Peds Quiz #3 Flashcards

1
Q

What is an Obstetric Brachial Plexus Injury (OBPI)?

A
  • Obstetric Brachial Plexus Injury (OBPI) is a type of brachial plexus injury that occurs during delivery, often due to trauma to the shoulder or spine.
  • Results from traction or compression of the brachial plexus nerves.
  • This injury can range from mild (stretching of nerves) to severe (nerve rupture or avulsion).
  • It is commonly associated with difficult vaginal births, including shoulder dystocia or breech presentations.
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2
Q

What are the four types of brachial plexus lesions?

A

(1) Avulsion: The nerve is torn away from its attachment to the spinal cord.

  • Most severe form and typically irreversible.

(2) Rupture: The nerve is completely torn but remains detached from the spinal cord.

(3) Neuroma: Scar tissue grows around the injured nerve, applying pressure and preventing proper conduction.

(4) Neurapraxia: A stretch injury where the nerve remains intact but temporarily loses function.

  • Neurapraxia has the best prognosis for recovery.
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3
Q

What is the clinical presentation of Erb’s Palsy?

A

Erb’s Palsy involves injury to the C5-C6 nerve roots, sometimes C7.

The affected limb assumes a “waiter’s tip” position:

  • shoulder adduction, internal rotation, and extension; elbow extension;
  • forearm pronation; and
  • wrist/finger flexion.

Grip strength is typically intact since the lower nerve roots (C8-T1) are unaffected.

If C7 is involved, elbow, wrist, and finger extension may also be impaired.

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4
Q

What is the clinical presentation of Klumpke’s Palsy?

A
  • Klumpke’s Palsy involves the C8-T1 nerve roots and results in “claw hand” deformity due to weakness in the intrinsic hand muscles and wrist/finger flexors.
  • The forearm often rests in supination.
  • Shoulder and elbow movements are typically unaffected.

In severe cases, it may be associated with Horner’s Syndrome, which presents as:

  • ptosis (drooping eyelid)
  • miosis (constricted pupil)
  • anhidrosis (lack of sweating) on the affected side
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5
Q

What is the difference between Erb’s Palsy and Global Palsy?

A

Erb’s Palsy:

  • Involves injury to the upper nerve roots (C5-C6, sometimes C7)
  • Primarily affecting shoulder and elbow function.

Global Palsy:

  • Affects the entire brachial plexus (C5-T1), resulting in complete paralysis and sensory loss of the arm.
  • Global Palsy typically has a more severe prognosis and may include additional complications like Horner’s Syndrome.
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6
Q

What are the risk factors for Obstetric Brachial Plexus Injury?

A

Risk factors include:

  • macrosomia (birth weight >4500 grams)
  • shoulder dystocia
  • prolonged labor
  • maternal diabetes
  • breech delivery
  • use of mechanical assistance (forceps or vacuum)
  • hypotonic infants (floppy babies)

These factors increase the likelihood of traction or compression on the brachial plexus during delivery.

  • shoulder dystocia = obstetric emergency that occurs when a baby’s shoulder gets stuck during vaginal delivery
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7
Q

What is the purpose of the Active Movement Scale in brachial plexus examination?

A

The Active Movement Scale (AMS): Assesses voluntary muscle function in children with brachial plexus injury. It grades movement from

  • 0 (no contraction), to
  • 7 (full motion against gravity).
  • 4 = Full joint motion

- AMS is critical in determining motor recovery, guiding therapy plans, and identifying candidates for surgical intervention.

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8
Q

How is sensory grading performed for brachial plexus injuries?

A

Sensory grading for brachial plexus injuries is based on response to stimuli:

  • S0: No response to painful or touch stimuli.
  • S1: Response to painful stimuli only.
  • S2: Response to touch but not light touch.
  • S3: Normal sensation.

This grading helps evaluate sensory recovery and guide intervention strategies, particularly in cases of neuroma or rupture where sensory function may be impaired.

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9
Q

What interventions are used to prevent contractures in brachial plexus injuries?

