Pediatric Echo

Question 1

What is the Jatene (arterial switch) procedure (operation)?

Answer 1

An operation used in complete transposition of the great arteries, involving removal of the aorta from its attachment to the RV, and of the pulmonary artery from the LV, and the reattachment of the great arteries to the contralateral ventricles, with reimplantation of the coronary arteries into the neoaorta.
As a consequence, the left ventricle supports the systemic circulation.

Question 2

What are the four components that make up an MR jet?

Answer 2

The four components of MR are:
* zone of convergence
* vena contracta
* size of the jet by color flow
* flow into the pulmonary veins

Question 3

What is DiGeorge syndrome?

Answer 3

DiGeorge syndrome, also called 22q11.2 deletion syndrome, is a disorder caused by a defect in chromosome 22.

Question 4

What is Uhl’s anomaly?

Answer 4

Congenital malformation consisting of nearly total absence of the right ventricular myocardium, presenting with marked enlargement of both the right ventricle and right atrium and subsequent tricuspid regurgitation.
Arrhythmogenic right ventricular dysplasia may be one end of a spectrum and Uhl anomaly the other.

Question 5

What types of congenital heart defects are associated with a right aortic arch?

Answer 5

It is often associated with tetralogy of Fallot, pulmonary atresia, truncus arteriosus and other conotruncal anomalies.