SS

Question 1

What is the greatest mimicry of cutaneous systemic sclerosis and how will you differentiate it?

Answer 1

Eosinophilic fasciitis—- likely Vivian had it.

CHARCTERISTICALLY distal digits will be NORMAL, prayer sign can be falsely positive due to forearm involvement.

Question 2

Why is it important to DDx eosinophil fasciitis from systemic sclerosis

Answer 2

First line for EF: GC
Which is avoided in systemic sclerosis

Question 3

Why wouldn’t you start patient with cutaneous DM on HCQ

Answer 3

1. It doesn’t work beyond photoprotective effect
2. Patients have higher incidence of hypersensitivity in DM patient, particularly MDA-5