19 - Congenital Heart Dz 1 Flashcards
a child with cyanotic heart dz most likely has a heart defect that shunts left>right or right>left?
right>left
which of the following pts is most likely to have irreversible pulm HTN? 10 yo w/ tetralogy of Fallot 1 yo w/ muscular VSD 10 yo w/ truncus arteriosus 10 yo w/ ASD
truncus arteriosus
presentation of a congenital heart disease mostly depends on the state of the _____
pulmonary circulation
4 factors determining consequences of shunt
size of defect
vascular resistance
pressure gradient
distensibility of chambers
3 L>R shunts
ASD, VSD, PDA
major consequences of L>R shunts and when do they tend to present in general
pulm edema and CHF
tend to take years to present - could be well into adulthood
most common ASD is in which part of septum?
secundum (90%)
primum ASD is also assoc w/
TV and MV malformations
which type of VSD is associated with multiple holes?
muscular
when does VSD tend to cause problems?
often much earlier - even in neonatal period
why do you want to repair L>R shunts earlier rather than later?
avoid irreversible pulm HTN - at that point repairing defect is no longer indicated
tetraology of fallot defects
RVOT stenosis
VSD
aortic override of VSD
RV hypertrophy
which type of VSD is associated with multiple holes?
muscular
when does VSD tend to cause problems?
often much earlier - even in neonatal period
why do you want to repair L>R shunts earlier rather than later?
avoid irreversible pulm HTN - at that point repairing defect is no longer indicated
