PRIMARY DISORDERS: VASCULAR DISORDERS

Question 1

Characterized by local dilation of capillary walls. Most common inherited vascular bleeding disorder

Answer 1

Hereditary Hemorrhagic Telangiectasia

Question 2

Also called Osler-Webes -Rendu Disease

Answer 2

Hereditary Hemorrhage Telangiectasia

Question 3

Hyperextensible, hyperplastic akin

Answer 3

Ehlers-Danlos Syndrome aka Cutis hyperelastica

Question 4

Skeletal defects (long extermities) arachnodactyly (spider fingers)

Answer 4

Marfan’s syndrome

Question 5

Presence of bruised areas on the forearms of elderly persons

Answer 5

Senile purpura

Question 6

Gastrointestinal bleeding and joint swelling

Answer 6

Henoch-Schonlein Purpura aka allergic purpura or nonthrombocytopenic purpura

Question 7

Defects in the synthesis of collagen and hyaluronic acid

Answer 7

Scurvy (ascorbic acid or vitamin c deficiency

Question 8

Severe capillary damage following meningococcal septicemia

Answer 8

Waterhouse-Friderichsen syndrome aka hemorrhagic adrenalitis

Question 9

Associated with tumors composed of vessels that commonly swell and bleed at the surface

Answer 9

Kasabach-Meritt Syndrome