Amyotrophic Lateral Sclerosis Flashcards

1
Q

Define ALS

A

Amyotrophic Lateral Sclerosis is a progressive disease that causes muscle weakness, disability, and eventually death.

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2
Q

Is limb weakness asymmetrical or symmetrical?

A

Asymmetric limb weakness

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3
Q

Where does upper extremity weakness often present?

A

Hand weakness and shoulder girdle muscles

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4
Q

Where does lower extremity weakness often present?

A

Weakness with dorsiflexion

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5
Q

Besides limb weakness, what are other clinical manifestations of ALS?

A
Fatigue
Dysarthria/dysphagia
muscle atrophy and spasticity 
Fasciculations/twitching of the face and tongue
 Respiratory muscle weakness
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6
Q

What is the most common cause of death for those with ALS?

A

Respiratory failure

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7
Q

True or False: Those with ALS are cognitively aware/intact

A

True

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8
Q

What do moderately intensive exercises for the trunk and limbs do for the patient?

A

Decrease spasticity

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9
Q

What is the only drug approved for ALS? What does it do?

A

riluzole

Reduces damage to the damage to the motor neurons –> extends survival

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10
Q

Why is someone with ALS need to be NPO?

A

Weakness of throat muscles –> major aspiration risk!

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11
Q

What is the plan of care for someone with ALS

A
NPO
Pain assessment
Emotional and Psychological support
Minimize risk for injury
Provide diversional activities
PT consult, Speech therapy consult
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12
Q

What is another name for ALS?

A

Lou Gehrig Disease

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