A
  • Gentle range-of-motion (ROM) exercises are essential to prevent contractures in affected joints.
  • These exercises should focus on maintaining flexibility in the shoulder, elbow, wrist, and fingers.
  • Splinting or positioning devices may also be used to promote proper alignment and prevent fixed deformities, especially in cases of long-term nerve dysfunction.
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10
Q

Why is caregiver education critical in managing brachial plexus injuries?

A
  • Caregiver education ensures consistency in performing home exercises, maintaining positioning, and monitoring the child’s progress.
  • Caregivers play a vital role in encouraging active use of the affected limb during daily activities and preventing neglect of the limb.
  • Without caregiver involvement, therapeutic benefits may be limited.
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11
Q

What are key surgical interventions for brachial plexus injuries?

A

Surgical options include

  • nerve grafting (replacing damaged nerve segments with donor tissue)
  • nerve transfers (redirecting functional nerves to replace damaged ones).

- Surgery is typically recommended if no significant recovery is observed by 3-8 months, especially in cases of avulsion or rupture.

- Early surgery is more effective in restoring function and preventing long-term deficits.

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12
Q

What are the indications for nerve transfer surgery in brachial plexus injuries?

A

Nerve transfer surgery is indicated in severe cases like avulsion or rupture when spontaneous recovery is unlikely.

Key signs include

  • the absence of biceps function by 3 months old, or
  • minimal improvement in other muscle groups

- The procedure aims to reinnervate paralyzed muscles and improve limb function.

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13
Q

How does kinesiotaping support therapy in brachial plexus injuries?

A
  • Kinesiotaping provides support and promotes proper alignment by facilitating or inhibiting specific muscles.
  • For example, it may enhance activation of weak shoulder stabilizers while reducing spasticity in overactive muscles.
  • This adjunct therapy complements active and passive exercises to improve function and prevent compensatory patterns.
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14
Q

How does electrical stimulation assist in the treatment of brachial plexus injuries?

A
  • Electrical stimulation helps activate weak or paralyzed muscles, promoting neuromuscular reeducation and preventing muscle atrophy.
  • It is particularly useful in outpatient settings for muscles that have partial innervation or are beginning to recover from neurapraxia.
  • This modality is often used in conjunction with active movement exercises.
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15
Q

What are the long-term outcomes of untreated brachial plexus injuries?

A

Untreated brachial plexus injuries may lead to

  • permanent weakness
  • sensory deficits
  • joint contractures

- In severe cases, limb function may be severely impaired, impacting the child’s ability to perform age-appropriate activities and potentially leading to lifelong disability.

  • Early intervention significantly improves outcomes.
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16
Q

What is Congenital Muscular Torticollis (CMT)?

A

Congenital Muscular Torticollis (CMT) or “wry neck,” is a condition characterized by unilateral shortening of the sternocleidomastoid (SCM) muscle, leading to:

  • Lateral head tilt toward the affected side
  • Rotation to the opposite side.

- It may involve other muscles like the scalenes, levator scapulae, and upper trapezius.

  • It often develops due to intrauterine positioning, birth trauma, or postnatal factors like prolonged positioning.
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17
Q

What are the associated conditions with CMT?

A

- Conditions commonly associated with CMT include:

  • deformational plagiocephaly (skull asymmetry due to positioning)
  • congenital hip dysplasia
  • brachial plexus injury
  • facial asymmetry
  • scoliosis
  • foot deformities (metatarsus adductus)

- These associations highlight the importance of a thorough examination beyond just the neck.

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18
Q

What prenatal, perinatal, and postnatal factors contribute to CMT?

A

Prenatal:

  • intrauterine positioning
  • ischemic injury to SCM leading to compartment syndrome.

Perinatal:

  • breech presentation
  • use of forceps/vacuum
  • birth trauma

Postnatal:

  • positional preference
  • plagiocephaly
  • reflux

- These factors influence the degree and severity of SCM shortening.

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19
Q

How is CMT severity classified?

