Ch. 35 & 36 Flashcards
Caudal region of the primitive heart
Sinus venosus
Primitive atrium develops into
Left and right atria
Primitive ventricle develops into the
Left ventricle
Bulbous cord is develops into the
Right ventricle
Truncus arteriosus dilates to form
Aortic sac from which the aortic arches arise
Sinus venosus initially this is a separate chamber that opens into the
Right atrium
Sinus venosus receives all blood returning to the heart from
Common cardinal veins
Vitelline veins
Umbilical veins
The left horn of the sinus becomes the
Coronary sinus
The right horn is incorporated into _, this forms the _
The wall of the right atrium
Smooth portion of the adult right atrial wall
The right half of the primitive atrium persists as the
Right auricle
Left atria is formed by
Incorporation of the primitive pulmonary vein
4 pulmonary veins eventually enter the _ from the _
Left atrium
lung
The smooth wall of the left atrium is formed from the _
Absorbed pulmonary vein
The left atrial appendage (_) is from the _
Left auricle
Primitive heart
Division of the 4CH occurs during _ of fetal development
4th & 5th weeks
Endocardium cushions develop in _ region of the heart
Atrioventricular
The cushion grows toward each other and fuse to divide the _
Atrioventricular canal into right and left canals
The foramen oval is an opening between
The free edge of the septum secundum
and the dorsal wall of the atrium
The left ventricle is formed from the
Primitive vein
The right ventricle is formed from
Bulbous cordis
The interventricular septum begins as
A ridge in the floor of the primitive ventricle and slowly grows toward the endocardial cushion
Foramen ovale allows communication from _ to the _
right atrium to the left atrium
Ductus arteriosus allows fetal circulation to bypass the _
Lungs
Ductus arteriosus allows communication from the _ to the _
Pulmonary trunk
Descending aorta
Ductus venosus allows fetal circulation to bypass
The liver
Ductus venosus: flow passes from _ through the ductus venosus to the _ and then _
Umbilical vein
IVC
Right atrium
After birth, fetal lungs begin to function. The omission of placenta circulation causes an immediate fall in _
Blood pressure in the newborns IVC and right atrium.
After birth, as lungs expand with air, there is a fall in _. This causes an increase in _
Pulmonary resistance
Pulmonary blood flow and progressive thinning of the wall of the pulmonary artery.
Pressure in the _ becomes higher than the _. This causes _
Left atrium
Right atrium
The foramen ovale to close
First shunt to close after birth
Foramen ovale
If the foramen ovale does not close after birth
Patent foramen ovale
The ductus arteriosus usually constricts _ after birth, once _
24-48hrs
Left sided pressure exceeds right sided pressure
There is a small shunt from the _ to the _ until _
Aorta
Pulmonary artery
The left and right sided pressures adjust to neonatal life
Ductus arteriosus turns into the _ in the neonate.
