Paeds Cardiology Flashcards
what is the difference between acyanotic and cyanotic heart disease?
acyanotic heart disease: the blood contains enough oxygen but is pumped abnormally around the body
cyanotic: there is not enough oxygen present in the blood
name the type of acyanotic heart diseases?
ASD
VSD
aortic stenosis
pulmonary stenosis
mitral stenosis
PDA (patent ductus arteriosus)
coarction of aorta
name the type of cyanotic heart diseases
the five ‘t’s’
- tetralogy of fallot
- transposition of the great arteries
- total anomalous pulmonary venous return (TAPVR)
- truncus arteriosus
- tricuspid valve abnormalities
(- univentricular heart)
what is patent ductus arteriosus?
when the ductus arteriosus (shunt from aorta to pulmonary artery) doesnt close
what is the pathophysiology of a patent ductus arteriosus?
- blood flows into pulmonary vessesl due to increased pressure in teh aorta
- increases the pressure in the pulmonary vessels = pulmonary HTN
- this leads to right heart strain and right ventricular hypertrophy
- increased blood in pulmonary vessels and returnign to left side of heart = left ventricular hypertrophy
how does a patient with patent ductus arteriosus present?
- continuous crescendo-decrescendo ‘machinery’ murmur
- SOB
- difficulty feeding
- poor weight gain
- lower resp tract infections
how is patent ductus arteriosus diagnosed?
confirmed by echo (+/- doppler flow studies)
management of patent ductus arteriosus?
monitored until 1yo with echos (as can close spontaneously up to this age)
after this: transcatheter or surgical closure needed
**those who are symptomatic or have heart failure needed earlier
what are the types of atrial septal defects?
ostium secondum
patent foramen ovale
ostium primum
what are teh complications of atrial septal defects?
stroke in pts with DVTs
atrial fibrillation or atrial flutter
pulmonary HTN and right sided heart failure
eisenmenger syndrome
presentation of a pt with atrial septal defect?
mid systolic, crescendo-decrescendo murmur (loudest at upper left sternal border)
SOB
difficulty feeding
poor weight gain
lower resp tract infections
may present in adulthood with dyspnoea, heart failure or stroke
Mx of atrial septal defect?
small - watching and waiting may be appropriate
transvenous catheter closure (via femoral vein) or open heart
anticoags (aspirin, warfarin, NOACs) needs to reduce clots/strokes in adult
what syndromes are ventricular septal defects associated with?
downs syndrome and turners syndrome
typical clinical features of ventricualr septal defects?
- poor feeding
- dyspnoea
- tachypnoea
- failure to thrive
- pan systolic murmur (heard at left lower sternal border in 3rd and 4th intercostal space, possible systolic thrill)
Tx of ventricular septal defect?
watched overtime if have no symptoms/pulmonary HTN/heart failure - close spontaneously
surgically -> transvenous catheter closure via femoral vein or open heart surgery
need ABX prophylaxis as high risk of developing infective endocarditis
symptoms of aortic stenosis
- fatigue
- SOB
- dizziness
- fainting
**all worse on exertion - if severe can present as heart fialure witihin months of birth
key signs of aortic stenosis
- ejection systolic murmur (heard loudest in aortic area) + crescendo-decrescendo charcter and radiates to carotids
may be present:
- ejection click before murmur
- palpable thrill during systole
- slow rising pulse and narrow pulse pressure
Ix for aortic stenosis?
echo = gold standard
Mx for aortic stenosis?
monitoring + guidance to endocarditis + family screening
- percutaneous balloon aortic valvoplasty
- surgical aortic valvotomy
- valve replacement
complications of aortic stenosis?
- left ventricular outflow tract obstruction
- heart failure
- ventricular arrhythmia
- bacterial endocarditis
- sudden death, often on exertion