A

According to the APTA’s Clinical Practice Guidelines, CMT severity is graded from

  • 1 (mild, early identification), to
  • 8 (severe, late identification and significant ROM limitations).

Severity is based on

  • the age of identification
  • degree of cervical ROM restriction
  • presence of an SCM mass
  • age at physical therapy evaluation.

  • Higher grades indicate a poorer prognosis if untreated.
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20
Q

What are the three types of cranial deformation associated with plagiocephaly?

A

Plagiocephaly:

  • Flattening on one side of the back of the head, with asymmetrical ear and facial alignment.

Brachycephaly:

  • Generalized flattening of the back of the head, leading to a wide and short skull shape.

Dolichocephaly (Scaphocephaly):

  • Long, narrow head shape often seen in premature infants due to extended time in the NICU.

  • These deformations can occur secondary to CMT.
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21
Q

What are the 7 key components of a PT examination for CMT?

A
  • Infant posture in supine, prone, sitting, and standing.
  • Bilateral active cervical rotation, lateral flexion, and diagonal movements.
  • Passive and active ROM of the cervical spine and extremities.
  • Hip screening for dysplasia.
  • Pain assessment (e.g., FLACC scale).
  • Integumentary evaluation (skin folds and integrity).
  • Craniofacial assessment for asymmetry and deformities like plagiocephaly.

  • These components guide diagnosis and treatment planning.
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22
Q

What is the Muscle Function Scale, and how is it used for CMT?

A

The Muscle Function Scale measures active lateral head righting ability in infants with CMT.

- It assesses the strength of the SCM & other neck muscles during lateral flexion against gravity.

- Scoring ranges from

  • 0 (no response), to
  • 4 (full ability to hold the head laterally aligned for >5 seconds)

- This scale helps monitor progress and guide strengthening interventions.

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23
Q

What are the primary interventions for CMT?

A

Interventions include:

  • Stretching exercises for cervical rotation and lateral flexion.
  • Strengthening of cervical and trunk muscles through active head righting and midline control.
  • Positioning techniques to avoid prolonged postures and encourage symmetrical development.
  • Tummy time to promote prone play and neck strengthening.
  • Parent education for home exercises and positioning.

- These approaches aim to restore cervical ROM, prevent deformities, and support symmetrical developmental milestones.

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24
Q

How can kinesiotaping assist in CMT treatment?

A

Kinesiotaping

  • Provides sensory input to facilitate active movement or inhibit overactive muscles.
  • For CMT, it may help activate weakened neck muscles on the non-affected side or provide gentle resistance to improve alignment and reduce reliance on passive structures.
  • It complements manual therapy and positioning.
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25
Q

What is the purpose of cranial orthoses in plagiocephaly management?

A

Cranial orthoses, like the DOC Band or STAR Band, are used to remodel the shape of the skull in infants with plagiocephaly or severe asymmetry.

  • These devices are typically prescribed around 4-5 months of age (after head control develops) and are worn 23-24 hours per day.
  • They apply gentle pressure to redirect growth toward flattened areas, improving cranial symmetry.
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26
Q

When are Botox injections indicated?

A

Botox injections may be used in severe CMT cases to reduce overactivity in the SCM or upper trapezius muscles, allowing for more effective stretching and active movement.

  • These injections are typically paired with intensive physical therapy to optimize outcomes.
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27
Q

What surgical interventions are available for severe CMT?

A

Surgical options include

  • Distal SCM release
  • Z-plasty for severe cases unresponsive to conservative treatment.

- Surgery is typically considered after 12 months of age and involves cutting the shortened SCM to allow for greater ROM.

  • Post-operative splinting and intensive therapy are essential to prevent recurrence.
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28
Q

What factors influence the prognosis of CMT?

A

Early identification and intervention significantly improve outcomes.

  • Infants diagnosed before 3 months of age typically achieve full ROM and symmetrical development.
  • Late identification, severe ROM limitations, and the presence of an SCM mass are associated with poorer prognoses.
  • Persistent deformities may lead to secondary issues like plagiocephaly, facial asymmetry, and scoliosis.
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29
Q

What are the benefits of prone positioning in CMT treatment?