If communication persisist _
Ligamentum arteriosum
Patent ductus arteriosus
Umbilical arteries also constrict after birth to _
Prevent blood loss from the newborn
Umbilical vein may
Remain patent for some time after birth
Normal HR
120-160bpm
Bradycardia _bpm
<100
Tachycardia _bpm
> 200
Umbilical arteries go _
Around the bladder
Indicators for fetal echo
IUGR Cardiac arrhythmias Abn. amnio Abn. HR Hydrops fetalis Thickened NT
Extracardiac abnormalities are assoc. w/
Congenital heart block
Echo: maternal factors
Previous child with congenital heart disease
Parent with congenital heart disease
Maternal diseases affecting fetus (diabetes, lupus, drug/alc. use)
Echo: Fetal US landmarks
Fetal position
Fetal thorax
Apex of heart
Echo: When fetus is in a difficult position
Ask mother to change positions
Have mother go to the restroom
Normal cardiac study should include the following views
o4 chambers
oOutflow tracts [RVOT, LVOT]
oOblique long-axis view for aortic arch and ductus arteriosus
The most commonly acquired view of the fetal heart
4CH
4-chamber view anatomy
▪Right atrium & ventricle [with moderator band] ▪Tricuspid valve ▪Left atrium & ventricle ▪Mitral valve ▪Interventricular septum ▪Interatrial septum ▪Foramen ovale ▪Pulmonary veins as they enter the left atrium
Moderator band can be used to locate the
Rt ventricle
Most anterior chamber
Rt ventricle
Most posterior chamber
Left atrium
The _ side of the heart is slightly larger in utero
Right
In utero the foramen ovale opens toward the _, as the pressure is slightly _ in the right atrium
Left atrium
Greater
After birth the pressure in the _ heart forces the foramen to close
Left
Failure of the foramen to close results in
defect in the atrial septum
_ valve is slightly inferior to the _ valve
Tricuspid
Mitral
The IVC and SVC can be seen entering the _
Right atrium
Junction of the interatrial and intraventricular septa, AV valves, and the 4 chambers
Crux
Five chamber view allows for the _
aortic flow to be recorded leaving the left ventricle
For 5CH, the transducer position is _
Slightly anterior to the 4CH
Criss-cross view, as the transducer is angled from the aorta slightly left
Pulmonary artery may be seen as it arises from the right ventricular outflow tract
Criss cross view: Pulmonary artery is normally _ and to the _ of the aorta
Anterior
Left
Criss cross view allows visualization of _
The normal relationship of the pulmonary artery and aorta to one another
Great vessels
Pulmonary artery and aorta
The “sweep” from the aorta to the pulmonary artery is called the_ view
Criss cross
LVOT: The origin of the aorta is identified arising from the
Left ventricle
Best view to obtain septal defects
LVOT
LVOT: Evaluate size of
▪Right & left ventricles
▪Right & left atriums
▪Thickness of interventricular septum
▪Continuity of interventricular septum
LVOT allows you to evaluate for _
A septal defect
LVOT: _ may not be detected with US
Small defects
Short axis view
RVOT
Long axis view
LVOT
For RVOT, from LVOT, rotate transducer _degrees in a _ direction
90
Cephalic
RVOT: Visualize the _ of the _ into the right and left pulmonary arteries
Bifurcation
Main pulmonary artery
RVOT: Demonstrates the normal relationship of the pulmonary artery as it lies _
Anterior and to the right of the aorta
Normally the RVOT and PA “drape” _ to the circular aorta
Anterior
Oblique view
Ductal/aortic views
Angulation of the transducer to oblique longitudinal plane provides visualization of this aortic anatomy:
Root of the aorta
Ascending aorta
Arch
Descending aorta
For oblique views, find the fetal spine in sagittal plane and angle _ to find the _ & _
Slightly inward toward the chest
Aortic & ductal arches
Aortic Arch: The three head and neck branch arteries arise from the perfect curve of the aortic arch as they
Ascend into the fetal head
3 head and neck branch arteries
Innominate (brachiocephalic)
Left common carotid
Left subclavian
Appearance of the aortic arch
Candy cane
Ductal Arch: Transducer is angled
inferior from the aortic arch
Ductal Arch: Arch type pattern represents
patent ductus arteriosus
Ductal arch: Ductus is slightly _ than the aortic arch
Larger
Ductal arch appearance
Hockey stick
Ductal arch: Does not have _ arising from its wall like the aortic arch
Head and neck vessels
Ductal arch: SVC/IVC emptying into the _
Right atrium
The most common types of congenital heart disease
Ventral septal defect
Atrial sseptal defects
Pulmonary stenosis
Most common single cardiac anomaly
Ventral septal defect
Influencing factors of congenital heart disease
Environmental
Chromosomal
Hereditary
Fetal echo helps to establish the
presence and severity of the cardiac abnormality
Indications for Sonographic detection of congenital heart disease
CHRISTMAS Concordance & contractility Hydrops Risk factors & rhythm Incorrect size (LGA/SGA) Symmetry Tetralogy of Fallot, transposition, tricuspid atresia, truncus arteriosus Masses & mobility Aneuploidy Situs
Common occurrence of _ with congenital heart disease
Chromosomal abnormalities
Majority of CHD have _
Trisomy 21
Followed by 13, 18, and Turners
Certain cardiac abnormalities are more likely to be associated with chromosomal defects, such as
Atrioventricular septal defect [ASD] Tetralogy of Fallot Double outlet right ventricle Coarctation of the aorta *Hypoplastic left heart
Malformations of the _ side of the heart are rarely assoc. w/ karotypic abn.
