CLIPP 26 - CF Flashcards
1
Q
FTT criteria (3)
A
Any of:
- weight below 3rd percentile
- weight for height/length less than 3rd percentile
- downward crossing of two or more major percentiles
2
Q
FTT causes (8)
A
- chronic diarrhea/vomiting
- CHF
- formula allergy
- improperly prepared formula
- inadequate formula volume
- malabsorption
- parental neglect
- severe gastroesophageal reflux
3
Q
CF genetics
A
autosomal recessive
4
Q
Average daily weight gain up to 4 months
A
20-30g/day (~1oz/day)
5
Q
When should birth weight be doubled?
A
By 4 months
6
Q
Organic FTT causes (underlying pathology)
A
- congenital heart defects
- CF
- developmental delay with poor suck/swallow
- renal tubular acidosis
- milk protein allergy
- HIV
- vomiting d/t reflux or bowel obstruction
7
Q
Non-Organic FTT Causes (inadequate caloric intake)
A
- poverty
- poor feeding technique
- improperly prepared formula
- inadequate supply of breast milk
8
Q
Daily caloric intake for first 4 months
A
100-110cal/kg/day
9
Q
Normal infant RBC values (birth and 2 months)
A
Birth: 16.5 g/dL
2 months: 11.2 g/dL (physiologic anemia)
10
Q
CF treatment plan
A
- nutritional management (enzymes, vitamins, calories)
- airway clearance
- treatment of airway infections
11
Q
Labs for FTT evaluation
A
- CBC (anemia, infection)
- Urinalysis (renal dysfunction, infection)
- BUN/Cr (renal function)
- Others: electrolytes (hydration, renal function, acid/base status), sweat test (CF), occult blood (milk protein intolerance), xray (cardiomegaly/pulmonary infilatrates), fecal fat analysis (malabsorption), fecal elastase (pancreatic insufficiency), LFTs (infection, biliary obstruction), neonatal screen, O&P (parasite), stool culture (salmonella, campylobacter), TSH (hypothyroid)
12
Q
DDX FTT
A
- CHF (difficulty feeding, respiratory distress)
- Formula allergy (intestinal blood loss, fussiness, vomiting)
- gastroenteritis (vomiting, diarrhea, fever, bloody stool)
- hypothyroidism (poor feeding, constipation)
- malabsorption (loose stools, good caloric intake)