveNADPH oxidase,
-susceptible to catalase positive organisms( s. aureus, nocardia, E Coli, candied, klebsielle, pseudomonas, aspergillus, serrait)

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26
Q

clinical features of congenital cytomegalovirus in utero

managment

A

fetal growth resticition, enlarged liver with multiple intrahepatic calcifications, bilateral periventricular intracranial calcifications

management is expectant or pregnancy termination

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27
Q

Common variable immunodeficiency

A
  • abnormal differentiation of B cells into plasma cells causes decreased immune globulin production ( no response to vaccinations, normal B cells)

=B cell defect

  • will see lots of infections, Giardia, PNA
  • TX: immunoglobulin replacement therapy
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28
Q

congenital rubella classic triad

A

CDC
-Cataract,
- sensorineual Deafness,
-Cardiac disease ( patent ductus arteriosis and pulmonary artery stenosis)

Other: fetal growth restriction, hepatomegaly

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29
Q

Congenital syphillis

A

Early <2 yo
hepatomegaly with jaundice,
Snuffles: Rhinorrhea with white or bloody discharge
pemphigus symphiliticus: bullous rash on palms and soles
skeletal abnormality
generalized lymph adepnopathy

Late> 2yoL
- saddle nose, frontal bossing, short maxilla
- hutchinson teeth, mulberry molar, syphillic keratitis, hearing loss
- saber shin ( bowing)
- CN 8 palsy, deafness, intellectual disability

other: PNA, hemolytic anemia, blueberry muffin spots

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30
Q

contraindications to breastfeeding

A

Baby Gotta HAV CASH TU
Baby Galactosemia
HIV
Active Varicella
Chemo or radiation therapy
A ctive Substance disorder
Herpestic Breast Untreated
active TB Untreated,

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31
Q

cornelia de lange syndrome

A

Bushy Syndrome
long curly eyelashes, hirsutism, short stature, microcephaly, VSD, undescended testes, confluent eyebrow(uni-brow)

intrauterine growth restriction, intellectual disability

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32
Q

cri du chat syndrome
cause and core symptoms

A

mutation of short arm of chromosome 5

think cat-chat: cries like a cat,
high pitched cry
microcephaly, intellectual disability
cardiac VSD

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33
Q

dactylitis is_________

sign of _______

A

symmetric swelling of hands and feet, can see low grade fever, soft tissue swelling on x-ray fo rearly stages

vaso-occlusion in sickle cell disease

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34
Q

Delayed separation of umbiilical cord is when
___, caused by?

A

umbilicial cord remains more than 1 month post partum

leukocyte adhesion deficiency type 1: genetic condition where defect in leukocytic chemotaxis results in decreased phagocytic activity

  • leukocytosis, but decreased neutrophils
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35
Q

Di Georges syndrome
Classic triad? symptoms

A

chromosome** 22**q11 microdeletion
Defective development of 3rd and 4th pharyngeal pouch
22 yr old George was a CATCH

Cleft Palate
Anomalous face: Micrognathia, dysplastic ears, hypoplastic wing of nose
Thymic Aplasia: T-cell deficiency
Cardiac Abnormalities (truncus arteriosus, Tetralogy of fallot)
Hypoparathyroidism, hypocalcemia with tetany

classic triad: loss of parathyroid, loss of thymus, congenital heart def

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36
Q

dialectal behavior therapy is for

A

treating emotional dysregulation and self-harm behaviors in borderline personality disorder

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37
Q

Digeorge Syndrome
cause

A

chromosome 22q11 microdeletion
Defective development of 3rd and 4th pharyngeal pouch

Catch 22
CATCH -22
Cleft Palate
Abnormal facies
Thymic Aplasia
Cardiac Abnormalities (truncus arteriosus, Tetralogy of fallot)
Hypocalcemia (no parathyroid)

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38
Q

diphtheria
features,
Physical exam finding

A

prodromal: fever malaise, sore throat (2-5 days)
Systemic: myocarditis, arrhythmmia, septic arthritis
Can be fatal

unique physical finding: grayish white pseudomembrane over posterior pharyngeal wall and/or tonsils

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39
Q

excess androgens, virilization, advanced bone age

A

adrenal tumor

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40
Q

Fanconi Anemia
What is it
clinical findings?
increases risk for?