A

Prone positioning, or tummy time =

  • strengthens neck and trunk muscles
  • promotes symmetrical development
  • counters the effects of supine positioning that may worsen deformational plagiocephaly.

- Encouraging at least 30-60 min/day helps infants develop head control and improves cervical ROM.

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30
Q

What is the referral process for cranial orthosis treatment?

A
  • Referral for cranial orthoses typically occurs at 4-5 months of age when head control develops.
  • Evaluation by a specialist determines the need for treatment.
  • Delayed referral may reduce the effectiveness of orthoses as cranial sutures begin to close.
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31
Q

What is pediatric cancer?

A

Pediatric cancer refers to the uncontrolled growth of abnormal cells in children, which do not function properly and may crowd out normal cells.

  • These cancers often start at a primary site and may metastasize to other areas.

Unlike adult cancers, they are less likely linked to environmental factors

  • More often associated with genetic or developmental processes.
32
Q

What are the most common types of pediatric cancers?

A

The most common pediatric cancers include

  • Leukemia (28%),
  • CNS Tumors (26%)
  • Lymphoma (8%),
  • Neuroblastic Tumors (6%),
  • Sarcomas (e.g., Osteosarcoma, Ewing Sarcoma, Rhabdomyosarcoma),
  • Retinoblastoma,
  • Wilms Tumor.

- Leukemia is the most prevalent, especially acute lymphoblastic leukemia (ALL), which accounts for 75% of childhood leukemia cases.

33
Q

What are the general risk factors for pediatric cancer?

A

Risk factors for pediatric cancers include

  • genetic predispositions (e.g., Down syndrome, Li-Fraumeni syndrome)
  • environmental exposures (e.g., ionizing radiation toxic chemicals)
  • developmental abnormalities.

- Unlike adult cancers, lifestyle factors (e.g., smoking, diet) are typically not significant contributors in pediatric cases.

34
Q

What are common signs and symptoms of pediatric leukemia?

A

- Common symptoms include:

  • anemia (fatigue, pallor)
  • thrombocytopenia (easy bruising, bleeding)
  • neutropenia (frequent infections)
  • bone pain
  • fever
  • lymphadenopathy (enlarged lymph nodes)
  • splenomegaly
  • hepatomegaly

- These symptoms result from overproduction of immature white blood cells, crowding out normal bone marrow function.

35
Q

What are the primary treatments for leukemia in children?

A

Treatments include:

  • Multi-agent chemotherapy (administered over 2-3 years)
  • Stem cell transplant (used in relapsed cases)
  • Supportive care for symptoms like anemia and infections.

- Acute lymphoblastic leukemia (ALL) has a survival rate >90% with proper treatment

- Acute myeloid leukemia (AML) has a survival rate of 65-70%

36
Q

What are the common symptoms of CNS tumors in children?

A

Symptoms vary based on tumor location but may include:

  • headaches
  • seizures
  • drowsiness
  • nausea/vomiting
  • poor coordination
  • ataxic gait,
  • changes in speech, vision, or hearing

- Tumors in the posterior fossa (e.g., medulloblastoma) often present with balance and coordination deficits.

- Tumors in the cerebral hemispheres may cause focal neurological signs.

37
Q

How are CNS tumors typically treated in pediatric patients?

A

Depending on tumor type, size, and location, CNS tumors are treated with a combination of:

  • surgery
  • radiation therapy
  • chemotherapy

- For example, medulloblastoma often requires surgical resection followed by radiation and chemotherapy.

  • Radiation is generally avoided in children under 3 years old due to its severe cognitive effects.
38
Q

What differentiates Hodgkin lymphoma from Non-Hodgkin lymphoma in children?

A

Hodgkin lymphoma:

  • Primarily affects older children/adolescents
  • Presents with painless cervical or supraclavicular adenopathy, night sweats, fatigue, and weight loss.
  • Survival rate of 98%

Non-Hodgkin lymphoma (NHL):

  • More common in younger children
  • Presents with abdominal swelling, changes in bowel habits, or respiratory symptoms.
  • NHL varies based on subtype, with a survival rate of ~91%.
39
Q

What is neuroblastoma, and where does it commonly occur?

