Tetrology of Fallot

Question 1

What are there 4 components of TOF?

Answer 1

1) Large VSd
2) RV outflow obstruction
3) Overriding Aorta
4) Right Ventricular Hypertrophy

Question 2

What is used to diagnose TOF with pulmonic stenosis?

Answer 2

TTE

Question 3

How is anatomy of MAPCA’s (Major Aortopulmonary collateral arteries) delineated in TOF with pulmonary atresia?

Answer 3

Cardiac Cath/MRI/MRA

Question 4

What is a Waterson Shunt?

Answer 4

Side to side anastomosis between ascending aorta and right PA

Question 5

What is a Potts shunt?

Answer 5

Side to side anastomosis between the descending aorta and left PA

Question 6

What is a central shunt?

Answer 6

Synthetic tube graft between ascending aorta and the main branch PA

Question 7

What is a Blalock-Taussig Shunt?

Answer 7

End to end anastomosis of the right or left subclavian artery to the ipsilateral PA

Question 8

What is a modified Blalock-Taussig Shunt?

Answer 8

Goretex tube between innominate artery or subclavian artery and the branch PA

Question 9

What % of children with congenital heart defects have other congenital anomalies?

Answer 9

8%

Question 10

What is the dose of oral ketamine?

Answer 10

7-10 mg/kg

Question 11

What factors prolong ACT (activated clotting time)?

Answer 11

Hypothermia, hemodilution, platelet dysfunction, low coat factors

Question 12

What is the heparin dose for CPB?

Answer 12

400 units/kg

Question 13

What is post-junctional ectopic tachycardia?

Answer 13

Transient tachyarrhythmia that occurs immediately following congenital heart surgery. Due to AV node or bundle dysfunction

Question 14

What is treatment of post-junctional ectopic tachycardia??

Answer 14

Atrial pacing