Right
*Mother who had a child with _ heart abnormality has significantly higher risk of delivering another child with a form of _ heart disease
Left
Left
Risk for heart disease _ with each pregnancy
Increases significantly
*_is the most common severe congenital abnormality
Congenital heart disease
CHD: _ of these are _
Half
Minor
CHD: may be corrected with _
Surgery
CHD: Other half (not minor) is responsible for more than _ of the deaths from congenital abnormalities in childhood
Half
Prenatal Evaluation of Congenital Heart Disease: Several cardiac abnormalities may be detected with the _
4CH but many will be missed with only this view
Dextrocardia: _ with the apex pointing to the _
Heart is in the right side
Right
Dextrocardia is assoc. w/
Normal visceral situs
Situs inversus
Dextroposition: Heart is in the _ with the apex pointing
Right side of the chest
Medially/left
Dextroposition: Usually found with intrinsic factors such as
Diaphragmatic hernia or hypoplasia of the right lung
Levocardia:
Both normal position of the heart in the left chest & when visceral/partial situs abnormalities are present
Levocardia is assoc. w/
Normal situs
Situs inversus
Levoposition
Heart is displaced further toward the left chest
Levoposition is assoc. w/
Space occupying lesion that would shove the heart more towards the left (diaphragmatic hernia)
Mesocardia
Cardiac apex is pointing toward the middle of the chest. Heart is usually more midline
Mesocardia is assoc. w/
Extracardiac mass
Lung abnormalities
Cardiomyopathy
Disease of myocardial tissue in the heart
Causes of cardiomyopathy
▪Exposure to virus or bacteria leading to infection
▪Errors of metabolism
▪Endocardial fibroelastosis
Myocarditis: characterized by
necrosis & destruction of myocardial cells and inflammatory infiltrate
Viral cardiomyopathy AKA
Myocarditis
All 4 chambers dilated and thinning of myocardial walls
Viral cardiomyopathy
Myocarditis: Severely decreased cardiac functionleadingto
▪congestive heart failure
▪Bradycardia ▪Death
Myocarditis prognosis
Poor
Pericardial effusion
Abnormal collection of fluid surrounding the epicardial layer of the heart
Pericardial effusion: in the 4CH view, *normal hypoechoic area in the peripheral part of the epicardial/pericardial interface should be
2mm or less
Pericardial effusion:
*Separation of greater than _mm may be associated with _
2
Hydrops
3 types of septal defect
Atrial septal defect [ASD]
Ventricular septal defect [VSD]
Atrioventricular septal defect [AVSD]
Atrial Septal Defect creates a communication between the
Right and left atrium
3 common forms of ASD
Osteum secundum
Osteum primum
Sinus venosus
Osteum Secundum:
_ common
Defect in _
Most common, yet most difficult to see.
The central atrial septum near foramen ovale
Osteum primum is assoc. w/
Trisomy 21
Sinus venosus: Near the _
_ common
Entrance of the SVC to the right atrium
Least
ASD is _ in utero, because _, unless _
not always diagnosed in utero
Foramen ovale
Part of the intra-atrial septum is missing
Failure of the foramen ovale to close may cause
ASD
Color flow helpful in detecting
ASD
Most common congenital lesion of the heart
VSD
VSD accounts for _% of all structural heart defects.
