Cardiology Flashcards
Egg on a string
Transposition of the Great Arteries
Boot-shaped heart
Tetralogy of Fallot
Four structural heart defects in ToF
- Overriding Aorta (aorta goes anterior to septal wall)
- VSD
- Pulmonic stenosis/outflow obstruction
- Right ventricular hypertrophy
Pathophysiology behind Tet spells
Increased R –> L shunting across VSD leading to circulation of deoxygenated blood; can overcome this by increasing venous return/systemic vascular resistance to overcome shunt
Most common cyanotic heart disease to present in the newborn period?
Transposition of the Great Arteries
Most common cyanotic congenital heart disease in general?
Tetralogy of Fallot (but usually presents around 3-5 months of age, not immediately).
ASD murmur?
Fixed wide split of S2, loudest at the LUSB due to increased flow across the pulmonary valve
SEM audible at the LUSB with thrill radiating to the back, varies with respiration
Pulmonic stenosis
SEM audible at the RUSB with thrill at the sternal notch, does not vary with respiration?
Aortic stenosis
A single second heart sound
Tetralogy of Fallot (pulmonic valve sound virtually absent)
During a Tet spell, which of the two is correct?
- Previous murmur is not audible
- Auscultation of a new murmur
Previous murmur (pulmonic stenosis murmur) is not audible because of lack of RV outflow
Which heart diseases presents with a single S2 heart sound? How can you differentiate the two HDs?
Tetralogy of Fallot (virtually minimal pulmonic outflow so no natural delay in P2 sound) & TGA
ToF– decreased pulmonary vascularity
TGA– increased pulmonary vascularity
CHD where lower extremity sats may be higher than the upper extremity sats?
Transposition of the great arteries–
1) RV –> aorta (upper extremities
(2) LV–> pulmonary artery –> PDA –> (lower extremities)
William Syndrome heart defect?
Supravalvular aortic stenosis
Noonan Syndrome heart defect?
Supravalvular pulmonic stenosis
Turner Syndrome heart defect?
Bicuspid aortic valve, coarctation of the aorta
22q11 deletion related heart defect?
Conotruncal defects and VSD
Down Syndrome related heart defect?
AV canal defects