Rhabdomyosarcoma

Question 1

Primary orbital malignancy in kids

Avg age of onset 7 yrs

Answer 1

Undifferentiated mesenchymal cells that have the potential to develop into striated muscle

Question 2

Embryonal
Alveolar
Pleomorphic

Answer 2

Acute subacute onset of rapidly progressive proptosis and orbital inflammation

Cellulitis

Proptosis

Question 3

Supranasal quadrant

Pain uncommon

Answer 3

B scan ultrasonography
Cat MRI
Irregular but we’ll defined masses w Bony erosion
Surgery and radiotherapy

Question 4

Optic nerve glioma arise from astrocytes
Kids
Neurofibromatosis type 1

Answer 4

Slowly progressive vision loss
Associated w gradual unilateral painless proptosis
Dec vision
Relative afferent pupillary defect

Question 5

Fundus
Disk swelling
Optic atrophy
Shunt vessels
Intracranial spread(chiasma and hypothalamus)

Answer 5

CT MRI and ultrasonography
Enlargement of nerve
Clear margins cuz of dural sheath
Tumor and it's extension
Fusiform enlargement of nerve

Question 6

Trwatmennt

Answer 6

Observation
Surgically excused
Chemo when less extension
Radio if can’t be cut

Question 7

Meningothelial cells of the archnoid villi
Middle age women
Pri optic nerve sheathe meningioma less common than optic nerve glioma

Answer 7

2/3 extension of intracranial lesion
Vision. Loss in 1 ete
Dec vision pupillary defect afferent 
Restricted motility
Gradually proptosis
Unilateral

Question 8

Fundus exam
Disk swelling
Opticiliary vessel
Optic atrophy
CT

Answer 8

Thickening and calcification of ON tram tracking of sheath
MRI
Tubular enlargement of ON
Ultra sonography
Observation
Surgically if blind