Cyanotic Defects Flashcards
1
Q
Cyanotic congenital heart diseases
A
Tetralogy of fallot Transposition of great vessels Tricuspid atresia Truncus arteriosus Trilogy of fallot Total anomalous pulmonary venous return Ebstein's disease Eisenmenger's syndrome
2
Q
What is the primary defect in tetralogy of fallot?
A
Anterior deviatoon of the infundibular septum (muscular septum separating the aortic and pulmonary outflow)
3
Q
What are the four characteristics components of TOF?
A
- large subaortic VSD
- overriding aorta
- RV outflow tract obstruction (infundibular pulmonary stenosis)
- RV hypertrophy
4
Q
What are the manifestations of TOF?
A
Cyanosis
Hypoxic spells
Easy fatigability
5
Q
Clinical features of TOF
A
- cyanosed (depends on severity of pulmonary stenosis)
- retardes growth, but not mental devt
- clubbing
- squatting (lessens R to L shunting by increasing systemic vascular resistance; RV outflow tract relaxes, more blood oxygenated to the lungs)
- cyanotic spells
- hyperpnea
6
Q
Malformations in TOF
A
- pulmonary stenosis
- VSD
- dextroposition of aorta
- RV hypertrophy
- ASD (pentalogy of fallot)
