ENCEPHALOTRIGEMINAL ANGIOMATOSIS (STURGE-WEBER SYNDROME) Flashcards
1
Q
CONCEPT
A
UNCOMMON CONGENITAL DISORDER
2
Q
CHARACTERISTICS
A
PORT-WINE BIRTH STAIN AND NEUROLOGICAL ABNORMALITIES
3
Q
PORT-WINE STAINS
A
MACULAR HEMANGIOMA THAT FOLLOWS THE DISTRIBUTION OF THE TRIGEMINAL NERVE
4
Q
PLACES
A
UNDERLYING MENINGES AND CEREBRAL CORTEX
5
Q
NEUROLOGICAL PROBLEMS
A
- SEIZURE AND INTELLECTUAL DISABILITIES
- GLAUCOMA
6
Q
INTRAORALLY CLINICALLY
A
- HYPERVASCULAR CHANGES TO THE IPSILATERAL MUCOSA
- GINGIVA EXHIBIT SLIGHT VASCULAR HYPERPLASIA (INCREASED VASCULAR COMPONENT, ANTICONVULSANT TERAPY OR BOTH)