A

Neuroblastoma is the most common extracranial solid tumor in infants.

  • Typically arising from the adrenal glands or sympathetic nervous system.
  • Commonly metastasizes to lymph nodes, bones, and bone marrow.
  • Often presents as a palpable, hard mass in the neck or abdomen.

- Other symptoms depend on tumor location and may include

  • pain
  • paralysis (if nerves are involved)
  • systemic (fever & weight loss)
40
Q

What are the main treatment modalities for sarcomas in children?

A

Sarcomas (Osteosarcoma, Ewing sarcoma, rhabdomyosarcoma) are treated with a combination of

  • surgery (e.g., limb-sparing or amputation),
  • chemotherapy,
  • sometimes radiation therapy

- Pre-operative (neoadjuvant) chemo may reduce tumor size.

- Post-operative (adjuvant) chemo/radiation ensures local and systemic control.

  • Osteosarcoma = Bone tumor
  • Ewing Sarcoma = Bone or soft tissue
  • Rhabdomyosarcoma = Soft tissue
41
Q

What is rotationplasty, and when is it performed?

A

Rotationplasty is a surgical procedure often used for osteosarcoma in the distal femur.

  • The tumor is removed while preserving the neurovascular bundle.
  • The lower leg is rotated 180 degrees, and the ankle joint functions as a new knee joint with a prosthesis.
  • This procedure allows for better functional outcomes compared to above-knee amputation.
42
Q

What are the key features of retinoblastoma?

A

Retinoblastoma is a malignancy of the retina.

  • Most common in children under 6 years.
  • It can be unilateral (75% of cases) or bilateral.

- It may present with

  • leukocoria (white reflection in the pupil)
  • strabismus (misaligned eyes - cross eyed)
  • visual deficits

- Treatment options include

  • radiotherapy
  • laser therapy
  • chemotherapy
  • enucleation (removal of the eye) for advanced cases
43
Q

What are the clinical features of Wilms tumor, and how is it staged?

A

Wilms tumor is a nephroblastoma commonly diagnosed in children aged 3-4 years.

- Presents with

  • abdominal swelling/mass
  • fever
  • anemia
  • hypertension

- COG Staging System:

  • Stage I: continued in kidney, removed by surgery
  • Stage II: grown beyond kidney (nearby fatty tissue or blood vessels, removed by surgery
  • Stage III: Not fully removed by surgery, cancer remains in abdomen
  • Stage IV: Spread by blood or organ away from kidney
  • Stage V: tumor in both kidneys

- Treatment

  • surgery
  • chemotherapy
  • possibly radiation (depending on the stage)
44
Q

What are the primary side effects of chemotherapy in children?

A

Side effects vary but often include:

  • fatigue
  • nausea/vomiting
  • chemotherapy-induced peripheral neuropathy (CIPN)
  • hair loss
  • bone marrow suppression (causing anemia, thrombocytopenia, and neutropenia)
  • cognitive deficits

- Long-term effects may include

  • infertility
  • osteoporosis
  • secondary cancers
45
Q

How does physical therapy assist children undergoing cancer treatment?

A

PT addresses functional impairments caused by cancer or its treatments, focusing on ROM deficits, muscle strength, endurance, and age-appropriate developmental skills. Interventions include gait training, prosthetic fitting, and balance exercises. PT also prevents secondary complications like contractures and promotes quality of life by engaging children in creative, family-centered activities.

46
Q

What are the main differences between prenatal and postnatal musculoskeletal development?

A

Prenatal:

  • Bone modeling is minimal, with primary ossification centers forming by 12 weeks gestation.
  • Abnormal intrauterine positioning can lead to deformities like torticollis or clubfoot.