A

Inherited DNA defect think
Fanconi: Diet Cafe with Abnormal TEA shrinks testes and kidneys

Deafness
Cafe Au lait
mAcrocytic or normocytic Anemia
Thumbs and Ears Abnormal
Atrophy of Testes and Kidneys

inc risk for AML and MDS

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41
Q

Febrile seizure age

A

6 months- 5 years

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42
Q

forward best test that shows asymmetric thoracic lumbar prominence is most likely _____

further evaluated via, and managed?

A

adolescent idiopathic scoliosis (AIS) , x-ray of spine

Cobb angle determines treatment
0-30: monitor
30 or greater: thoracolumbar spinal brace
40-50: surgical fixation

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43
Q

fragile x syndrome

A

X-tra large face, ears, testes
- learning disability
- joint hypermobility
large face with prominent ears, macrocephaly

Flat feet or pes planus
Regurgitation at mitral valve
Autism
Genitals giant after puberty
IQ low
Large face, head circumference
Ears protruding
X sensible joints

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44
Q

Friedrich ataxia

A

autosomal recessive disorder that causes degenerations of spinal tracts: spinocerebellar, posterior columns

FrieD Hassh: Friedrish
Symptoms:
Dysarthria( imparted speech),
Hypercardiotrophic myopathy
Ataxia(impaired gait),
loss of Sense of vibration/propioception,
Skeletal deformity: scoliosis
high arches

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45
Q

gastroschisis

A
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46
Q

Gaucher disease

A

Gaudy GiRl HaS Painted A Bone Meticulously on a Crumpled Tissue Paper

Glucocerebrosidase accumulation in leukocytees and fibroblasts
HepatoSplenomegaly
Pancytopenia
Avascular necrosis of femur
Bone Crisis
Macrophage inclusions that resemble crumpled tissue paper

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47
Q

gram diplococci contact precaution

A

neisseria meningitis

  • droplet
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48
Q

Hemolytic Uremic Syndrome

A

hematuria, low C3, acute kidney injury , Hg<8

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49
Q

Henoch Schloein purpura
IgA vasculitis

A

abodominal pain (intusseption)
pupura ( petechal rash on butt & leggs)
Arthralgia following URI

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50
Q

hereditary angioedema characterized by

cause and test?

A

cutaneous swelling , no urticaria or pruritis
abdominal pain, vomitting diarrhea

C1 inhibitor deficiecny will causes decreased levels of C4

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51
Q

how do you diagnose bacterial pharyngitis?

A

1) rapid step antigen
2) If negative, throat culture

causative organism Group A step
**don’t use antistreptolysin O antibody cuz it takes too long

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52
Q

how should a biliary cyst be managed?

A

surgical resection to decrease risk of malignancy

53
Q

HSV encephalitis

A

Triad:
-Focal neuro deficit (aphasia, memory loss, ataxia, altered smell)
-seizure
-altered mental status (confusion)

CSF: inc. lymphocytes, mild inc in protein normal glucose

54
Q

Bruton agammaglobulinemia

A
  • low levels of everything IgG, IgM, IgA, and B lymphocytes
    -recurrent sinopulmonary infections
55
Q

Hyper IgM Syndrome or Cd40 ligand deficiency4

A

recurrent sinopulmomary infections, frequent viral infection, inc risk for opportunistic infection

56
Q

hyperthermia sx and treatment

A

symptoms: dry hot skin, mental status changes, athletes may continue to sweat profusely

tx: agreesive cooling ie cold immersion therapy

57
Q

Idiopathic intracranial hemorrhage
signs
medications

A

meds: retinoids, tetracycline, growth hormone

signs: papilledema, headache, bilateral vision changes

vs cluster headache- no papilledema
vs optic neuritis: unilateral, no headache or vomiting

58
Q

In children with an open, full fontanelle and concerns of meningitis– would you image first or go straight to LP?

A

LP, no concern of elevated ICP rinse it’s open

59
Q

infants born to mothers with __________ are risk for thrombocytopenia

A

preeclampsia

60
Q

ITP management

A

Observe
- Children: if cutaneous symptoms only
- Adults: cutaneous symptoms and platelet greater than or equal to 30k
Glucocorticoids, IVIG, and anti-D
-Children: bleeding
-Adults: bleeding or platelet less than 30k

***If all tx given and still symptomatic splenectomy ( spleen recycles platelets and removal sometimes improves low platelet count)

61
Q

laryngomalacia

A

stridor worsens with feeding, crying and supine position

stridor improves with prone position since tongue moves anteriorly and relieves obstruction

62
Q

lead poisoning management

diagnosis and when to start therapy?

