Chronic Restrictive Pulmonary Disease

Question 1

What is considered extrapulmonary?

Answer 1

Muscle, nerve, spinal cord, musculoskeletal, pleural

Question 2

What is considered intrapulmonary?

Answer 2

Interstitial fibrosis, cancers, vascular disease, resections, radiation

Question 3

What are some known causes of pulmonary fibrosis?

Answer 3

Rheumatoid arthritis, silicosis, asbestosis, idiotpathic

Question 4

What is Bronchiectasis?

Answer 4

A triggered event from severe acute infection and is localised dilation of part of the bronchial tree

Question 5

What are some treatments for Bronchiectasis?

Answer 5

Postural drainage, exercise, anti-biotics, anti-mucolytic agents, bronchodilators

Question 6

True or false, people with CRPD and score <207m in the 6MWT have a higher chance of mortality compared to norm

Answer 6

True! 4 times more likely

Question 7

What are some special considerations when exercising in this population?

Answer 7

Worsening hypoxia, bronchodilators on hand, some may need supplemental O2 to remain about 90% SpO2

Question 8

Explain extrapulmonary in CRPD.

Answer 8

Extrapulmonary -> lung is intrinsically normal -> greatly increased respiratory effort, overcome stiffening, increased dead space -> secondary alveolar collapse and fibrosis (no longer springy and stretchy) -> impaired O2/CO2 transfer

Question 9

Explain intrapulmonary in CRPD.

Answer 9

Intrapulmonary -> parenchymal destroyed, alveoli capillaries fibrosis -> replaced with fibrous tissue (increased vascular resistance -> impaired O2/CO2 transfer