Situs and Heterotaxy Flashcards
+ venous abnormalities
Describe the R bronchus in terms of its relation to RPA branching
Eparterial - bronchus branches before the RPA
Describe the L bronchus in terms of its relation to LPA branching
Hyparterial- bronchus branches below the LPA branching
What EP conditions are seen in Right and Left isomerism
Right isomerism: EAT, double SA nodes
Left isomerism: Complete heart block
What is the most common form of TAPVR?
Supracardiac
What is the form of TAPVR most likely to be obstructed?
Infracardiac
Where is the site of obstruction for supracardiac TAPVR?
Compression of vertical vein by the bronchus
Where is the site(s) of obstruction for infracardiac TAPVR?
Level of the diaphragm, portal vein, ductus venosus
What is the most common form of PAPVR?
LUPV to left innominate vein
What is associated with a RUPV to SVC?
Superior sinus venosus defect
What is associated with a RLPV to IVC?
Inferior sinus venosus defect
What two genetic conditions are associated with PAPVR?
Turners and Noonan
What is important to rule out before diagnosing someone with primary pulmonary hypertension?
Pulmonary vein stenosis
In cases of a persistent L-SVC, where does it usually drain to?
Coronary sinus
What causes a cor triatritum dexter?
Persistence of the right valve of the sinus venosus
What causes a cor triatritum sinister?
Abnormality with the connection of the pulmonary venous chamber to the LA
