ENCEPHALOTRIGEMINAL ANGIOMATOSIS (STURGE-WEBER SYNDROME) Flashcards

1
Q

CONCEPT

A

UNCOMMON CONGENITAL DISORDER

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2
Q

CHARACTERISTICS

A

PORT-WINE BIRTH STAIN AND NEUROLOGICAL ABNORMALITIES

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3
Q

PORT-WINE STAINS

A

MACULAR HEMANGIOMA THAT FOLLOWS THE DISTRIBUTION OF THE TRIGEMINAL NERVE

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4
Q

PLACES

A

UNDERLYING MENINGES AND CEREBRAL CORTEX

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5
Q

NEUROLOGICAL PROBLEMS

A
  • SEIZURE AND INTELLECTUAL DISABILITIES
  • GLAUCOMA
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6
Q

INTRAORALLY CLINICALLY

A
  • HYPERVASCULAR CHANGES TO THE IPSILATERAL MUCOSA
  • GINGIVA EXHIBIT SLIGHT VASCULAR HYPERPLASIA (INCREASED VASCULAR COMPONENT, ANTICONVULSANT TERAPY OR BOTH)
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