Neuromuscular Disorders (Lecture) Flashcards

1
Q

What are the primary sites of pathology for ALS, MD, GBS, PPS, and MS?

A

GBS: Peripheral nervous system demyelination

ALS and PPS: Anterior horn cell and motor neuron

MS: CNS demyelination

MD: muscle

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
2
Q

What are the 4 basic clinical syndromes?

A

Generalized Peripheral Neuropathy: Longest peripheral nerve fibers involved.

Focal Peripheral Neuropathy: Localized disorders of single nerves anywhere from spinal root to smallest branch of the nerve.

Mononeuropathy Multiplex: individual peripheral nerves or their branches are involved at several sites giving rise to multi-focal signs and symptoms.

Mononeuropathy Multiplex and Polyneuropathy may co-exist: often motor and sensory S&S exist.

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
3
Q

What are the S&S, cause, stages, and treatment (general) of GBS?

A

slides 11-13

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
4
Q

what are the PT assessment guodelines for GBS wrt impairments, activity limitations, and participation restriction?

A
  • slides 14-17
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
5
Q

descrbe PT intevention in the acute phase of GBS

A

slide 18-20

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
6
Q

descrbe PT intevention in the plateau phase of GBS

A

slide 21

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
7
Q

descrbe PT intevention in the recovery phase of GBS

A

slide 22-23

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
8
Q

describe the overall Pt summary for GBS patients

A

Intervention goals:

  • Resolve respiratory problems
  • Minimize pain
  • Prevent secondary effects of immobilization
  • Promote recovery of muscle strength and function

For peripheral neuropathy: Inadequate evidence to evaluate the effect of exercise on functional ability but some evidence points to the benefit of strengthening exercises.

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
9
Q

what is post-polio syndrome?

A

progressive clinical syndrome consisting of new weakness, fatigue and pain in those individuals who have recovered from past paralytic polio

  • poliomyelitis (polio), a contagious viral illness that in its most severe form causes paralysis, difficulty breathing and sometimes death
  • infection leads to inflammation of nerve cells in the ventral horns of the spinal cord – damages motor neurons (anterior horn cells)
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
10
Q

how do you make a post-polio diagnosis?

A
  • slide 28
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
11
Q

what is the etiology of post polio syndrome?

A
  • slide 29
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
12
Q

hwta happens to motor units after a polio onset?

A

slide 30-32

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
13
Q

what are risk factors of post-polio syndrome?

A

slide 33

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
14
Q

what things need to be managed with post-polio syndrome patients?

A

identification and treatment of other medical and neurological disorders which can mimic the symptoms of PPS

weakness

fatigue

pain

other problems (pulmonary dysfunction, dysphagia, and psychosocial difficulties

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
15
Q

how to manage weakness for post-polio syndrome patients - and treatment guidelines

A

slide 35-39

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
16
Q

what are the key muscle groups to assess for post polio syndrome?

A
How well did you know this?
1
Not at all
2
3
4
5
Perfectly
17
Q

how to assess, manage, and treat fatigue for post-polio syndrome patients

A

slide 40-44

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
18
Q

describe the management/treatment of pain symptom for post-polio patients

A

slide 45-48

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
19
Q

what is the prognosis for people with post-polio syndrome?

A

slide 50

How well did you know this?
1
Not at all
2
3
4
5
Perfectly
20
Q

what is MS? what causes it and how does it progress?

A

slides 51 and 52

21
Q

what are the outcome predictors for MS?

A

slide 53

22
Q

how do you reach an ms diagnosis?

A

slide 54

23
Q

what is the medical management of ms?

A

slides 55-57

24
Q

what are the most common symptoms of ms?

A

slide 58

25
Q

evidence-infomred practice for MS

A

slide 60

26
Q

what are the goals of rehab for Ms patients?

A

slide 61

27
Q

for Ms, describe how the type of PT intervention depends on the stage od the disease

A

slide 62

28
Q

explain good and bad responses to therapy for MS patients

A
29
Q

what assessment scales are most commonly used for MS?

A

slide 64-68

30
Q

describe management of fatigue for patients with MS. primary vs secondary fatigue

A

slides 69 - 72

31
Q

describe management of muscle weakness for patients with MS - and exercise perscription

A

slides 73-74

32
Q

describe PT management of spasticity for MS patients

A

slide 75

33
Q

describe functional mobility management for MS patients

A

slides 76 - 78

34
Q

describe PT management for MS patients for lack of balance and coordination

A

slide 79

35
Q

describe PT management of deconditioning for MS patients

A

slides 80 and 81

36
Q

describe PT management of sensory dysfunction for MS patients

A

slide 82

37
Q

describe PT management of psychosocial issues for MS patients

A
  • Employment
  • Family coping
  • Social life
    overall: AN EFFECTIVE INTERVENTION CAN HELP GAIN OR SUSTAIN FUNCTION AND MAINTAIN ACTIVITY LEVEL
38
Q

what is ALS? what structures does it involve?

A

slides 87-88

39
Q

how to reach a clinical diagnosis of ALS

A

slide 89

40
Q

onset and symptoms of ALS?

A

slide 90

41
Q

ALS treatment and immediate care after diagnosis

A

slide 91, 92

42
Q

PT goals for patient with ALS

A

slide 94

43
Q

describe typical PT assessment for ALS patients - also measures used to track evolution of symptoms

A

slides 95-97, 105

44
Q

describe the phases and stages of ALS (general)

A

slide 98

45
Q

describe exercise and rehab guidelines for ALS patients in phase 1

A

slides 99-101

46
Q

describe exercise and rehab guidelines for ALS patients in phase 2

A

slides 102-103

47
Q

describe exercise and rehab guidelines for ALS patients in phase 3

A

slide 104, 106

48
Q

in summary, what are the parameters for a submaximal strengthening exercise program for persons with a neuromuscular disease such as Amyotrophic Lateral Sclerosis, Multiple Sclerosis, Post-Polio Syndrome or Guillain-Barre Syndrome?

A

slides 104-110

49
Q

describe upper vs lower motor neuron symptoms

A