Chapter 43 - Pediatrics I Flashcards

1
Q

What makes up the foregut?

A

Lungs, esophagus –> duodenum to ampulla + pancreas, liver, gallbladder

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
2
Q

What makes up the midgut?

A

Duodenum from ampulla –> distal 1/3 of transverse colon

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
3
Q

What makes up the hindgut?

A

Distal 2/3 transverse colon –> anal canal

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
4
Q

Which way/how far does the midgut rotate?

A

270 degrees counterclockwise

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
5
Q

What defines low birth weight? Premature?

A

<2,500g, <37wks

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
6
Q

What makes up infant’s immunity at birth?

A

IgA from milk, IgM synthesized in child

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
7
Q

What is the #1 cause of childhood death?

A

Trauma

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
8
Q

What makes up a trauma bolus for kids?

A

20cc/kg x2; then give blood 10cc/kg

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
9
Q

What is the best indicator of shock in peds?

A

Tachycardia Neonate: 150+ < 1 yo: 120+ > 1yo: 100+

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
10
Q

What is the normal UOP for ped?

A

2-4cc/kg/hr

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
11
Q

What % GFR capacity do kids have compared to adults?

A

25%; poor concentrating ability

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
12
Q

What makes up the umbilical vessels?

A

2 arteries and 1 vein

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
13
Q

What are maintenance IV fluids

A

4cc/kg/hr for the 1st 10 kg

2cc/kg/hr for the 2nd 10 kg

1cc/kg/hr for everything after that

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
14
Q

What is pulmonary sequestration?

A

nonfunctioning mass of normal lung tissue that lacks normal communication with the tracheobronchial tree, and that receives its arterial blood supply from the systemic circulation.

  • Arterial supply MC from thoracic aorta or abdominal aorta through inferior pulmonary ligament.
  • Extra lobar: systemic venuous drainage via azygous system
  • Intra Lobar: pulmonary vein drainage
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
15
Q

What is the most common presentation of pulmonary sequestration? Treatment?

A

Infection, respiratory compromise, abnormal CXR

Tx: Ligate arterial supply first (risk of severe hemorrhage) then lobectomy

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
16
Q

What is congenital lobar overinflation (emphysema)?

A

Cartilage fails to develop in bronchus leading to air trapping with expiration

  • normal vascular suply
  • normal lobes
  • LUL most commonly affected
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
17
Q

Presentation of congenial lobar overinflation? Treatment?

A

Can get vascular compromise (same mechanism as tension pneumo) or respiratory insufficiency

Tx: Lobectomy

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
18
Q

What is congenital cystic adenoid malformation? (CCAM)

A

Alveolar structure not well developed although lung tissue is present, connects with airway

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
19
Q

Presentation of congenital cystic adenoid malformation? Treatment?

A

Resp compromise and recurrent infection

Tx: Lobectomy

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
20
Q

What is a bronchiogenic cyst?

A

Extrapulmonary cysts formed from bronchial tissue and cartilage wall

  • MC cyst of the mediastinum, usually posterior to the carina.
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
21
Q

Presentation of bronchiogenic cyst? Treatment?

A

Presents as mediastinal mass filled with milky fluid, can compress adjacent structures or become infected

Tx: Cyst resection

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
22
Q

What is the most common mediastinal mass in children?

A

Neurogenic tumors (neurofibroma, neuroganglionoma, neuroblastoma)

  • Usually located posterior
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
23
Q

What symptoms are common to all mediastina masses regardless of location?

A

Respiratory symptoms, dysphagia

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
24
Q

What are anterior mediastinal masses?

