Plastics / Orbit Flashcards
What is a/w rubella, toxo, maternal vit A def with a blue mass of the lower eyelid and posterior segment coloboma?
Microphthalmos with cyst
Where is the most common site of rhabdomyoscarcoma to metastasize?
Chest - intrathoracic area has worst prognosis.
What type of internal relectivity does rhabdo have?
MEDIUM
What are the most and least common types of rhabdo?
most - embryonal (elongated spindle cells)
least - pleomorphic (cross striations)
Which histocystosis has proptosis, lytic bone/skull lesions, and diabetes insipidus?
Hand-schuller
What does a neurofibroma stain with?
S-100
Where is typical location of capillary hemangioma?
Superior nasal quad or medial upper eyelid
What 3 pediatric lid lesions are UNCAPSULATED?
- Neurofibroma
- Capillary hemangioma
- Lymphangioma
How do you differentiate an ON meningioma from fibrous dysplasia?
Menigoma has a DURAL TAIL
What is Albright’s syndrome?
POLYostoic fibrous dysplasia causing short height, decreased hearing and vision, with immature woven bone
Monostoic vs Polyostoic affects what in fibrous dysplasia?
Monostoic - orbital involvement with frontal bone and U/L proptosis
POLYostoic - narrowing of optic canal and lacrimal drainage systems
Which dz has lateral lid colobomas with curved downward slanting lateral can thus ?
Treacher collins
What is the most common craniofacial d/o and what is the gene?
Crouzon’s with FGFR2 gene (NO hand/feet/limb deformities)
What is a/w increased paternal age with decreased intelegence and syndactly?
APERT’S syndrome
What dz has an asymmetric face with the TWIST gene?
Saethre-Chotzen syndrome
Which craniofacial d/o b/l cats and gl with sponaneous rupture of lens capsule and absorption of lens protein (phacoanayphytic uveitis) with beaked nose?
Hallerman-Streiff Syndrome
What is a/w Sticklers with micrognathia and glosoptosis?
Pierre Robin Sequence
The lateral canthal tendon is lower or higher than the medial usually?
Higher
What has horizontally and vertically shortened Palebral fissure?
Blepharophimosis
How do u fix ptosis in congenital Horner’s?
Levator resection!
Trachoma causes what lid abnl?
Congenital ECTROPION - inclusion conjunctivitis (also Down’s snd blepharophimois a/w congenital ectropion)
What are 2 lesions a/w Linear Sebaceous nevus syndrome?
- Dermoid cysts
2. Complex choristoma
What is a fleshy vascularized tumor that usually extends into the corneal stroma with mild growth during puberty?
Ectopic LACRIMAL GLAND!
What conjucntivits affects males with upper eye lid papillary rxn in the spring and fall?
VERNAL - horner trantus dot with sheild uclers
What is the most common neontal conjunctivitis?
Chalymdia
