test 5 absent pulmonary valve

Question 1

What 3 things happen in the heart and vessels when you have an absent pulmonary valve

Answer 1

1. Absent Pulmonary Valve
2. Dilated Pulmonary Arteries
3. VSD

Question 2

Absent Pulmonary Valve

Answer 2

 Rare defect (3% to 6% of patients with TOF)
 Pulmonary valve tissue not formed or incomplete
 4+ Pulmonary Insufficiency
 Flood pulmonary arteries (pulmonary overcirculation)
 Massive dilation of Pulmonary Arteries
 Lead to extrinsic compression of the bronchial airway
 leads to abnormal development of bronchial tree.
 Associated with VSD

Question 3

Respiratory impairment due to Absent Pulmonary Valve

Answer 3

 Flood pulmonary arteries (pulmonary overcirculation)
 Massive dilation of Pulmonary Arteries
 R L shunting
 systemic desaturation
 Compression of airway = compromised oxygen saturation

Question 4

Absent Pulmonary Valve Treatment

Answer 4

 Plication of the Pulmonary Arteries (fix the dilated pulmonary arteries
- suture the artery walls together minimizing the size of the vessel lumen
 Pulmonary Valve Replacement
 VSD Closure