UWorld Peds Flashcards

1
Q

Evaluation of 1˚ amorrhea when uterus is present

A

FSH

high: karyotyping
low: pituitary MRI

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2
Q

Leukocyte adhesion deficiency

A

delayed cord separation

recurrent infections w/o purulence

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3
Q

Onion skinning distal bone

A

Ewing’s sarcoma

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4
Q

SCID genetics

A

XR

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5
Q

Chronic granulomatous disease etiology

A

NADPH oxidase deficiency

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6
Q

Erythromycin ointment is put on to prevent

A

gonococcal conjunctivitis

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7
Q

Which coxsackie causes myocarditis

A

B

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8
Q

Trachoma

A

leading cause of blindness worldwide

Chlamydia trachomatis

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9
Q

Neuroblastoma vs nephroblastoma/Wilms tumor

A

neuro crosses midline

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10
Q

Agammaglobulinemia
inheritance
Sx

A

XR (affects tyrosine kinases)

recurrent sinopulmonary and GI infections

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11
Q

McCune-Albright syndrome sx

A

precocious puberty, cafe-au-lait spots, multiple bone defects
3 p’s: precocious puberty, pigmentation, polyostotic fibrous dysplasia

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12
Q

Tx of congenital long QT

A

BB + pacemaker

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13
Q

Spondylolithesis

A

when over vertebrae is pushed over edge of the other

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14
Q

PPx cat bite

A

augmentin

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15
Q

Edwards syndrome

A

trisomy 18

small jaw, VSD

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16
Q

Tx of sickle cell

A

hydroxyurea (increases HgF)

myelosuppression

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17
Q

Anemia in Fanconi anemia

A

macrocytic

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18
Q

Fanconi dx

A

chromosomal breaks seen

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19
Q

Toxo transmission

A

undercooked meat, cat feces

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20
Q

Subcutaneous nodules after sore throat

A

rheumatic fever

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21
Q

When to bolus hypotonic saline in initial resuscitation

A

NEVER JUST F***ING NEVER

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22
Q

Biphasic stridor in infant

A

vascular ring

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23
Q

Laryngomalacia stridor

A

inspiratory

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24
Q

Cervical lymphadenitis etiology

A

S aureus

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25
Q

Tx of pt with rheumatic fever, but not treated and now asymptomatic

A

continuous ppx, IM PCN q4wk

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26
Q

Fever with rash starting at head going to toe

A

rubella

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27
Q

Wehn to do renal and bladder US in UTI

A

if <24 mo and febrile

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28
Q

Tetrology of Fallot combination results in

A

right ventricular outflow obstruction
creates right –> left shunt
fixed by squatting (increased systemic vascular resistance)

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29
Q

Reye syndrome bx

A

micro vesicular fatty infiltration

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30
Q

Difference between CF and 1˚ ciliary dyskinesia

A

malabsorption

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31
Q

Congenital rubella

A

cataracts, hearing loss, PDA, IUGR (worst during first trimester)

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32
Q

Congenital varicella

A

limb defects

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33
Q

Marfan’s mutation

A

fibrillin-1

34
Q

When to do exchange transfusion for bili

A

> 20-25

35
Q

Meconium ileum is basically diagnostic of

A

CF
extremely thick meconium, difficult to get out
therefore small colon

36
Q

Death in meningococcal disease

A

adrenal failure
bil adrenal hemorrhage
Waterhouse-Friedrichson syndrome

37
Q

Howell-Jolly bodies

A

asplenia or functional asplenia

nuclear remnants of RBC not removed by a functioning spleen

38
Q

Impetigo treatment

A

local if possible

muporicin

39
Q

Kallman syndrome

A

X-linked recessive in boys and girls

absence of GnRH secretion

40
Q

Deferoxamine

A

used in iron overdose

41
Q

Complication of bronchiolitis in <2 mo olds

A

apnea

42
Q

Tx of measles

A

vitamin A

regeneration of epithelial cells in gut, lungs, retina

43
Q

Tx of renal tubular acidosis

A

oral bicarb

44
Q

Recurrent infections in lymph nodes, neutrophils filled with organisms

A

chronic granulomatous disease
prevents oxidative burst with H2O2
dihydrorhodamine test/nitro blue tetrazolium