A

need 2 tests: capillary and venous
start chelations therapy if lead greater than or equal to 45 microgram/dl

63
Q

legs-calves perthes

A

vascular necrosis of femoral head
-presents as painless limp
onset2-12 yo

64
Q

manamgedment of pediatic patient older than 4 with anogenitial warts

A

sexual abuse assessment

65
Q

4manifestations of lupus

A

consitutitional: feverfstigue, wt loss
symmetric: migratory arthritis
Skin: butterfly rash, photosensitivity
serositisL pericarditis
thromboembolic events
neurologic: psychosis, seizures

Hemolytic anemia,
low c3, c4
AB: Anti dsDNA, Anti0Smith, ANA
renal involvement

66
Q

mass that forms in quadricep after trauma is most likely

A

myositis ossification or heteroscopic ossification

67
Q

McCune Allbirght Syndrome 3 P’s

A
  1. precocious puberty
  2. polyostotic fibrous dysplasia (normal tissue is replaced. by fibrous tissue causing x-ray changes)
  3. pigmentation Café-au-lait spots
68
Q

medicaitons that can casue serum sickness-like reaction

A

PCN, cefaclor, bactrim

69
Q

milia vs seborrheic dermatitis (SD) vs HSV

A

milia: unpoppable keratin plugs
- (SD) weepy rash of face and scalp

HSV: child is usually ill

70
Q

moa for drug-induce hemolysis

A

drug binds to RBS creating hapten for IgG attachment/ hemolysis

71
Q

neonatal teeth mangement

A

remove if its lose or interferes with feeding, if not just leave it (normal)

72
Q

Neonstal resuscitation whne to just to skin to skin

A

-term gestation, good, tone, breathing/cryin
- what to do if one of thsoe are not met
1) warmth airway, stimulate
2) If HR <100, initite positve pressure
3) If still bradycardia, CPR advanced resuscitation)

73
Q

nephrItic syndromes

A

I for Injury to kidney- blood and protein in urine,
drinking IPA beers kills kidney despite seeing DR
- IgA nephropathy, Post strep glomerulonephritis , Alport Syndrome
- Diffuse proliferative and Rapidly progressive glomerulonephritis

74
Q

Nephrotic syndrome

A

FM DAMM- keeps the peace so no blood seen
-Focal segmental glomerulonephritis, Membrane proliferative glomenrulonephritis
-Diabetes, Amyloidosis, Minimal Change Disease, Membranous Nephropathy

-

75
Q

Neurofibromatosis Type 1

A

Neurofibromas collect on skin, eyes, bones

CAFESPOT

Cafe Au lait spots
Axillary Freckles
Eye nodules
Skeletal Abonormalties
Pressure high
Optic Tumor
S short

76
Q

newborn how becomes rapidly ill with hypothermia tachycardia, tachypnea, hypotension, and respiratory distress most likely has

CXR: diffuse bilateral granulates

A

GBS PNA

77
Q

Niemann pick Disease

A

No Man Pictures the Sphinx PruNing HouSe Cherries
Niemann Pick Dx
Spingomyelinase deficinecy
Progressive neurodegeneration
Hepatosplenomegaly/ Areflexia (difference form tay sachs)
Cherry spots on macula

78
Q

osgood schlatter

A

overuse causes swelling of tibial tubercles

79
Q

osteogenesis Imperfecta

A

dec synthesis of collagen type causing brittle bones and hones hyperlaxity

can’t BITE only Juice
- Bones (reccurent fracture),
-I (“eye”= blue sclera),
-Teeth Abnormality (opalescent teeth)
-Ears (Hearing loss from faulty ossicles )
Joint Hypermobility

80
Q

otitis media with effusion features

when to plave tympasnostomy tubes?