A

T cell lymphoma, teratoma (and other germ cell tumors), thymoma, thyroid ca

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
25
What are middle mediastinal masses?
T cel lymphoma, teratoma, cyst (cardiogenic, bronchiogenic)
26
What are posterior mediastinal masses?
T cell lymphoma, neuroblastoma, neurogenic tumors
27
What is the treatment for choledochal cysts? Etiology?
All need resection do to risk of cholangiocarcinoma, pancreatitis, cholangitis, obstructive jaundice Etiology: Reflux of pancreatic enzymes into biliary system in utero
28
What is a type I choledochal cyst? %?
Fusiform dilation of entire common bile duct, mildly dilated CHD, normal intrahepatic ducts 85%
29
What is a type II choledochal cyst? %?
True diverticulum that hangs off the common bile duct 3%
30
What is a type III choledochal cyst? %?
Dilation of distal intramural common bile duct, involves sphincter of Oddi 1%
31
What is a type IV choledochal cyst? %?
Multiple cysts, both intra and extrahepatic 10%
32
What is type V choledochal cyst? Other name? %?
Caroli's disease Intrahepatic cysts, get hepatic fibrosis, may be associated with congenital hepatic fibrosis and medullary sponge kidney
33
What is lymphadenopathy most likely caused by?
Acute suppurative adenitis associated with URI or pharyngitis
34
Workup for fluctuant lymphadenophathy? Asymptomatic?
Fluctuant: FNA, culture and sensitivity, abx; may need I&D Asymptomatic: abx for 10d --\>excisional biopsy if no improvement (lymphoma until proven otherwise)
35
What causes **_chronic_** fluctuant lymphadenopathy?
Cat scratch fever, atypical mycoplasma
36
What is cystic hygroma? Treatment?
Lymphangioma Found in lateral cervical and submandibular regions in neck, gets infected Tx: Resection
37
Overall survival of diaphragmatic hernias?
50%
38
What % of diaphragmatic hernias have associated anomalies? What are they?
80% Cardiac and neural tube defects, malrotation
39
Diaphragmatic hernias are increased on which side?
Left
40
Treatment for diaphragmatic hernias?
High-frequency ventilation, ECMO, prostacyclin (pulmonary vasodilator); stabilize before operating, reduce bowel, repair +/- mesh, look for visceral anomalies (run the bowel)
41
What is Bochdalek's hernia?
Most common diaphragmatic hernia Posterior
42
What is Morgagni's hernia?
Rare diaphragmatic hernia Anterior
43
What is eventration?
Failure of diaphragm to fuse
44
Treatment for pectus excavatum?
(Sinks in) Sternal osteotomy, need strut Performed if causing respiratory symptoms or emotional distress
45
Treatment for pectus craniatum?
(Pigeon chest) Strut not necessary Repair for emotional distress
46
Branchial cleft cyst causes what?
Cysts, sinuses, fistulas
47
Where is a 1st branchial cleft cyst? Associated with which nerve?
Angle of mandible, may connect with external auditory canal Facial nerve
48
Where is a 2nd branchial cleft cyst?
On anterior border of SCM muscle, goes through carotid bifurcation into tonsillar pillar
49
Where is a 3rd branchial cleft cyst?
Lateral neck
50
What is the treatment for branchial cleft cysts? Which is most common?
Resection 2nd branchial cleft cyst most common
51
Where is a thyroglossal duct cyst? Presentation?
From descent of thyroid gland from foramen cecum, goes through hyoid Presents as midline cervical mass
52
Treatment for thyroglossal duct cyst?
Resection of cyst, tract, and hyoid bone
53
Characteristics of hemangioma?
Appears at birth or shortly after Rapid growth between 6-12mo, then begins to involute
54
Treatment of hemangioma?
Observation Steroids, laser/surgery if uncontrollable growth, impairs function (eyelid/ear canal), persistent after age 8
55
What is the #1 solid abdominal malignancy in children?
Nueroblastoma
56
How do neuroblastomas usually present?
Asymptomatic mass Can have secretory diarrhea, raccoon eyes (orbital mets), HTN, opsomy oclonus syndrome (unsteady gait)
57
What is the most common location of neuroblastomas?
Adrenals; can occur anywhere on sympathetic chain
58
Most common lab findings with neuroblastoma?
Elevated catecholamines, VMA, HVA, metanephrines
59
Abd xray findings of neuroblastoma?
Stippled calcifications in tumor
60
What is elevated in all patients with neuroblastoma mets?
Elevated NSE
61
Treatment for neuroblastoma?
Resection (30-40% cured), chemo if initially unresectable
62
Presentation of Wilms tumor?
Usually as asymptomatic mass Hematuria, HTN, 10% bilateral
63
What is prognosis of Wilms tumor based on?
Tumor grade Anaplastic and sarcomatous variations with worst prognosis
64
Where do mets from Wilms tumor go?
Bone and lung; can resect lung mets
65
What syndromes are Wilms tumors associated with?
Beckwith-Widermann (hemihypertrophy, cryptorchidism, Drash syndrome, aniridia)
66
What are CT findings with Wilms tumors?
Replacement of renal parenchyma NOT displacement as seen with neuroblastoma
67
Treatment for Wilms tumor?
Nephrectomy (80-90% cured) Examine contralateral side for implants Avoid rupture of tumor Actinomycin and vincristine (except for stage I \<500g)
68
What is the most common malignant tumor in children?
Hepatoblastoma
69
What lab value is elevated in hepatoblastoma? Presentation?
Elevated AFP in 90% Fractures, precocious puberty (from beta-HCG release)
70
Hepatoblastomas are associated with what syndrome?
Beckwith-Wiedemann syndrome
71
Treatment for hepatoblastoma?
Resection; otherwise doxorubicin-cisplatin based chemo
72
What is the #1 children's malignancy overall?
ALL
73
What is the #1 solid tumor class?
CNS tumors
74
What is the #1 general surgery tumor in child 2?
2y: Wilms tumor
75
What is the #1 cause of duodenal obstruction in newborns?
Duodenal atresia
76
What is the #1 cause of duodenal obstruction after newborn period and overall?
Malrotation
77
Wat is the #1 cause of colon obstruction?
Hirschsprung's disease
78
What is the #1 liver tumor in children?
Hepatoblastoma
79
What is the #1 lung tumor in children?
Carcinoid
80
What is the #1 cause of painful lower GI bleeding?
Benign anorectal lesion (fissure, etc.)
81
What is the #1 cause of painless lower GI bleeding?
Meckel's diverticulum
82
What are the causes of upper GI bleeding in children 0-1? 1-adults?
0-1y: gastritis, esophagitis 1-adult: esophageal varices, esophagitis