Structural Cardiac Disorders and CM Flashcards
What is the MC type of congenital heart disease?
VSD
What are the 4 types of VSD? Which is MC?
- Perimembranous (MC): hole in LV outflow near tricuspid valve
- Muscular: multiple holes in “swiss cheese” pattern
- Inlet: posterior to tricuspid valve
- Supracristal: Beneath pulmonic valve
What are the s/s of small (restrictive) VSD?
Asx or mild
Found incidentally due to murmur
Restrictive = normal pressure btwn ventricles maintained
What are s/s of moderate VSD?
Excessive sweating or fatigue, esp. during feeds
What are s/s of Eisenmenger’s syndrome?
Right to left shunt
Asx at rest, but +/- cyanosis*, dyspnea, CP, & syncope
What does VSD look like on PE?
Loud high-pitched holosystolic murmur at lower left sternal border
Mod VSD: +/- thrill, diastolic rumble at mitral area
Large VSD: signs of CHF
How do you dx VSD?
CXR: LA enlargement, RV hypertrophy Echo: preferred over cath ECG: LVH/RVH MRI Cath
How do you treat VSD?
Most close spontaneously within 10 years
Patch closure if sx
Larger shunts are repaired by age 2 to prevent pulmonary HTN
What are characteristics of coarctation of the aorta?
Increased LV afterload –> HTN, LVH, CHF
70% also have bicuspid aortic valve
What are s/s of coarctation of the aorta?
Secondary HTN*
Bilateral claudication*, dyspnea, syncope
What does coarctation of the aorta look like on PE?
Systolic murmur that radiates to back/scapula/chest
Increased BP upper > LE
Delayed/weak femoral pulses
How do you dx coarctation of the aorta? What is gold standard?
CXR: Rib notching, “3 sign”
ECG: LVH
Angiogram = GOLD
How do you treat coarctation of the aorta?
Surgical repair
Balloon angioplasty +/- stent
PGE1
What is the MC cyanotic congenital heart disease?
Tetralogy of fallot (right to left shunt)
What are causes of tetralogy of fallot?
- RV outflow obstruction (pulmonary artery stenosis)
- RV hypertrophy
- VSD (large unrestrictive)
- Overriding aorta
What are s/s of tetralogy of fallot?
Blue baby syndrome (cyanosis)
“Tet-spells”: older children relieve spells by squatting
Eisenmenger’s syndrome (seen w/ VSD, PDA, & TOF)
What does tetralogy of fallot look like on PE?
Harsh holosystolic murmur @ left upper sternal border
Right ventricular heave