Postnatal:

  • Rapid bone remodeling occurs, with 50% of an infant’s skeleton being replaced annually.
  • Growth occurs through epiphyseal (length) and appositional (diameter) processes, and weight-bearing stimulates bone density.
47
Q

What are the key components of a pediatric musculoskeletal exam?

A

History: Includes pain patterns, changes in activity, and birth details.

Postural Screen: Sitting and standing alignment.

ROM and Strength: Includes popliteal angle for hamstring length and dorsiflexion in different positions.

LE Alignment: Staheli’s rotational profile, foot progression angle, and thigh-foot angle.

Sensation and Gait: Assessment of compensations or asymmetries. These components guide diagnosis and intervention.

48
Q

What is Staheli’s rotational profile, and how is it assessed?

A

Staheli’s rotational profile measures lower extremity alignment through:

  • the foot progression angle,
  • hip rotation (IR/ER),
  • thigh-foot angle,
  • transmalleolar axis

- For example, medial rotation of the hip >70° may indicate femoral anteversion.

  • This assessment identifies abnormal torsional patterns contributing to in-toeing or out-toeing.
49
Q

What is metatarsus adductus, and how is it classified?

A

Metatarsus adductus is a congenital forefoot deformity where the forefoot is adducted relative to the midfoot.

- It is classified into three grades:

  • Grade I (mild): Fully correctable beyond the lateral border of the foot.
  • Grade II (moderate): Corrects to neutral.
  • Grade III (severe): Does not correct to neutral.

- Treatment includes stretching, serial casting, or Bebax shoes for severe cases.

50
Q

What is clubfoot (talipes equinovarus), and how is it managed?

A

Clubfoot (talipes equinovarus) is a congenital deformity characterized by:

  • forefoot adduction
  • hindfoot varus
  • ankle plantarflexion.

- Causes include

  • intrauterine positioning
  • neuromuscular (myelomeningocele)

- Management includes

  • Ponseti method (manual correction followed by serial casting)
  • Achilles tenotomy for residual equinus deformity

- PT interventions focus on developmental skills, weight-bearing, and ambulation.

51
Q

What are the risk factors for developmental dysplasia of the hip (DDH)?

A

Risk factors include breech presentation, female gender, family history, first-born status, and associated conditions like torticollis or metatarsus adductus. These factors contribute to instability or abnormal development of the hip joint, which can lead to dislocations if untreated.

52
Q

What are the classifications of DDH?

A

Subluxable: Femoral head in the acetabulum but partially displaceable.

Dislocatable: Head can be fully dislocated using maneuvers (e.g., Barlow).

Subluxed: Head is partially displaced but reducible.

Dislocated: Head is completely out of the acetabulum and unreducible without intervention.

53
Q

What are the Ortolani and Barlow maneuvers, and how do they detect DDH?

A

The Ortolani maneuver reduces a dislocated hip by abducting and externally rotating the hip while applying gentle pressure.

  • A palpable “clunk” indicates reduction.

The Barlow maneuver tests for dislocatable hips by adducting and applying posterior pressure to a flexed hip.

  • Both are most effective before 2 months of age for detecting hip instability.
54
Q

What is the management strategy for DDH in infants under 6 months of age?

A

Pavlik harness is the first-line treatment for infants under 6 months.

  • It holds the hips in flexion (90-100°) and abduction, promoting proper alignment of the femoral head in the acetabulum.
  • The harness is worn 23-24 hours/day.
  • Complications include avascular necrosis and femoral nerve palsy if improperly fitted.
55
Q

What is arthrogryposis multiplex congenita (AMC), and what are its clinical features?

A

Arthrogryposis multiplex congenita (AMC) is a non-progressive condition characterized by multiple congenital joint contractures due to reduced fetal movement.

  • Clinical features include cylindrical limbs without skin creases, symmetrical joint contractures, hip dislocations, muscle atrophy, and intact sensation.
  • Common deformities include shoulder internal rotation, elbow extension or flexion, wrist flexion, and clubfoot.
56
Q

How is AMC managed during infancy?

A

- Management includes positioning and stretching, serial casting, and splinting to prevent contractures.

