Pediatrics Flashcards
Choledochal cysts tx
Always excise
25% risk of cancer
30% risk of pancreatitis
Type I choledochal cyst tx
whole CBD involved
tx: excise and do hepatico-j
Type II choledochal cyst tx
diverticulum that hangs off CBD
tx: do diverticulectomy
Type III choledochal cyst tx
distal dilation involving sphincter of Oddi
tx: resection or marsupialization
Type IV choledochal cyst tx
intra- and extrahepatic cysts
tx: resection, lobectomy, transplant
Type V choledochal cyst tx
intrahepatic cysts (Caroli's disease) tx: resection, lobectomy, transplant
congenital lobar emphysema
massive hyperinflation of a single lobe (usually upper/middle)
1/3 have respiratory distress at birth
CXR: radioluceny of affected lobe, compression of other lobe
M:F ratio is 2:1
tx: severely symptomatic - lobectomy, good prognosis
cystic hygroma (lymphangioma) tx #1 complication?
resect #1 complication = infection
1st sign of CHF in children?
hepatomegaly
Strawberry hemangioma
appear in 1st few weeks of life. leave alone, most involute by age 7.
Neuroblastoma
- markers its associated with?
- origin cells?
MC solid peds malignancy
- high VMA, high HVA associated with worse prognosis, N-myc
- neural creast cells
1 peds malignancy overall
Leukemia
Wilms tumor
nephroblastoma
80% cure with nephrectomy
Biliary atresia tx
Kasi procedure (before 3 months age) hepatoportoenterostomy
Meckel’s diverticulum
on anti-mesenteric border 2ft from ileocecal valve 2% population 2% symptomatic 2 types of tissue: pancreatic, gastric 2 common presentations: diverticulitis, GIB
1 cause of GIB in children
Meckel’s diverticulum - persistent omphalomesenteric duct
Intussusception tx
reduce with air/contrast enema
IV glucagon can help (relaxes smooth muscle)
Usually presents in < 3 yo
peritonitis = ex lap
(if adult, automatically go to OR due to high risk of malignancy)
Intestinal atresia caused by
Intra-uterine vascular events
10% atresias are multiple
Duodenal atresia sx
Bilious vomiting
Double bubble sign
#1 cause of neonatal duodenal obstruction
associated w/ trisomy 21, 1/3 have cardiac defects
TE fistulas MC type and sx
90% are type C (most “common”): blind esophagus, distal TEF
spits up feeds and NG tube won’t pass
Type A TE fistula
Blind esophagus, no fistula
No air seen in entire GI tract
VATER
Vertebral Anorectal (imperforate anus) TEF Radial Renal anomalies
Ladd’s procedure
For malrotation - appendectomy, take down bands, counterclockwise rotation
Meconium ileus dx and rx
associated with cystic fibrosis
Dx and rx: gastrografin enema
1 cause of colon obstruction
Hirschsprung’s
no BM in 1st 24hrs
dx: rectal biopsy
necrotizing enterocolitis sx and tx
presents AFTER initiating feeds in neonate with blood in stool
tx: peritonitic, free air - OR for resection with ostomy
do contrast eval weeks later to evaluate for stenosis before reconnecting bowel