Congenital Heart Disease

Question 1

How do you identify LV and RV in a congenitally malformed heart?

Answer 1

LV will have septophobic papillary muscles

No septal papillary muscles In LV

Question 2

What are the predictors of SCD in patients with TOF?

Answer 2

RBBB >170ms
Severe PR
NSVT

Question 3

What are the complications of Eisenmenger syndrome?

Answer 3

Hyperviscosity 
Bleeding
Call stones
Gout 
Stroke 
Cerebral abscess 
Heart failure 
Sudden cardiac death

Question 4

What is the three year survival of patients with Eisenmenger Syndrome?

Answer 4

80%

Question 5

Management of Eisenmenger Syndrome

Answer 5

Phlebotomy only for symptomatic hyperviscosity
Pulmonary vasodilators

Suggest avoid warfarin because increased bleeding risk

Question 6

What is the formula to assess shunt size?

Answer 6

QP:QS

Aortic Oxygen - Mixed Venous Oxygen)/(Pulmonary Vein Oxygen-Pulmonary Artery

Question 7

What is a significant QP:QS?

Answer 7

1.5 : 1 or more

Question 8

What is the rate of residual hypertension after coarctation repair?

Answer 8

30%

Question 9

What are the causes of cyanotic heart disease?

Answer 9

Transposition 
Tetralogy 
Truncus arteriosus 
TAPVR
Tricuspid atresia