Amyotrophic Lateral Sclerosis Flashcards
Define ALS
Amyotrophic Lateral Sclerosis is a progressive disease that causes muscle weakness, disability, and eventually death.
Is limb weakness asymmetrical or symmetrical?
Asymmetric limb weakness
Where does upper extremity weakness often present?
Hand weakness and shoulder girdle muscles
Where does lower extremity weakness often present?
Weakness with dorsiflexion
Besides limb weakness, what are other clinical manifestations of ALS?
Fatigue Dysarthria/dysphagia muscle atrophy and spasticity Fasciculations/twitching of the face and tongue Respiratory muscle weakness
What is the most common cause of death for those with ALS?
Respiratory failure
True or False: Those with ALS are cognitively aware/intact
True
What do moderately intensive exercises for the trunk and limbs do for the patient?
Decrease spasticity
What is the only drug approved for ALS? What does it do?
riluzole
Reduces damage to the damage to the motor neurons –> extends survival
Why is someone with ALS need to be NPO?
Weakness of throat muscles –> major aspiration risk!
What is the plan of care for someone with ALS
NPO Pain assessment Emotional and Psychological support Minimize risk for injury Provide diversional activities PT consult, Speech therapy consult
What is another name for ALS?
Lou Gehrig Disease