CONGENITAL ANOMALIES GIT Flashcards

1
Q

Congenital anomalies of git

A

TEF
IHPS
Duodenal atresia
Meckels diverticulum
Hirschsprung disease

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2
Q

Ass of TEF with esophageal atresia

A

85%

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3
Q

Name of classification for TEF

A

Gross
Type C most common 85%

Type D least common 1%

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4
Q

Type C TEF

A

Proximal esophageal atresia + distal TEF

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5
Q

Most common cause of death in TEF BABIES

A

Aspiration pneumonia, also most common complication

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6
Q

🌟VACTERL association of TEF

A

Vertebral anomalies
Anal atresia
CHD
TEF
renal ABN
Limb defect

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7
Q

IHPS association

A

Jaundice ( ictero pyloric synd) decreased UDP GT

Erythromycin in first 2 weeks of life

M:F= 4:1

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8
Q

IHPS IOC

A

USG abd

Thickness of pylorus >=3-4 mm

Length of pyloric canal >16 mm

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9
Q

IHPS brarium meal signs 🌟MDSS

A

Mushroom sign
Double track sign
String sign
Shoulder sign

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10
Q

Dehydration correction in IHPS

A

1/2 NS + RINGER LACTATE / K+

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11
Q

Complication of IHPS

A

Hypokalemic
Hypochloremic
Metabolic alkalosis

Paradoxical aciduria

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12
Q

Most common site for DA

A

Distal D2

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13
Q

DA DEFN

A

Failure of recanalization of duodenal lumen

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14
Q

Double bubble sign

A

X ray feature

DA
Annular pancreas

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15
Q

DA association

A

Downs syndrome - most common 30%

Prematurity
CHD

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16
Q

Most common cause of intestinal obstruction in neonate

A

DA

17
Q

Most common GIT ANOMALY

A

Meckels diverticulum

18
Q

Surgical mgt of IHPS

A

Ramstedts pyloromyotomy

19
Q

Meckels diverticulum DEFN

A

Remanent of Omphalomesentric or vitellointestinal duct

20
Q

MD - True diverticulum . How ?

A

All layers are present

21
Q

Rule of 2’s in M DIVERTICULUM (6)

A

Size= 2 inches
Location - 2 feet away from illeocecal junction
Lined by 2 ectopic mucosa - gastric and pancreatic
Age < 2 yr
M: F = 2:1
If symptoms presents <=2 yrs ( painless rectal bleed )

22
Q

IOC for Meckels diverticulum

A

Technitium 99 petecnetate scan

23
Q

Association in hirschsprung disease

A

Downs syndrome
Mutation in RET PROTOONCOGENE
M:F=4:1

24
Q

Hirschsprung disease IOC

A

Rectal biopsy

25
Q

MC site of hirschsprung disease

A

Rectosigmoid
80%= shirt segment disease
15%= long segment dis
5%= entire colon

26
Q

Features on rectal biopsy in hirschsprung disease

A

Hypertrophy nerve fibres
Acetylcholinesterase staining
Calretinin staining

27
Q

Mgt techniquines in hirschsprung disease

A

Duhamel procedure
Soave technique ( disease part of epithelium is striped off and normal mucosa is tied on to it )