Paeds Surg

Question 1

Omphalocele

• Associated conditions
• mgx

Answer 1

A/w

• cardiac abnormalities
• Trisomy 13, 18, 21
• Beckwith Wiedermann Syndrome
• cleft palate

Immediate tx

• sterile wrapping of bowel to preserve heat, minimise insensible fluid loss
• NG to decompress
• ABC

primary closure of defect
else place bowel in silo bag - reduce gradually over 3-7d in ICU > op again for final closure of ab wall or paint with silver sulphadiazine

Question 2

Associations of situs inversus

Answer 2

primary ciliary dyskinesia
Kartagener syndrome = triad of Situs Inversus + chronic sinusitis + bronchiectasis

• male infertility