30
VSD: Defects smaller than _ are not detected by ultrasound
2mm
VSD prognosis
Good
VSD is assoc. w/
▪Tetralogy of Fallot
▪Single ventricle
▪Transposition of the great arteries
▪Endocardial cushion defect
Atrioventricular septal defect AKA
Endocardial cushion defect and AV canal malformation
Defect in the atrial & ventricular septum–failure of the common AV orifice to separate into mitral and tricuspid valves
Atrioventricular septal defect
Atrioventricular septal defects are subdivideed into
Complete
Incomplete
Partial
Atrioventricular septal defects are assoc. w/
Downs
Asplenia
Polysplenia
Tricuspid atresia _ causing _
Interruption of the growth of tricuspid leaflets
Valve to be hypoplastic or atretic
Tricuspid atresia: in the 4CH
Large dilated left ventricular cavity
Small, underdeveloped right ventricular cavity
Echogenic tricuspid annulus is seen with no valvular movement
Mitral valve is clearly the dominant atrioventricular valve
Ebstein’s Anomaly
*Abnormal displacement of the septal leaflets of the tricuspid valve toward the apex of the right ventricle-(low insertion)
Ebstein anomaly: _ is usually massively dilated
Right atrium
Ebstein anomaly: abn. function of the right side of the heart is related to the following 3 factors:
Malformed tricuspid valve
Atrialized portion of the right ventricle
Reduced capacity of pumping portion of right ventricle
Hypoplastic right heart
Right heart is underdeveloped
due to obstruction of RVOT secondary topulmonary stenosis
Hypoplastic right heart: small _
RV, RA, and tricuspid valve
Hypoplastic Left Heart Syndrome
Small hypertrophied left ventricle with aortic &/or mitral atresia
Hypoplastic left heart is a _ condition
Autosomal recessive
Hypoplastic left heart: Overload of _ may lead to_ with _
Right ventricle
Congestive heart failure
Pericardial effusions and hydrops
Hypoplastic left heart: small left ventricle due to
Blood cannot fill LV to provide volume
Aortic stenosis
Mitral &/or aortic valve atresia
Hypoplastic left heart is considered _ but prognosis has _
Lethal
improved with cardiac transplant
*Most common form of cyanotic disease in infants & children
Tetralogy of Fallot
Tetralogy of Fallot: severity varies according to
degree of pulmonary stenosis present
Tetralogy of Fallot consists of 4 abn. (sonographically)
VSD
Over-riding aorta
Pulmonary stenosis
Right ventral hypertrophy
Large septal defect with severe pulmonary stenosis
“Blue baby” at birth
Cyanotic disease
Large septal defect with mild to moderate pulmonary stenosis
Acyanotic disease
Tetralogy of Fallot is assoc. w/
Trisomy 13, 18, 21
other congenital cardiac malformations
If aorta overrides over 50%
*Called double-outlet right ventricle
Means that both great vessels arise from the right side of the heart
*Most common form of RVOT obstruction is _
Pulmonary valve stenosis
Pulmonary stenosis: abn. cusps become
Thickened
Pulmonary stenosis: main pulmonary artery may be
Hypoplastic
Pulm. stenosis: assoc. w/
other cardiac anomalies
Pulm. stenosis is _ to diagnose
Very difficult
*Transposition of the Great Arteries
Aorta is abnormally connected to the RV and the pulmonary artery is abnormally connected to the LV
Transposition of great arteries: In fetal heart
no hemodynamic compromise is seen when the great arteries are transposed
BUT, after birth, the problem occurs due to inadequate mixing of oxygenated & deoxygenated blood
Prognosis of transposition of great arteries
Good with surgical intervention
Transposition of great arteries is assoc. w/
ASD
Anomalies of the atrioventricular valves Underdevelopment of the right or left ventricles
