Transposition of Great Vessels

Question 1

What is cardiac situs?

Answer 1

Refers to orientation of the right atrium

Question 2

What is situs solitus?

Answer 2

Normal right atrial position which is to the right

Question 3

What is situs inversus?

Answer 3

Mirror or opposite position for right atrium

Question 4

True or false: Infants with transposition of great vessels rarely have extra cardiac defects?

Answer 4

True

Question 5

What is the mustard/senning procedure?

Answer 5

Interatrial septum excised and large ASD created

Question 6

At what temp is pH stat and alpha stat relevant?

Answer 6

Below 30 C

Question 7

How is alpha stat approach to ABG management performed?

Answer 7

Electrochemical neutrality is maintained by keeping pH alkalotic in temperature corrected gases and normal in temperature uncorrected gases

Question 8

What is corrected vs. uncorrected temp with ABG?

Answer 8

Uncorrected: Gas values for PaCO2, PaO2, pH run at 37 C
Corrected: Gas values for PaCO2, PaO2, pHrun at actually body temp

Question 9

How is pH stat performed for acid base management?

Answer 9

Maintain pH and PCO2 at normal values for uncorrected blood regardless of actual blood temp.

Question 10

True or false: When blood in a closed system is cooled to a lower temp the electrochemically neutral pH is higher and the PCO2 lower than in a closed system at 37 C?

Answer 10

True

Question 11

What is the most common long term complication of arterial switch operation?

Answer 11

Supravalvular pulmonic stenosis