Test III Meds

Question 1

Hemophilia

Answer 1

Factor VIII concentrate Desmopressin (DDAVP (mild-moderate) Xnytha (severe) Avoid aspirin, ibuprofen and other NSAIDS that inhibit platelet function

Question 2

SCA

Answer 2

TYLENOL and IBUPROFEN may be used at the beginning of crisis PCA (MORPHINE) Avoid the use of DEMEROL=SEIZURES Heat to affected area Blood transfusion HYDROXYUREA (chemo drug)

Question 3

MCNS

Answer 3

May adm 25% ALBUMIN IV for severe edema PREDNISONE given until proteinuria stops and remains free for 10-14 days CYTOXAN: immunosuppressant

Question 4

PKU

Answer 4

Lofenalac or Phenex 1 special formula KUVAN helps the body activates the enzymes needed to control blood levels

Question 5

CF

Answer 5

Higher doses of antibiotics bc these pts metabolize them faster IV ANTIBIOTICS NEBCIN (tobramycin)liver/kidneys/ears AEROSOLIZED ANTIBIOTICS lowers rates of kidneys/ears CAYSTON, DNASE, ibuprofen, FLUTTER DEVICE, KALYDECO (pill)

Question 6

Meningitis

Answer 6

IV antibiotics for at least 7-10 days CEPHALOSPORINS STEROIDS (DEXAMETHASONE)