- Physical therapy focuses on developmental progression (e.g., sitting, standing) and bracing to support mobility.

- Parent education is essential for home stretching and positioning routines.

  • Surgical corrections may address severe deformities.
57
Q

What is osteogenesis imperfecta (OI), and what are its key clinical features?

A

Osteogenesis Imperfecta (OI) is a genetic connective tissue disorder affecting collagen production, leading to fragile bones.

- Key features include frequent fractures, bowed long bones, spinal deformities, muscle weakness, and ligament laxity.

- Other findings include hearing loss, growth deficiency, and cardiopulmonary issues.

- There are eight types

  • Type II = lethal
  • Type III and VIII = severe
58
Q

What are common interventions for osteogenesis imperfecta?

A

Osteogenesis Imperfecta (OI) interventions include:

  • pharmacologic treatments (e.g., bisphosphonates to improve bone density)
  • orthopedic management (e.g., IM rods, soft splints), and
  • rehabilitation

- PT focuses on safe mobility, strengthening, and aquatic therapy to reduce fracture risk.

  • Handling and positioning in infancy are critical to prevent injury.
59
Q

What is Legg-Calve-Perthes disease, and what are its signs and symptoms?

A

Legg-Calve-Perthes is an avascular necrosis of the femoral head.

  • Most common in boys aged 3-13 years.

- Symptoms include groin, thigh, or knee pain, a limp or Trendelenburg gait, and decreased hip ROM (especially abduction and internal rotation).

- The condition progresses through four stages:

  • condensation
  • fragmentation
  • reossification
  • remodeling
60
Q

How is Legg-Calve-Perthes disease managed?

A

Early management includes

  • pain relief (anti-inflammatories),
  • traction,
  • partial or non-weight bearing with crutches

- Orthotic bracing (e.g., abduction braces) supports proper alignment.

- Surgical options, such as femoral osteotomy, may be used for severe cases.

- PT focuses on restoring ROM, strengthening, and gait training post-surgery.

61
Q

What is Slipped Capital Femoral Epiphysis (SCFE), and what are its causes?

A

Slipped Capital Femoral Epiphysis (SCFE) is the displacement of the femoral head at the growth plate, typically anteriorly and superiorly.

  • It most commonly occurs in adolescents and is associated with factors like obesity, hormonal imbalances, femoral retroversion, and certain conditions (e.g., Down syndrome).
  • SCFE is more common in boys and presents with pain in the groin, medial thigh, or knee and limited hip flexion, abduction, and internal rotation.
62
Q

How is SCFE managed, and what role does PT play?

A

- Management involves surgical stabilization, such as pin fixation, to prevent further slippage.

- PT is crucial post-surgery, focusing on gait training with assistive devices, maintaining knee and ankle ROM, core strengthening, and gradual return to weight-bearing activities.

- Open-chain exercises and aquatic therapy may be introduced early to improve strength without stressing the hip.

63
Q

What is Blount disease, and what are its main features?

A

Blount disease, or tibia vara, is a growth disorder affecting the proximal tibia, resulting in bow-legged deformity. It is classified into three types: infantile (<3 years), adolescent (6-13 years, often trauma-related), and late-onset (associated with obesity). Features include bow-legged posture, knee instability, and medial joint pain. It is more common in early walkers and overweight children.

64
Q

What are the treatment options for Blount disease?

A

- Early stages may be treated with orthotics to realign the tibia, but surgical intervention (e.g., tibial osteotomy) is required for severe deformities or older children.

- PT focuses on lower extremity strengthening, ROM exercises, and gait training to improve functional mobility and reduce compensatory patterns.

65
Q

What is a limb length discrepancy (LLD), and what are its common causes?

A

Limb Length Discrepancy (LLD) refers to a difference in the length of the lower extremities

- Caused by congenital limb deficiencies, fractures, growth plate injuries, neuromuscular disorders, or tumors.

  • It may lead to compensatory gait patterns, scoliosis, and functional limitations.

- Differences greater than 2 cm typically require intervention.

66
Q

How is LLD managed?