Transposition of great arteries: _ is key in imaging the great arteries & their relationship
RVOT
Transposition of great arteries: RVOT, pulmonary artery & bifurcation should be seen _ to the aorta. In transposition this relationship _
anterior to the aorta
Is not present
Transposition of great arteries: LVOT: Normal criss-cross pattern seen when sweeping from LVOT to RVOT With transposition this
is not possible
Transposition of great arteries: LVOT: The great arteries are seen _ because
Parallel to each other
They both arise from the ventricles
Truncus Arteriosus
*Heart lesion which only 1 great artery arises from the base of the heart
Truncus arteriosus: from single great artery arises the
Pulmonary truck
Systemic arteries
Coronary arteries
Truncus arteriosus is assoc. w/
Mitral atresia
Atrial septaldefect [ASD]
Univentricular heart
Aortic arch abnormalities
Prognosis of truncus arteriosus _, fetal usually develops _
Poor
▪Congestive heart failure
▪Pericardial effusion
▪hydrops
Ultrasound: Truncus arteriosus
Abnormal, large, single great vessel arising from the ventricle
Coarctation of the Aorta
Shelf-like lesion in the isthmus of the arch.
Narrowing/kinking in the aorta
Coarctation of aorta: Assoc. intracardiac malformations are present in _% of cases
90
Cardiac malformations assoc. w/ coarctation of the aorta
▪Aortic stenosis
▪Aortic insufficiency ▪Septal defects ▪Transposition of great arteries
▪Truncus arteriosus
▪Double-outlet right ventricle
Coarctation of the aorta is _ to diagnose in fetus. Blood flow may _. After delivery, _
Difficult
Still be flowing into the arch
This will be very evident
Cardiac tumors are
Very unusual
Most cardiac tumors are
Benign and isolated
Most common cardiac tumor
Rhabdomyoma followed by teratoma
Cardiac tumors: _ are malignant
<10%
Rhabdomyoma tends to be
Multiple and involve the septum
Rhabdomyoma is assoc w/
Tuberous sclerosis
Rhabdomyoma: Fetus becomes _ when tumor_
Symptomatic
Becomes large enough to obstruct one of the outflow tracks
Rhabdomyoma leads to
Congenital heart failure
Pericardial effusion
Hydrops
Death
Rhabdomyoma: Prognosis depends on
Size
Location
Histologic type
Rhabdmyoma is best seen in
4CH
Single Ventricle
2 atrium _
1 ventricle
Single ventricle: 1 ventricle receives
Both mitral and tricuspid valves. Both are patent
Single ventricle: the right or left AV connection _
May be absent
Single vent.: Great arteries _. Aorta arises above _
May be transposed
A small outlet chamber
Single vent.: Pulmonary stenosis _
may or may not exist
Ectopia Cordis
Abnormal development of the heart outside of the chest
Ectopia cordis is assoc. w/
Facial & skeletal deformities Ventral wall defects[omphalocele] CNS malformations [meningocele, cephalocele] •Cardiac anomalies include: Tetralogy of Fallot Transposition of the great arteries
Prognosis of ectopia cordis
Very poor
Premature Atrial & Ventricular Contractions: called
PAC’s and PVC’s
Premature Atrial & Ventricular Contractions results from
An immature heart
Premature Atrial & Ventricular Contractions
Ectopic premature contraction
Premature Atrial & Ventricular Contractions: Atrium & ventricle may both experience
extrasystoles & ectopic beats
Echogenic intracardiac focus
An echogenic structure in the heart that is bright as bone
EIF: seen in the
Left ventricle of the heart
EIF is thought to represent
calcification of the papillary muscle or chordae tendineae (puts pressure on valves to keep closed)
EIF may be
Normal or linked with trisomy 21
How would you tell EIF from the moderator band
EIF is on the left (MB on right)
EIF will be bright as bone