congenital Flashcards
how many phases of developemtn
4
weeks 1-5
embryonic
foregut development
day 9 endoderm
lung buds
week 4
mainstem bronchi and trachea
week 5
weeks 5-16
pseudoglandular stage
last event in pseudoglandular
PA and bronchial tree
weeks 16-26
cannicular stage
last event in cannicular
PV
weeks 26-40
terminal sac, production of surfactant
when does acinar production stop
8 years of age
airway diameter increases until
5 years of age
period of rapid growth of length of vasculature
18 months
Most common TEF
Type C EA with distal TEF
how to reduce chance of recurrence after TEF repair
interposition muscle flap
ELS or ILS more problematic
ELS (25%)
congenital lobar emphyesema lobes
LUL> RUL> RML
cause of CLE
cartilaginous defect, or extrinsic compression, often no identifiable cause
are CLE symptomatic at BIRTH
no
is prompt treatment required of symptomatic CLE
yes, 50% dead at 1 week
can asymptomatic CLE be observed
yes, 50% normalize at infancy
CCAM type 1
mediastinal shift, rare to be associated with other anomalier, half will develop PNA, prognosis good
CCAM type 2
mostly premature and stillborn, small cysts
CCAM type 3
most commonly LLL, prognosis poor usually hours after birth
