Anesthesia and Altered Hemoglobin Structures Flashcards
Physiology of anemia

Effect of Anemia on Cardiac Output
As a patient becomes more anemic, cardiac output increases to compensate

Chronic vs. Acute Anemia

Hemolytic anemia


G6PDH-deficiency


Immune Hemolytic Anemia

CAHA (28-31C)

WAHA (37oC)

Alloimmune Hemolysis

Non-Immune Hemolytic Anemia

Anemia Anesthesia Management

When to give blood?


Sickle Cell Disease


SCD - Complications

Prevent Sickling

Yes

Α and β Thalassemia

Thalassemia

Polycythemia


Methemoglobinemia

Treatment for Methemoglobinemia

Mild Hemophilia


Moderate Hemophilia


Severe Hemophilia


Hemophilia A (Classic Hemophilia)


Hemophilia B (Christmas’ Disease)


Hemophilia Diagnosis

Treatment of Hemophilia A
(Factor VIII Deficiency)


Desmopressin DDAVP


Treatment of Hemophilia B
(Factor IX Deficiency)


Surgical Prophylaxis for Hemophilia A & B

High-risk Hemorrhagic Events
Hemophilia A and B

Von Willebrand disease (vWD)


Treatment of Von Willebrand Disease

Preoperative Considerations for Hemophiliacs - Elective Surgeries

Preoperative Considerations for Hemophiliacs -
Urgent Surgeries

Preoperative Considerations for those with risk factors or suspicion

Major Perioperative Risks

Non-immune Platelet Destruction

Disseminated Intravascular Coagulopathy


Clinical Manifestations of DIC

Drug Induced Platelet Destruction

Autoimmune Platelet Destruction

Hypercoaguabilty

Anticoagulation Therapy

