CHOANAL ATRESIA Flashcards
This is the most common congenital anomaly of the nose
CHOANAL ATRESIA
CHARGE syndrome one of the more common anomalies associated with it:
- Coloboma: in one of the structures of the eye
- Heart disease
- Atresia choanae
- Retarded growth and development or CNS anomalies or both
- Genital anomalies or hypogonadism or both
If unilateral,
may be asymptomatic for a prolonged period, often until the 1st respiratory infection( unilateral nasal discharge or persistent nasal obstruction)
If bilateral ,
difficulty with mouth breathing make vigorous attempts to inspire, often suck in their lips, and develop cyanosis▶️Distressed children▶️cry▶️relieves the cyanosis and become calmer, only to repeat the cycle after closing their mouths.
Diagnosis
inability to pass a firm catheter through each nostril 3-4 cm into the nasopharynx.
The anatomy is best evaluated by using high-resolution CT
Treatment
1- placement of an oral airway, maintaining the mouth in an open position, or intubation.
⏺ In bilateral cases, intubation or, less often, tracheotomy.
⏺ If the child is free of other serious medical problems, operative intervention is
considered in the neonate.
⏺ transnasal repair is the treatment of choice with the introduction of small magnifying
endoscopes and smaller surgical instruments and drills.
⏺ Stents are usually left in place for weeks after the repair to prevent closure or stenosis.
⏺ Operative correction of unilateral obstruction may be deferred for several yr.
⏺ Mitomycin C help prevent the development of granulation tissue and stenosis.