29: Paediatric Orthopaedics - Complex needs, CTEV and Scoliosis Flashcards

1
Q
A
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1
Q

what do we mean by complex needs?

A

A child with multiple and complex disabilities has at least two different types of severe or profound impairment such that no professional, agency or discipline has a monopoly in the assessment and management.

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2
Q

A child or young person (< 19) is defined as having complex exceptional needs (CEN) if:

A
  • severe impairment in at least 4 categories (learning and mental function, communication, motor skills, self-care, hearing or vision) together with enteral/parenteral feeding OR
  • severe impairment in at least 2 categories and ventilation/CPAP AND
  • impairments are sustained for more than 6 months and ongoing
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3
Q

what is cerebral palsy (CP)?

A
  • CP refers to a group of permanent, non-progressive movement disorders that appear in early childhood.
  • This condition occurs due to damage to a child’s CNS, particularly areas involving motor control.
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4
Q

CP causes
Antenatal/intrapartum and postnatal causes

A

Antenatal/Intrapartum causes:
- hypoxic-ischaemic encephalopathy
- infection

Postnatal causes:
- meningitis
- trauma
- haemorrhage
- medication toxicity
- Kernicterus (bilirubin induced encephalopathy)

  • A portion of CP cases remain idiopathic.
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5
Q

what are the different categories of motor disorders in CP?

A
  • spastic (pyramidal system, motor cortex)
  • athetoid (extrapyramidal system, basal ganglia)
  • ataxia (cerebellum and brainstem)
  • mixed (combo of spasticity and athetosis)
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6
Q

describe the stages of the gross motor function classification system (GMFCS) used in CP

A
  • level 1: walks without limitations
  • level 2: walks with limitations
  • level 3: walks using a hand-held mobility device
  • level 4: self-mobility with limitations, may use powered mobility
  • level 5: transported in a manual wheelchair
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7
Q

The higher the GMFCS level, the higher the risk of what in CP patients?

A

hip dislocation

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8
Q

CP management

A

Multi-disciplinary team:
- physio
- occupational therapy
- speeck and language therapy for swallowing assessments
- dieticians

Medical management:
- baclofen and diazepamused to manage muscle spasms
- botox injections may help with contractures

Surgical management:
- orthopaedic surgery for MSK deformities, injuries or tendon releases
- general surgery may be neccessary for example for fitting a PEG tube

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9
Q

what is the most common congenital deformity?

A

congenital talipes equinovarus (club feet)

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10
Q

list some traditional treatment options for club feet

A
  • strapping, positional talipes only
  • serial casting
  • Dennis Browne boots
  • surgery: postero-medial release, percutaneous tenotomy of achilles tendon (90% will need this)
  • llizarov frame
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11
Q

what degree of scoliosis is clinically significant?

A

> 10 degree deviation

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12
Q

describe the difference between non-structural vs structural scoliosis

A
  • non-structural = due to an extrinsic cause e.g. a leg length discrepany, a hip problem etc. Resolves when causal factor is addressed.
  • Structural scoliosis = abnormal rotation of the vertebrae and is an intrinsic spinal problem. Has a propensity to progress.
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13
Q

what factors determine whether scoliosis has a high risk of progressions?

A
  • premenarchal
  • < 12 y/o at presentation
  • size of curve at presentation
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14
Q

how do you classify scoliosis by aetiology?

A
  • congenital (abnormalities of vertebrae formation)
  • idiopathic
  • neuromuscular
  • others: post-trauma, degenerative, infective, syndrome etc.
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15
Q

what do you look for when examining a patient with suspected scoliosis?

A
  • inspect posterior torso, structural scoliosis will look worse when bent forward into flexion
  • abnormal neurology or pain should be noted
  • risk factors for progression
16
Q

what investigations are performed for scoliosis?

A
  • AP x-ray erect whole spine +/- lateral
  • MRI: cord abnormalities, vertrebral anomalies and tumours
17
Q

scoliosis management

A
  • bracing
  • surgical spinal fusion
18
Q

scoliosis surgery complications

A
  • nerve root damage
  • cord traction injury
  • vascular injury
  • degenerative changes later
  • problems of growth: growing rods, changing rods, Crankshaft phenomenon