Congenital Heart Abnormalities Flashcards
Heart anomalies are the most common congenital anomaly in newborns. What % of newborns are born with congenital anomalies?
1 - 1%
2 -15%
3 - 40%
4 - 60%
1 - 1%
Leading cause of infant mortality in among birth defects
What % of liveborn infants have significant cardiac malformations?
1 - 8 per 1000
2 - 300 per 1000
3 - 50 per 1000
4 - 800 per 1000
1 - 8 per 1000
- 30% of these patients will require intervention in the first year of life.
What % of still births are thought to be due to congenital anomalies?
1 - 1%
2 - 10%
3 - 30%
4 - 60%
2 - 10%
Congenital heart anomalies can be due to a variety of reasons, including maternal disorders, maternal drugs or Chromosomal abnormalities. All of the following are maternal disorder that can lead to congenital heart anomalies, EXCEPT which one?
1 - Rubella
2 - SLE
3 - Diabetes Mellitus
4 - Bacterial vaginosis
4 - Bacterial vaginosis
Congenital heart anomalies can be due to a variety of reasons, including maternal disorders, maternal drugs or Chromosomal abnormalities. Which 2 of the following can lead to congenital heart anomalies?
1 - Warfarin
2 - Alcohol
3 - NSAIDs
4 - Apixiban
1 - Warfarin
2 - Alcohol
Congenital heart anomalies can be due to a variety of reasons, including maternal disorders, maternal drugs or chromosomal abnormalities. Which of the following is NOT a common chromosomal abnormality that leads to congenital heart anomalies?
1 - Down Syndrome
2 - Edward or Patua Syndrome
3 - Turners Syndrome
4 - Type 1 diabetes
4 - Type 1 diabetes
In the growing foetus there are 4 key adaptations to the foetal circulatory system:
- umbilical veins and arteries in the umbilical cord
- ductus venosus
- foramen ovale
- ductus arteriosus
Which if these 4 adaptations allows oxygenated blood to be carried from the foetus to maternal circulation and the liver?
- umbilical veins and arteries in the umbilical cord
This blood enters all the lobes of the liver and becomes de-oxygenated
In the growing foetus there are 4 key adaptations to the foetal circulatory system:
- foramen ovale
- umbilical veins and arteries in the umbilical cord
- ductus arteriosus
- ductus venosus
In addition to carrying oxygenated blood to the liver, what forms off the left umbilical vein, bypassing the liver and drains into the inferior vena cava as a second adaptation?
- ductus venosus
This oxygenated blood mixes with de-oxygenated blood from the lower limbs
By bypassing the liver this delivers oxygenated blood to the left heart for systemic circulation and to the res tof the body
Congenital heart disease can be classified as cyanotic and acyanotic. In acyanotic congenital heart disease is there sufficient oxygen?
- Yes oxygen level is ok
But blood is being pumped around the body in an abnormal manner
- left to right shunt
- obstruction
Which of the following is NOT a cause of cyanotic congenital heart disease?
1 - Tetralogy of Fallot
2 - Transposition of the great arteries
3 - Tricuspid / pulmonary atresia
4 - Ventricular septal defect
5 - Persistent truncus arterious
6 - Total anomalous pulmonary venous return
4 - Ventricular septal defect
Tetralogy of Fallot:
- a heart composed of four different heart problems: ventricular septal defect, overriding aorta, pulmonary stenosis and right ventricular hypertrophy.
All of the following are causes of acyanotic congenital heart disease caused by aobstruction, EXCEPT which one?
1 - Pulmonary Stenosis(7%)
2 - Aortic Stenosis (5%)
3 - Co-arctation of the aorta(5%)
4 - Hypoplastic left heart syndrome
5 -Tetralogy of Fallot
5 -Tetralogy of Fallot
Of all the causes of congenital heart disease below, which is by far the most common, accounting for 30% of all cases?
1 - Tetralogy of Fallot
2 - Transposition of the great arteries
3 - Ventricular septal defect
4 - Patent ductus arteriosus
5 - Atrial septal defect
3 - Ventricular septal defect
This is a acyanotic congenital heart disease causing a left to right shunt
There are some ductal-dependent congenital heart diseaseconditions that are dependent on the ductus arteriosus remaining open to maintain systemic blood flow, including:
- Hypoplastic left heart syndrome
- Critical aortic stenosis
- Coarctation of the aorta
- Pulmonary atresia or severe tetralogy of Fallot
What are patients given to keep the ductus arteriosus open until they can receive surgery?
1 - prostaglandins
2 - surfactant
3 - corticosteroids
4 - aspirin
1 - prostaglandins
This is what keeps it open during foetal development
Which of the following is NOT a typical presentation in a baby with suspected congenital heart defect at birth?
1 - Heart murmur
2 - Heart failure
3 - Liver failure
4 - Shock
5 - Cyanosis
3 - Liver failure
Babies may also present with a soft murmur, which may not be congenital heart disease and this would have the following features:
- Systolic murmur only
- Left Sternal edge.
normal heart sounds, no added sounds - No parasternal thrill
- No radiation.
Babies with congenital heart defects can also suffer from heart failure. Which of the following is NOT a common symptom in a baby with suspected heart failure?
1 - Breathlessness (particularly on feeding or exertion)
2 - Sweating
3 - Haemoptysis
4 - Poor feeding
5 - Recurrent chest infections
3 - Haemoptysis