Paediatric Cardiology Flashcards

1
Q

What are the three fetal shunts?

A

Ductus venosus (umbilical vein to inferior vena cava)

Foramen ovale (right atrium to left atrium)

Ductus arteriosus (Pulmonary artery to aorta)

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2
Q

How can you keep the ductus arteriosus open and when might you want to keep it open?

A

Prostaglandin infusion

When there is a cardiac abnormality causing right->left shunt.

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3
Q

What are features of an innocent murmur?

A

Soft

Short

Systolic

Symptom-less

Situation dependent

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4
Q

What murmur is associated with an atrial septal defect?

A

Ejection systolic murmur, crescendo decrescendo

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5
Q

What murmur is associated with a PDA?

A

Machinery murmur of 2nd heart sound

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6
Q

What murmur is associated with Tetralogy of Fallot?

A

Ejection systolic murmur heard best at LUSE (pulmonary stenosis)

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7
Q

Which congenital heart conditions cause CYANOTIC heart disease?

A

Tetralogy of Fallot

Transposition of the great arteries

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8
Q

What murmur is associated with aortic stenosis? What other features are there?

A

Ejection systolic murmur, crescendo-decrescendo

Narrow pulse pressure

Slow rising pulse

Soft or absent S2

S4

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9
Q

How is aortic stenosis managed?

A

If asymptomatic -> observe

If symptomatic -> valve replacement

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10
Q

What is the most common complication of aortic stenosis?

A

Left ventricular outflow tract obstruction

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11
Q

What conditions are associated with pulmonary stenosis?

A

Tetralogy of Fallot

William syndrome

Noonan syndrome

Congenital rubella syndrome

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12
Q

How does pulmonary stenosis present?

A

Ejection systolic murmur - louder on inspiration

Often found incidentally

Symptoms can be fatigue, SOB, failure to thrive

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13
Q

What murmur is associated with pulmonary stenosis? What other signs are there?

A

Ejection systolic murmur loudest in the pulmonary area

Palpable thrill

Right ventricular heave due to RV Hypertrophy

Raised JVP

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14
Q

What are causes of heart failure in: Neonates, infants, and older children?

A

Neonates = due to obstructed circulation (Hypoplastic left heart syndrome, aortic stenosis, coaractation of the aorta, interruption of aortic arch)

Infants = due to high pulmonary blood flow (ventricular septal defect, atrioventricular septal defect, large PDA_

Older children (Eisenmenger syndrome, Rheumatic heart Disease, Cardiomyopathy)

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15
Q

Which heart conditions cause a left to right shunt?

A

ASD

VSD

PDA

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16
Q

Which heart conditions cause a right to left shunt?

A

Tetralogy of Fallot

Transposition of the great arteries

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17
Q

Which type of shunt causes cyanosis?

A

Right to left

18
Q

What are signs of heart failure in neonates/infants?

A

Breathlessness

Sweating

Poor feeding

Recurrent chest infections

Failure to thrive

19
Q

What are symptoms and signs of atrial septal defect?

A

Symptoms = wheeze, may be often asymptomatic

Signs =
Ejection systolic murmur

Fixed, widely split S2

20
Q

What is seen on CXR in atrial septal defect?

A

Cardiomegaly

Enlarged pulmonary arteries

Increased pulmonary vascular markings

21
Q

How does a ventricular septal defect present?

A

If it’s smaller than the aortic valve (<3mm) = asymptomatic, LOUD pan systolic murmur at LLSE, quiet pulmonary S2, CXR = normal.

If larger than aortic valve = presents with heart failure, recurrent chest infections, SOFT pan systolic murmur, LOUD pulmonary S2. CXR shows signs of heart failure.

22
Q

How is a ventricular septal defect managed?

A

Smaller asymptomatic VSD = close spontaneously

Larger symptomatic VSD = Surgical repair required

23
Q

What are signs of a patent ductus arteriosus?

A

Continuous machinery murmur

Left subclavicular thrill

Bounding collapsing pulse

Wide pulse pressure

Heaving apex beat

24
Q

How is a patent ductus arteriosus managed?

A

In preterm infants can give Indomethacin/Ibuprofen to help close the PDA

If asymptomatic - wait to see if it closes by 1 year

If symptomatic - needs closing

25
What is Eisenmenger syndrome and which conditions typically can cause it?
When a heart condition causing a L to R shunt, eventually causes pulmonary HTN and therefore it becomes a R to L shunt This leads to cyanosis Causes= ASD, VSD, PDA,TOF
26
How is Eisenmenger syndrome managed?
Complete heart-lung transplantation required
27
Which congenital heart condition is associated with Turner syndrome?
``` Coarctation of the aorta Aortic stenosis (due to bicuspid aortic valve) ```
28
How does coarctation of the aorta present?
Weak femoral pulses Mid systolic murmur Tachypnoea Radio-femoral delay Apical click
29
How is coarctation of the aorta managed?
If critical, need to keep ductus arteriosus open with prostaglandin infusion whilst awaiting surgery
30
What are the 4 features of Tetralogy of Fallot?
1. Ventricular septal defect 2. Right ventricular hypertrophy 3. Pulmonary stenosis 4. Overriding aorta
31
How does Tetralogy of Fallot cause cyanosis?
Pulmonary stenosis means that there is higher pressure on R side of heart, this means that there is a R to L shunt through the VSD
32
How does Tetralogy of Fallot present?
Ejection systolic murmur (due to pulmonary stenosis) Cyanosis "Tet spells" - cyanotic episodes, infant will typically squat
33
What is seen on CXR in Tetralogy of Fallot?
Boot shaped heart
34
How is Tetralogy of Fallot managed?
Surgical repair
35
What is Ebstein's Anomaly?
A congenital heart defect where the tricuspid valve is set lower than usual, causing the RA to be larger than usual and the RV to be smaller than usual
36
What are signs of transposition of the great arteries?
Loud single S2 Prominent right ventricular impulse
37
What does a continuous machinery murmur indicate?
Patent ductus arteriosus
38
What can an ejection systolic murmur indicate?
Aortic stenosis - LLSE (crescendo-decrescendo) Pulmonary stenosis - Pulmonary area Atrial septal defect (crescendo-decrescendo)
39
Aortic stenosis vs. ASD?
Aortic stenosis = narrow pulse pressure, slow rising pulse, soft S2 ASD = fixed splitting of S2
40
What might be seen on an ECG in an ASD?
RBBB
41
Which condition can cause patients with a DVT to develop a stroke?
Atrial septal defect