Benign familial chronic pemphigus

Question 1

Another name for this disease

Answer 1

Hailey-Hailey

Question 2

Inheritance

Answer 2

Autosomal dominant

Question 3

Clinical findings of Hailey Hailey

Answer 3

Longitudinal white bands on nails
Lesions on UV exposed areas like nape of neck and friction areas like groin and axilla (pruritic vesicles in annular or serpiginous pattern-> advancing rim of scale on UV areas and moist, fissured papules and plaques intertriginously)

Question 4

Treatment

Answer 4

Oral antibiotics + topical steroids/topical antifungals based on location