Porphyrias Flashcards
1
Q
What are the three porphyrias to be aware of?
A
Erythropoietic protoporphyria
Porphyria cutanea tarda
Acute intermittent porphyria
2
Q
What is used to investigate porphyrias?
A
Woods lamp
3
Q
What are common underlying causes of porphyria cutanea tarda?
A
Alcohol
Viral hepatitis
Oestrogens
Haemochromatosis
4
Q
How is Erythropoietic protoporphyria managed?
A
6 monthly LFTs and RBC porphyrins
Visible light photoprotection measures
5
Q
Name four types of photoprotective measures?
A
Behavioural - avoid sunlight
Clothing - weave, colour etc
Environmental - window films
Topical sunscreen
6
Q
A
