Plastics / Orbit

Question 1

What is a/w rubella, toxo, maternal vit A def with a blue mass of the lower eyelid and posterior segment coloboma?

Answer 1

Microphthalmos with cyst

Question 2

Where is the most common site of rhabdomyoscarcoma to metastasize?

Answer 2

Chest - intrathoracic area has worst prognosis.

Question 3

What type of internal relectivity does rhabdo have?

Answer 3

MEDIUM

Question 4

What are the most and least common types of rhabdo?

Answer 4

most - embryonal (elongated spindle cells)

least - pleomorphic (cross striations)

Question 5

Which histocystosis has proptosis, lytic bone/skull lesions, and diabetes insipidus?

Answer 5

Hand-schuller

Question 6

What does a neurofibroma stain with?

Answer 6

S-100

Question 7

Where is typical location of capillary hemangioma?

Answer 7

Superior nasal quad or medial upper eyelid

Question 8

What 3 pediatric lid lesions are UNCAPSULATED?

Answer 8

1. Neurofibroma
2. Capillary hemangioma
3. Lymphangioma

Question 9

How do you differentiate an ON meningioma from fibrous dysplasia?

Answer 9

Menigoma has a DURAL TAIL

Question 10

What is Albright’s syndrome?

Answer 10

POLYostoic fibrous dysplasia causing short height, decreased hearing and vision, with immature woven bone

Question 11

Monostoic vs Polyostoic affects what in fibrous dysplasia?

Answer 11

Monostoic - orbital involvement with frontal bone and U/L proptosis
POLYostoic - narrowing of optic canal and lacrimal drainage systems

Question 12

Which dz has lateral lid colobomas with curved downward slanting lateral can thus ?

Answer 12

Treacher collins

Question 13

What is the most common craniofacial d/o and what is the gene?

Answer 13

Crouzon’s with FGFR2 gene (NO hand/feet/limb deformities)

Question 14

What is a/w increased paternal age with decreased intelegence and syndactly?

Answer 14

APERT’S syndrome

Question 15

What dz has an asymmetric face with the TWIST gene?

Answer 15

Saethre-Chotzen syndrome

Question 16

Which craniofacial d/o b/l cats and gl with sponaneous rupture of lens capsule and absorption of lens protein (phacoanayphytic uveitis) with beaked nose?

Answer 16

Hallerman-Streiff Syndrome

Question 17

What is a/w Sticklers with micrognathia and glosoptosis?

Answer 17

Pierre Robin Sequence

Question 18

The lateral canthal tendon is lower or higher than the medial usually?

Answer 18

Higher

Question 19

What has horizontally and vertically shortened Palebral fissure?

Answer 19

Blepharophimosis

Question 20

How do u fix ptosis in congenital Horner’s?

Answer 20

Levator resection!

Question 21

Trachoma causes what lid abnl?

Answer 21

Congenital ECTROPION - inclusion conjunctivitis (also Down’s snd blepharophimois a/w congenital ectropion)

Question 22

What are 2 lesions a/w Linear Sebaceous nevus syndrome?

Answer 22

1. Dermoid cysts

2. Complex choristoma

Question 23

What is a fleshy vascularized tumor that usually extends into the corneal stroma with mild growth during puberty?

Answer 23

Ectopic LACRIMAL GLAND!

Question 24

What conjucntivits affects males with upper eye lid papillary rxn in the spring and fall?

Answer 24

VERNAL - horner trantus dot with sheild uclers

Question 25

What is the most common neontal conjunctivitis?

Answer 25

Chalymdia