Other Primary Malignant Neoplasms

Question 1

most common primary hepatic tumor of childhood

Answer 1

Hepatoblastoma

Question 2

at what age they Present in ? and any associated syndrome ?

Answer 2

Median age Around 18 Months
all cases occur before age of 3 years
associated with the FAP.

Question 3

Child presentation and Labs ?

Answer 3

• Asymptomatic
• High AFP
• Mild anemia and thrombocytosis

Question 4

Chemotherapy has a role in hepatoblastoma ?

Answer 4

Yes
Before resection for Down Staging

Question 5

what if patient has a pulmonary mets ?

Answer 5

can go for hepatic resection/tumor resection
then chemo or resection for the lungs

Question 6

There are variety of sarcomas in Liver? usually primary or Mets ?

Answer 6

• rarely manifested as primary liver tumors
• must always be considered metastatic lesions
• Angiosarcoma is probably the best-described primary hepatic sarcoma
• association with vinyl chloride or Thorotrast exposure.
• Angiosarcoma typically is manifested as multiple hepatic masses

Question 7

What is a rare Tumor manifest with multiple bilateral masses ?

Answer 7

Epithel-ioid hemangio-endothel-ioma