ERYTHROCYTES Flashcards

1
Q

What test is RARELY DONE because of its inaccuracy and questionable necessity?

A

RBC COUNT

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2
Q

RBC METABOLIC PATHWAYS:

NON-OXIDATIVE, ANAEROBIC PATHWAY

A

EMBDEN-MEYERHOF PATHWAY

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3
Q

RBC METABOLIC PATHWAYS:

Glucose penetrates the red blood cell with NO ENERGY EXPENDITURE via what transmembrane protein?

A

GLUT-1

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4
Q

RBC METABOLIC PATHWAYS:

What pathway handles 90% OF GLUCOSE UTILIZATION in RBCs?

A

EMBDEN-MEYERHOF PATHWAY

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5
Q

How many molecules of ATP does the EMP produce?

A

2 MOLECULES OF ATP

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6
Q

MOST COMMON ENZYME DEFICIENCY IN THE EMP

A

PYRUVATE KINASE DEFICIENCY

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7
Q

MOST COMMON form of HEREDITARY NONSPHEROCYTIC HEMOLYTIC ANEMIA (HNSHA)

A

PYRUVATE KINASE DEFICIENCY

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8
Q

What kind of disorder is PK deficiency?

A

AUTOSOMAL RECESSIVE (AR)

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9
Q

possible PBS findings in PK deficiency include what cells?

A

ACANTHOCYTES, BURR CELL

“siya daw mag P(a)Y sa CAN sa EMPe”

PYRUVATE KINASE, ACANTHOCYTES, EMP

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10
Q

RECOMMENDED SCREENING TEST for PK deficiency

A

PK FLUORESCENT SPOT TEST

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11
Q

CONFIRMATORY TEST for PK deficiency

A

QUANTITATIVE PK TEST

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12
Q

what shunt is also known as the Pentose Phosphate Pathway or Phosphogluconate Pathway?

A

HEXOSE MONOPHOSPHATE SHUNT

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13
Q

HMP is also known as?

A
  1. PENTOSE PHOSPHATE PATHWAY
  2. PHOSPHOGLUCONATE PATHWAY
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14
Q

AEROBICALLY converts GLUCOSE to PENTOSE

A

HEXOSE MONOPHOSPHATE SHUNT

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15
Q

end-product of HMP

A

NADPH (Nicotinamide Adenine Dinucleotide Phosphate (reduced))

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16
Q

NADPH reduces what substance?

A

GLUTATHIONE

17
Q

pathway that PREVENTS the DENATURATION of GLOBIN BY OXIDATION

A

HEXOSE MONOPHOSPHATE SHUNT

18
Q

MOST COMMON ENZYME DEFICIENCY in the Pentose Phosphate Pathway

A

G6PD DEFICIENCY

19
Q

MOST COMMON RBC ENZYME DEFECT

A

G6PD DEFICIENCY

20
Q

what kind of disorder is G6PD?

A

X-LINKED RECESSIVE (XLR)

21
Q

possible PBS findings for G6PD DEFICIENCY

A
  1. HEINZ BODIES
  2. BITE CELLS
22
Q

RECOMMENDED SCREENING test for G6PD DEFICIENCY

A

G6PD FLUORESCENT SPOT TEST

23
Q

CONFIRMATORY TEST for G6PD DEFICIENCY

A

QUANTITATIVE G6PD ASSAY

24
Q

what class of G6PD is FAVISM or FAVA BEANS associated with?

25
Class II variants of G6PD where Favism is related to
1. G6PD-MEDITERRANEAN 2. G6PD-CHATHAM | mostly related with G6PD-MEDITERRANEAN ang FAVISM :)
26
pathway that **MAINTAINS IRON IN THE HEME** in its **REDUCED STATE**
METHEMOGLOBIN REDUCTASE PATHWAY
27
Methemoglobin Reductase Pathway is also known as
CYTOCHROME B5 REDUCTASE
28
Pathway for the **PRODUCTION OF 2,3-DPG**
RAPOPORT-LUEBERING PATHWAY
29
what binds to the Hb and **DECREASES THE O2 AFFINITY OF Hb**?
2,3-DPG
30
a shift in the curve due to an **ALTERATION IN pH**
BOHR EFFECT
31
depicts the occurrence by which the binding of O2 to the hemoglobin promotes the release of CO2
HALDANE EFFECT
32
# SHIFT TO RIGHT OR LEFT: **INCREASED AFFINITY**
SHIFT TO THE LEFT | kapit jud teh para di ka ma "left" behind 🤩
33
**DECREASED AFFINITY**
SHIFT TO THE RIGHT | let go na because it's the "right" thing to do 😞
34
**INCREASED pH**
SHIFT TO THE LEFT
35
shape of the curve in Oxygen Dissociation Curve
SIGMOIDAL