A

mild discomfort (ear pulling)
air fluid levels posterior to TM, and poor TM mobility

tympanostomy tubesL OME> 3 months + hearing loss

81
Q

oxidative burst test is used to diagnose

A

chronic granulomatous disease

82
Q

papilledema

A

optic disc swelling secondary to elevated intracranial pressure

83
Q

patietn cystic fibrosis with PNA, that does not respond to antibiotics after 1 week, and a high IgE level most liekley has

A

allergic bronchopulmonary aspergillosis

84
Q

peritonsillar abscess features

A

large tonsil swelling with deviation of the uvula
- muffled voice

85
Q

pneumococcal-23 is given for

A

kids with high risk conditions ie sickle cell disease, immune deficiency, congenital heart disease

86
Q

prader wili syndrome

A

hypotonia, feeding difficulty (need NG tubein infancy(
-GU abnormality ( males, undescended testes)
-small hands or feet, short stature
-adolescence or adulthood: excessive eating and obese

deletion of 15q 11-134 on paternal side

87
Q

primary amenorrhea

A

no sex chracteristics and no menses AGE 13 OR OLDER

-sex chracteristics but no menses age 15 or older

88
Q

Primary amenorrhea, breast present, but uterus absent

A
  1. mullerian agenesis ( 46,xx) mullerian structures just don’t form, normal testosterone 2. Androgen insensitivity syndrome (46, xy) male but no androgen receptor so will see no pubic hair
89
Q

primary amenorrhea: no breasts, no uterus

A

17 alpha hydroxylase 46,XY

90
Q

primary amenorrhea: no breasts, uterus present

A
  1. no ovarian follicle top produce sex steroid, estrogen ( FSH high) GT17 Gonadal Dysgenesis, Turner Syndrome 17alpha-Hydroxylase deficiency 46(,XX) 2. HPA Axis disorder, low (FSH from lack of GnRh secretion) Kallman Syndrome, lesion in brain
91
Q

patient with no iris
hypospadias, one undescended testes is a riskfor?

A

willms tumor: delestion f of chromosome 11p13
WAGR Syndrome
wilms tumor
aniridia
genitourinary abnormality
mental Retardation

92
Q

pubertal gynecomastia

features, management

A
  • occurs in tanner stage 304 due to imbalance of estrogen
    -features: small < 4cm, firm
  • no pathologic features: nipple discharge, axillary lymphadenopathy, systemic illness

management: reassurance and observation, should resolve in a yr

93
Q

rett Syndrome

A

x-linked dominant ret Reggresses

MECP2 gene mutation, deceleration of brain growth

Lost of speech, gait abnormality, hand wringling, microcephaly

94
Q

Risk Factors for Scoliosis Progression

A

CSAFE
cob angle greater than or equal to 25 degree
skeletal immaturity
Age< 12 yo
female
early prepubertal status, premenarchal

95
Q

scalp hands and feet
what is this?

A

crusted scabies

96
Q

septic arthritis symptoms and treatment

A

ill appearing, acute hip pain, fever, inability to bear weight

-vancomycin

97
Q

child with fever, rash(below), arthralgia (pain in joints most likely has?

A

Serum sickness-like reaction or Serum sickness reaction

98
Q

side effect with lithium use in pregnancy

A

Epstein Anomaly: malformed tricuspid valves that are displaced into the RV with subsequent

**TV regurgitation **and right heart enlargement

99
Q

side of retinoid derivatives in pregnancy

A

-microtia (underdevelopment of pinna in ear leads to hearing impairment)
-congenital CNS effects: hydrocephalus, microcephaly, cortical blindness
-congenital heart disease: vessel anomalies

100
Q

SLE lab values

A

decreeased complement 1q, 2, 3,4, CH50
increased cr

101
Q

slipped cap femoral epiphysis

A

obese child with a limp

limited internal rotation of hip with waddling gait

femoral head is separated from neck and femur moves anteriorly

102
Q

spastic diplegia vs tethered cord vs transverse myelititis

A

tethered cord has. lower extremity motor neuron signs ( hyporeflexia, weakness), foot deformity
spastic diplegia: upper motor neuron sign hyperreflexia

transverse myelitis: weakness, bladder dysfunction but no foot deformity

103
Q

strength training can be done in children who are

A

8 years and older
cognitively mature

104
Q

Tay Sachs Disease

A

After they hexed tay;;s Sax he becasem deficent
hexosaminidase A deficiency
Developmental delay, hypotonia,
hyperreflexia seizure
cherry red spot on macula

