Peads PATH Flashcards
1
Q
Hemimegalencephaly features
A
- Large cerebral hemisphere & hemicranium
- Same hemispehre: Polymicrogyria/lissencephaly/agyria/pachygyria
grey matter heterotopia - Same hemisphere: Enlarged lateral ventricle
2
Q
Hemimegalencephaly clinical
A
(90%) of patients present with focal and generalised infantile spasms
Despite the markedly enlarged head, there are no symptoms of raised intracranial pressure
3
Q
Scimitar syndrome Triad
A
- PAPVR
- Hypoplastic right lung
- Systemic arterial supply to right lower lobe** (get heart failure)
4
Q
Dysgerminoma appearance ?
A
- large, solid, and be bilateral
- Hypercalcemia*