45
Q

Organisms that cause infection in chronic granulomatous disease

A

gram +

46
Q

When you done need to do a CT in meningitis before the LP

A

small babies, the fontanelle accommodates

47
Q

Choanal atresia

sx

A

cyclic cyanosis when infant cannot breath through mouth

failure of posterior nasal passage to canalize

48
Q

Osgood-Schlatter also called

A

traction appphysitis

49
Q

EDTA for lead poisoning

A

only if emergent, otherwise use dimercaptosuccinic acid DMSA for chelation

50
Q

Prader-Willi: loss of which copy?!

A

paternal

51
Q

Peri-splenectomy care

A

vaccinations weeks before

PCN for years/until adulthood/for life

52
Q

HUS symptoms

A

after diarrhea!

  • thombocytopenia (petechiae)
  • microangiopathic hemolytic anemia
  • AKI
53
Q

Kids with an itchy butt

A

pinworm

especially at night

54
Q

Milk-protein induced enterocolitis
dx
tx

A

bloody stools

eliminate all dairy and soy from mother’s diet, resolves by 1 yr old

55
Q

Croup sx

A

barky cough, hoarseness, inspiratory stridor

laryngotracheitis

56
Q

Contraindication to rotavirus vaccination

A

intuccesseption

can cause it!

57
Q

Omphalocele or gastrochesis, which is associated with other anomalies such as cardiac defects

A

Omphalocele

58
Q

When do not use doxy in Lyme

A

if <8 yr old

59
Q

Most common cause of pneumonia in CF <20 yr old

A

S aureus

60
Q

Tx common variable immunodeficiency

A

lifelong IVIG or subQ IG

61
Q

+ trendelenberg sign

A

gluteus medius + minimus weakness, superior gluteal nerve

62
Q

PAS+ lymphoma

A

ALL

TdT positive staining

63
Q

Cause of iron deficiency in infants

A

premature introduction of cow’s milk

64
Q

Beckwith-Wiedemann syndrome
at birth
complications

A

birth: macroglossia, hemihypertrophy, umbilical hernia
complications: Wilm’s tumor, hepatoblastoma

65
Q

Dx malrotation –> volvulus

A

upper GI series

66
Q

Definitive dx of muscular dystrophy

A

genetic testing

67
Q

Genu varum is a result of what

A

vit D deficiency

Ricketts!

68
Q

Hepatitis B renal disease

A

membranous nephropathy

69
Q

Wiskott-Aldrich syndrom

A

eczema
recurrent infections
impaired cytoskeletal changes in WBC, platelets (WAS gene)
tx: stem cell transplant

70
Q

Diarrhea –> nutritional deficiency with rash

A

pallegra (niacin/vit B3)
diarrhea
dermatitis
dementia

71
Q

When you can start XR of hips

A

4 mo old

72
Q

Common variable immunodeficiency vs Burton agammaglobulinemia

A

Burton’s is more severe and presents earlier

73
Q

How does standing quickly/valsalva affect hypertrophic cardiomyopathy

A

decrease preload, increase intensity of murmur

74
Q

Precocious puberty in obese children etiology

A

increased adrenal androgen production (development of hair only)
may also occur centrally

75
Q

Thalassemia on peripheral smear

A

target and teardrop cells

76
Q

Alpha thal minor hgb electrophoresis

A

normal

77
Q

Betal thal minor hgb electrophoresis

A

increased hgb A2

78
Q

Diamond-Blackfan anemia

A

pure red cell aplasia

presents around 3 mo

79
Q

Riboflavin deficiency

A

stomatitis, glossitis, angular ketosis

rash

80
Q

Beriberi

A

B1, thiamine

peripheral neuropathy, heart failure

81
Q

Breastfeeding reduces the risk of which cancers

A

ovarian and breast

82
Q

CF an infertility in men

A

absence of vas