Paediatric CVS Flashcards

1
Q

List the three shunts in fetal circulation

A

Ductus venosus - bypasses liver
Foramen ovale - bypasses the right ventricle/pulmonary circulation
Ductus arteriosus - redirects blood from the pulmonary artery to the aorta

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2
Q

List the 5 major cyanotic heart defects

A
Truncus arteriosus
Transposition of the great arteries
Tricuspid valve atresia 
Tetralogy of Fallot
Total anomalous pulmonary venous drainage
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3
Q

What type of shunt occurs in cyanotic heart disease?

A

Right –> left

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4
Q

What type of shunt occurs in acyanotic heart disease?

A

Left –> right

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5
Q

What are the risk factors for transposition of the great arteries?

A

Maternal age >40
Maternal diabetes
Maternal rubella infection
Poor nutrition

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6
Q

When does cyanosis in TGV present?

A

Presents within days of birth

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7
Q

What is the characteristic CXR finding for TGV

A

Cardiomegaly with egg on a string appearance

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8
Q

What is the management for TGV?

A
  1. Admit and stabilise
  2. Maintain patency of shunts
  3. Corrective surgery within 2 weeks of life
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9
Q

How is the potency of shunts maintained in management of TGV?

A

PGE1 (alprostadil) infusion

Balloon atrial septostomy.

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10
Q

What are the 4 classic finding of TOF?

A

VSD
Aorta overriding the VSD
Pulmonary outflow tract obstruction
Secondary RV hypertrophy

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11
Q

What are the risk factors for TOF?

A

Down syndrome
DiGeorge syndrome
Chromosome 22 deletions

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12
Q

Which two main issues occur in TOF?

A

VSD –> overriding aorta

Pulmonary outflow tract obstruction –> RV hypertrophy

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13
Q

What is the significance of the overriding aorta in TOF?

A

Deoxygenated blood also enters the aorta and the systemic circulation

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14
Q

What kind of shunt occurs in truncus arteriosus?

A

Left to right shunt

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15
Q

What kind of shunt occurs in tricuspic atresia?

A

Obligate right to left shunt

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16
Q

What is the presentation of TOF?

A

Cyanosis exacerbated by feeding and crying (Tet spell). Usually not present at birth.
Dyspnoea and tachypnoea

17
Q

What are the signs of TOF?

A

Harsh ejection systolic murmur with loud S2
Characteristic squat in older children
Clubbing

18
Q

How is a Tet spell relieved?

A

Knee to chest position
Oxygen
IV morphine for sedation
Beta-blocker (last resort)

19
Q

What is the characteristic CXR finding for TOF?

A

Boot-shaped heart

20
Q

What is the management for TOF?

A

Stabilise
Temporary shunt
Corrective surgery