CLIPP 26 - CF Flashcards

1
Q

FTT criteria (3)

A

Any of:

  • weight below 3rd percentile
  • weight for height/length less than 3rd percentile
  • downward crossing of two or more major percentiles
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2
Q

FTT causes (8)

A
  • chronic diarrhea/vomiting
  • CHF
  • formula allergy
  • improperly prepared formula
  • inadequate formula volume
  • malabsorption
  • parental neglect
  • severe gastroesophageal reflux
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3
Q

CF genetics

A

autosomal recessive

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4
Q

Average daily weight gain up to 4 months

A

20-30g/day (~1oz/day)

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5
Q

When should birth weight be doubled?

A

By 4 months

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6
Q

Organic FTT causes (underlying pathology)

A
  • congenital heart defects
  • CF
  • developmental delay with poor suck/swallow
  • renal tubular acidosis
  • milk protein allergy
  • HIV
  • vomiting d/t reflux or bowel obstruction
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7
Q

Non-Organic FTT Causes (inadequate caloric intake)

A
  • poverty
  • poor feeding technique
  • improperly prepared formula
  • inadequate supply of breast milk
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8
Q

Daily caloric intake for first 4 months

A

100-110cal/kg/day

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9
Q

Normal infant RBC values (birth and 2 months)

A

Birth: 16.5 g/dL

2 months: 11.2 g/dL (physiologic anemia)

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10
Q

CF treatment plan

A
  • nutritional management (enzymes, vitamins, calories)
  • airway clearance
  • treatment of airway infections
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11
Q

Labs for FTT evaluation

A
  • CBC (anemia, infection)
  • Urinalysis (renal dysfunction, infection)
  • BUN/Cr (renal function)
  • Others: electrolytes (hydration, renal function, acid/base status), sweat test (CF), occult blood (milk protein intolerance), xray (cardiomegaly/pulmonary infilatrates), fecal fat analysis (malabsorption), fecal elastase (pancreatic insufficiency), LFTs (infection, biliary obstruction), neonatal screen, O&P (parasite), stool culture (salmonella, campylobacter), TSH (hypothyroid)
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12
Q

DDX FTT

A
  • CHF (difficulty feeding, respiratory distress)
  • Formula allergy (intestinal blood loss, fussiness, vomiting)
  • gastroenteritis (vomiting, diarrhea, fever, bloody stool)
  • hypothyroidism (poor feeding, constipation)
  • malabsorption (loose stools, good caloric intake)
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