105
Q

TB meningitis lasts

A

6months- 4yrs of life
- week 1-2: irritable, listless, anorectic
- second stage: seizure, lethary, hypertonicity, hydrocephalus, focal neuro signs
-3rd stage: coma, hypertension, posturing, decompensation, death

diagnostic : increase adenosine deaminase (ADA) activity

106
Q

transient synovitis feeatures

vs. SCFE

A

vs SCFE affects younger age 3-8yo

107
Q

Transfusion associated circulatory overload

TACO

A

when blood is transfused in someone who has underlying anemia causes volumes overload
- will see respiratory distress, volume overload,
-s3 gallop, JVD, hypertension pulmonary edema

management : diuresis, oxygenation

108
Q

transfusion related acute lung injury

TRALI

A

prior to transfusion, host has neutrophils in lungs => donor blood activates those cells , pro-inflmmatory markers released, pulmonary edema

-hypotension, fever, leukopenia, thrombocytopenia

management: aggressive supportive care, ventilator, pressers
NO S3 gallop

109
Q

treatment for OCD

A

SSRI and cognitive behavioral therapy

110
Q

treatment of anal pinworn

A

pyrantel pamoate, albendazole

111
Q

trisomy 13

A

failure to thrive, cleft lip, aseizures, palate , congenital heart disease

low survival

112
Q

Turner Syndrome Symptoms

A

Horse CLOWNS
Horseshoe kidney
Cardiac abnormality: aortic coarctation or bicuspid aorta
Lymph adenopathy
Ovary nonexistent
W ebbed neck
Nipples wides spaced and Nails dysplastic
Short stature

113
Q

Turner syndrome karyotype

A

45,xo - partial deletion of x chromosome results in gonadal dysgenesis
-short stature,
-FSH ,and LH high

114
Q

VATER

A

or VACTERL, normal intelligence

3of the following:
Vertebral defect,
Anal atresia/ imperforate anus
Cardiac defect
TracheoEsophageal fistula
Renal/radial defect
Limb abnormalities ( fusion of fingers, too little or too many fingers, long bones)

115
Q

vesicoureteral reflux- what is it?
- complications
-presentation

A

retrograde flow of urine through ureter
-febrile UTI
-if untreated can renal scarring, CKD, and recurrent pyelonephritis

116
Q

44Vin Hippel Lindau Diisease symtoms

A

mutation of VHL - tumro suppresoors

-cerebellar & retinal hemiangioblastoma
-phreochromocytoma
-renal cell carcinoma (clear cell)

117
Q

what is congenital dacryostenosis

A

nasolacrimal duct obstruction
- duct fails to form resulting in blocked tear flow
-fluorescein testL dye persists and flows down cheek vs abrasion where ther would only be disrete staining

118
Q

what is this and mangemnt?

A

molluscum contagious
just watch it, shoudl self resolve

119
Q

what is this?

A

Right upper lobe atelectasis
linera density with associated shooting of mediastinum towards collapsed lung

120
Q

what is this?

A

clasisc scabies

121
Q

what is this?

A

impetigo

122
Q

what is this?

A

Kawasaki disease

unknown cause: genetic or infectious

-cervical lymphadenopathy unilateral

CRASH and BURN
Conjuntivitis, Rash, Adenopathy, Strawberry tongue Hands and feet swelling

BURN (fever for at least 5 days)

123
Q

what is this?

A

psoriasis

124
Q

4what is this? mangement?

A

neurofibromatosis type 1
NF1 genetic test to confirm

125
Q

what’s marked not he chest x ray?

A

sail sign; thymus
- could be absent in Di George Syndrome

126
Q

clinical features of developmental hip dysplasia

A

Red flags: + ortolani test, dislocated hip, limited hip abduction
supportive: limb-length discrepancy, asymmetric gluteal inguinal/thigh creases

treatment pavlik harness

127
Q

which blood pressure measurement method is the most accurate?
auscultation or oscillometric?

A

ausculation

128
Q

why would someone with sickle cell disease have Howell-jolly bodies?

A

episodes if vasoocculusive pain crisis leads to autoinfarction of the sleep and functional asplenia
- spleen no longer remove nuclear remnants of RBC (Howell-jolly body)

129
Q

Wiskott Aldrich Syndrome

A

bleeding due to microthrombocytopenia, recurrent infections, and eczema

  • low platelet count

Pediatrics (10 decks)

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