congenital

Question 1

how many phases of developemtn

Answer 1

4

Question 2

weeks 1-5

Answer 2

embryonic

Question 3

foregut development

Answer 3

day 9 endoderm

Question 4

lung buds

Answer 4

week 4

Question 5

mainstem bronchi and trachea

Answer 5

week 5

Question 6

weeks 5-16

Answer 6

pseudoglandular stage

Question 7

last event in pseudoglandular

Answer 7

PA and bronchial tree

Question 8

weeks 16-26

Answer 8

cannicular stage

Question 9

last event in cannicular

Answer 9

PV

Question 10

weeks 26-40

Answer 10

terminal sac, production of surfactant

Question 11

when does acinar production stop

Answer 11

8 years of age

Question 12

airway diameter increases until

Answer 12

5 years of age

Question 13

period of rapid growth of length of vasculature

Answer 13

18 months

Question 14

Most common TEF

Answer 14

Type C EA with distal TEF

Question 15

how to reduce chance of recurrence after TEF repair

Answer 15

interposition muscle flap

Question 16

ELS or ILS more problematic

Answer 16

ELS (25%)

Question 17

congenital lobar emphyesema lobes

Answer 17

LUL> RUL> RML

Question 18

cause of CLE

Answer 18

cartilaginous defect, or extrinsic compression, often no identifiable cause

Question 19

are CLE symptomatic at BIRTH

Answer 19

no

Question 20

is prompt treatment required of symptomatic CLE

Answer 20

yes, 50% dead at 1 week

Question 21

can asymptomatic CLE be observed

Answer 21

yes, 50% normalize at infancy

Question 22

CCAM type 1

Answer 22

mediastinal shift, rare to be associated with other anomalier, half will develop PNA, prognosis good

Question 23

CCAM type 2

Answer 23

mostly premature and stillborn, small cysts

Question 24

CCAM type 3

Answer 24

most commonly LLL, prognosis poor usually hours after birth

Question 25

asymptomatic CCAM

Answer 25

observe until 6 months, usually a lobectomy

Question 26

Tracheal stenosis type 1

Answer 26

entire thing

Question 27

Tracheal stenosis type 2

Answer 27

funnel shaped

Question 28

Tracheal stenosis type 3

Answer 28

segment

Question 29

associated vascular ring with tracheal stenosis

Answer 29

pulmonary vascular ring

Question 30

how many rings before autograft for tracheal stenosis can be removed

Answer 30

8 and need ecmo postoperatively

Question 31

how much can you pull together in neonatal tracheal resection

Answer 31

up to 50% and closed primarily