A

Management depends on the severity:

  • < 2 cm: Shoe lifts.
  • 2-5 cm: Guided growth (epiphysiodesis) or femoral osteotomy.
  • >5 cm: Limb-lengthening procedures, such as external fixation or internal lengthening devices.

- PT plays a key role in post-surgical rehabilitation, focusing on ROM, strength, and gait mechanics to ensure proper function.

67
Q

What is scoliosis, and what are its types?

A

Scoliosis is a lateral curvature of the spine >10°, classified as:

  • Functional (due to posture or leg length discrepancy)
  • Neuromuscular (from CP or other pathologies)
  • Idiopathic (unknown cause, often in adolescents)

- Idiopathic scoliosis is the most common

  • particularly in girls aged 10-13
  • becomes significant when the curve exceeds 30°
68
Q

How is scoliosis treated, and what role does PT play?

A

Treatment depends on curve severity:

  • 25-40°: Bracing to slow progression
  • >40°: Surgical correction with spinal rods

- PT focuses on postural education, muscle strengthening, flexibility, and post-operative care, including spinal precautions, bed mobility, and transfer training.

- For functional scoliosis, addressing the underlying cause (e.g., LLD) can resolve the issue.

69
Q

What is femoral anteversion, and how does it present in children?

A

Femoral anteversion refers to excessive internal rotation of the femur, leading to in-toeing gait.

  • It is common in young children and often resolves spontaneously with growth as the femur externally rotates.

- Persistent anteversion w/

  • IR > 70° and
  • ER < 20°
    may require intervention.
70
Q

How is tibial torsion assessed and managed?

A
  • Tibial torsion refers to rotational deformities of the tibia. It is assessed using the thigh-foot angle or transmalleolar axis.
  • Medial torsion presents as in-toeing
  • Lateral torsion causes out-toeing
  • Most cases resolve with growth, but persistent torsion may require surgical correction (e.g., osteotomy). PT focuses on gait retraining and strengthening.
71
Q

What is the difference between metatarsus adductus and clubfoot?

A
  • Metatarsus adductus involves adduction of the forefoot with a normal hindfoot and is often correctable.
  • Clubfoot (talipes equinovarus) includes forefoot adduction, hindfoot varus, and ankle plantarflexion, often requiring the Ponseti method for correction.

- Both conditions may be associated with intrauterine positioning, but clubfoot is more complex and involves neuromuscular components.

72
Q

What is the pathophysiology of Legg-Calve-Perthes disease?

A

Legg-Calve-Perthes involves temporary loss of blood supply to the femoral head, causing avascular necrosis. Over time, the bone becomes deformed and weak.

- The condition progresses through four stages:

  • Condensation (necrosis) Necrotic femoral head
  • Fragmentation (collapse) Deformed femoral head and acetabular flattening
  • Reossification
  • Remodeling

- Early intervention aims to prevent femoral head deformation during the reossification phase.

73
Q

How does PT address functional limitations in children with OI?

A

- PT for OI focuses on safe strengthening exercises, promoting mobility through assistive devices, and reducing fracture risk.

- Aquatic therapy is highly recommended due to its low-impact nature.

- Handling techniques are emphasized for caregivers to avoid injury during transfers or daily activities. Immobilization periods are minimized to prevent bone demineralization.

74
Q

What are the primary surgical interventions for severe DDH cases?

A

- For children >12 months with severe DDH, surgical interventions include soft tissue releases, femoral osteotomies, or acetabular osteotomies.

- These procedures realign the femoral head in the acetabulum to improve joint stability.

- Post-operative management often includes spica casting and physical therapy to restore ROM, strength, and functional mobility.

75
Q

Why is early detection crucial in managing pediatric orthopedic conditions?

A
  • Early detection allows for non-invasive or minimally invasive treatments (e.g., Pavlik harness for DDH, orthotics for Blount disease) that prevent long-term complications like joint deformity, gait abnormalities, and chronic pain.
  • Delayed intervention may require more extensive surgical procedures and lead to poorer functional outcomes.